Pulmonary atresia with ventricular septal defect and major aorto-pulmonary collateral arteries in a young adult

Pulmonary atresia with ventricular septal defect (PA-VSD) and pulmonary blood supply arising from the aorta in the form of major aortopulmonary collateral circulation (MAPCAs) surviving in the adulthood is a rare occurrence. It is usually fatal in the infancy without surgical repair. We report the c...

Full description

Bibliographic Details
Main Author: Rajshree U Dhadve
Format: Article
Language:English
Published: Wolters Kluwer Medknow Publications 2020-01-01
Series:Medical Journal of Dr. D.Y. Patil Vidyapeeth
Subjects:
Online Access:http://www.mjdrdypv.org/article.asp?issn=2589-8302;year=2020;volume=13;issue=4;spage=403;epage=405;aulast=Dhadve
_version_ 1818451797906292736
author Rajshree U Dhadve
author_facet Rajshree U Dhadve
author_sort Rajshree U Dhadve
collection DOAJ
description Pulmonary atresia with ventricular septal defect (PA-VSD) and pulmonary blood supply arising from the aorta in the form of major aortopulmonary collateral circulation (MAPCAs) surviving in the adulthood is a rare occurrence. It is usually fatal in the infancy without surgical repair. We report the case of a 25-year-old female with clinical and imaging findings of PA-VSD. She had previous episodes of cyanosis and exertional breathlessness which she could tolerate without much hampering of day-to-day activity. The current presentation was due to symptoms of bacterial infection which led to the diagnosis of the underlying complex cardiovascular malformation.
first_indexed 2024-12-14T21:12:55Z
format Article
id doaj.art-b0bfe6de3f6b4bf49f12174fd0078ad0
institution Directory Open Access Journal
issn 2589-8302
2589-8310
language English
last_indexed 2024-12-14T21:12:55Z
publishDate 2020-01-01
publisher Wolters Kluwer Medknow Publications
record_format Article
series Medical Journal of Dr. D.Y. Patil Vidyapeeth
spelling doaj.art-b0bfe6de3f6b4bf49f12174fd0078ad02022-12-21T22:47:10ZengWolters Kluwer Medknow PublicationsMedical Journal of Dr. D.Y. Patil Vidyapeeth2589-83022589-83102020-01-0113440340510.4103/mjdrdypu.mjdrdypu_118_19Pulmonary atresia with ventricular septal defect and major aorto-pulmonary collateral arteries in a young adultRajshree U DhadvePulmonary atresia with ventricular septal defect (PA-VSD) and pulmonary blood supply arising from the aorta in the form of major aortopulmonary collateral circulation (MAPCAs) surviving in the adulthood is a rare occurrence. It is usually fatal in the infancy without surgical repair. We report the case of a 25-year-old female with clinical and imaging findings of PA-VSD. She had previous episodes of cyanosis and exertional breathlessness which she could tolerate without much hampering of day-to-day activity. The current presentation was due to symptoms of bacterial infection which led to the diagnosis of the underlying complex cardiovascular malformation.http://www.mjdrdypv.org/article.asp?issn=2589-8302;year=2020;volume=13;issue=4;spage=403;epage=405;aulast=Dhadvecomputed tomography pulmonary angiographymajor aorto-pulmonary collateralspulmonary atresiaventricular septal defect
spellingShingle Rajshree U Dhadve
Pulmonary atresia with ventricular septal defect and major aorto-pulmonary collateral arteries in a young adult
Medical Journal of Dr. D.Y. Patil Vidyapeeth
computed tomography pulmonary angiography
major aorto-pulmonary collaterals
pulmonary atresia
ventricular septal defect
title Pulmonary atresia with ventricular septal defect and major aorto-pulmonary collateral arteries in a young adult
title_full Pulmonary atresia with ventricular septal defect and major aorto-pulmonary collateral arteries in a young adult
title_fullStr Pulmonary atresia with ventricular septal defect and major aorto-pulmonary collateral arteries in a young adult
title_full_unstemmed Pulmonary atresia with ventricular septal defect and major aorto-pulmonary collateral arteries in a young adult
title_short Pulmonary atresia with ventricular septal defect and major aorto-pulmonary collateral arteries in a young adult
title_sort pulmonary atresia with ventricular septal defect and major aorto pulmonary collateral arteries in a young adult
topic computed tomography pulmonary angiography
major aorto-pulmonary collaterals
pulmonary atresia
ventricular septal defect
url http://www.mjdrdypv.org/article.asp?issn=2589-8302;year=2020;volume=13;issue=4;spage=403;epage=405;aulast=Dhadve
work_keys_str_mv AT rajshreeudhadve pulmonaryatresiawithventricularseptaldefectandmajoraortopulmonarycollateralarteriesinayoungadult