Epigastric heteropagus associated with an omphalocele and double outlet right ventricle

Incomplete or asymmetrical conjoined twins are extremely rare congenital anomalies. We report a case of epigastric heteropagus associated with an omphalocele and double outlet right ventricle. The cystic legion of the epigastrium was detected in our patient by an ultrasound scan at 28 weeks' ge...

Full description

Bibliographic Details
Main Authors: Tatsuma Sakaguchi, Yoshinori Hamada, Yusuke Nakamura, Yuki Hashimoto, Hiroshi Hamada, A-Hon Kwon
Format: Article
Language:English
Published: Elsevier 2015-10-01
Series:Journal of Pediatric Surgery Case Reports
Subjects:
Online Access:http://www.sciencedirect.com/science/article/pii/S2213576615001189
_version_ 1811227506615779328
author Tatsuma Sakaguchi
Yoshinori Hamada
Yusuke Nakamura
Yuki Hashimoto
Hiroshi Hamada
A-Hon Kwon
author_facet Tatsuma Sakaguchi
Yoshinori Hamada
Yusuke Nakamura
Yuki Hashimoto
Hiroshi Hamada
A-Hon Kwon
author_sort Tatsuma Sakaguchi
collection DOAJ
description Incomplete or asymmetrical conjoined twins are extremely rare congenital anomalies. We report a case of epigastric heteropagus associated with an omphalocele and double outlet right ventricle. The cystic legion of the epigastrium was detected in our patient by an ultrasound scan at 28 weeks' gestation. He was born at 37 weeks' gestation by scheduled caesarean section. A parasite with an incomplete head and lower limb was attached to the epigastrium of the autosite. Surgical separation of the parasite and silo placement for an omphalocele was successfully performed on the 4th day of life. He underwent secondary surgical closure of the omphalocele on the 10th day. For treatment of the cardiac anomaly, he underwent an operation of Blalock–Taussig shunt because of pulmonary artery stenosis at the age of 3 months and correction of double outlet right ventricle at the age of 10 months. At the 20-month follow-up, he was alive and showed a normal growth pattern.
first_indexed 2024-04-12T09:43:25Z
format Article
id doaj.art-b0a1f06b4a5547439a8c71f3344b5650
institution Directory Open Access Journal
issn 2213-5766
language English
last_indexed 2024-04-12T09:43:25Z
publishDate 2015-10-01
publisher Elsevier
record_format Article
series Journal of Pediatric Surgery Case Reports
spelling doaj.art-b0a1f06b4a5547439a8c71f3344b56502022-12-22T03:38:01ZengElsevierJournal of Pediatric Surgery Case Reports2213-57662015-10-0131046947210.1016/j.epsc.2015.09.008Epigastric heteropagus associated with an omphalocele and double outlet right ventricleTatsuma SakaguchiYoshinori HamadaYusuke NakamuraYuki HashimotoHiroshi HamadaA-Hon KwonIncomplete or asymmetrical conjoined twins are extremely rare congenital anomalies. We report a case of epigastric heteropagus associated with an omphalocele and double outlet right ventricle. The cystic legion of the epigastrium was detected in our patient by an ultrasound scan at 28 weeks' gestation. He was born at 37 weeks' gestation by scheduled caesarean section. A parasite with an incomplete head and lower limb was attached to the epigastrium of the autosite. Surgical separation of the parasite and silo placement for an omphalocele was successfully performed on the 4th day of life. He underwent secondary surgical closure of the omphalocele on the 10th day. For treatment of the cardiac anomaly, he underwent an operation of Blalock–Taussig shunt because of pulmonary artery stenosis at the age of 3 months and correction of double outlet right ventricle at the age of 10 months. At the 20-month follow-up, he was alive and showed a normal growth pattern.http://www.sciencedirect.com/science/article/pii/S2213576615001189Epigastric heteropagusOmphaloceleDouble outlet right ventricle
spellingShingle Tatsuma Sakaguchi
Yoshinori Hamada
Yusuke Nakamura
Yuki Hashimoto
Hiroshi Hamada
A-Hon Kwon
Epigastric heteropagus associated with an omphalocele and double outlet right ventricle
Journal of Pediatric Surgery Case Reports
Epigastric heteropagus
Omphalocele
Double outlet right ventricle
title Epigastric heteropagus associated with an omphalocele and double outlet right ventricle
title_full Epigastric heteropagus associated with an omphalocele and double outlet right ventricle
title_fullStr Epigastric heteropagus associated with an omphalocele and double outlet right ventricle
title_full_unstemmed Epigastric heteropagus associated with an omphalocele and double outlet right ventricle
title_short Epigastric heteropagus associated with an omphalocele and double outlet right ventricle
title_sort epigastric heteropagus associated with an omphalocele and double outlet right ventricle
topic Epigastric heteropagus
Omphalocele
Double outlet right ventricle
url http://www.sciencedirect.com/science/article/pii/S2213576615001189
work_keys_str_mv AT tatsumasakaguchi epigastricheteropagusassociatedwithanomphaloceleanddoubleoutletrightventricle
AT yoshinorihamada epigastricheteropagusassociatedwithanomphaloceleanddoubleoutletrightventricle
AT yusukenakamura epigastricheteropagusassociatedwithanomphaloceleanddoubleoutletrightventricle
AT yukihashimoto epigastricheteropagusassociatedwithanomphaloceleanddoubleoutletrightventricle
AT hiroshihamada epigastricheteropagusassociatedwithanomphaloceleanddoubleoutletrightventricle
AT ahonkwon epigastricheteropagusassociatedwithanomphaloceleanddoubleoutletrightventricle