Computed Tomographic findings in Patients with Craniofacial Fibrous Dysplasia: A Case Series
Craniofacial Fibrous Dysplasia (CFD) is a rare developmental non inheritable, non neoplastic fibro-osseous disease of the bone, which can be monostotic or polyostotic. The term CFD is used to describe FD where the lesions are confined to contiguous bones of the craniofacial skeleton. This is a cas...
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JCDR Research and Publications Private Limited
2023-08-01
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| Series: | Journal of Clinical and Diagnostic Research |
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| Online Access: | https://www.jcdr.net/articles/PDF/18276/62563_CE[Ra1]_F(IS)_QC(SHK_OM_IS)_PF1(AG_KM)_PFA(AG_KM)_PN(KM).pdf |
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| author | Roopa K Tandur Revanasiddappa Kalyani Ashok Kumar Kattimani Santosh P Patil |
| author_facet | Roopa K Tandur Revanasiddappa Kalyani Ashok Kumar Kattimani Santosh P Patil |
| author_sort | Roopa K Tandur |
| collection | DOAJ |
| description | Craniofacial Fibrous Dysplasia (CFD) is a rare developmental non inheritable, non neoplastic fibro-osseous disease of the bone,
which can be monostotic or polyostotic. The term CFD is used to describe FD where the lesions are confined to contiguous bones of
the craniofacial skeleton. This is a case series of 18 patients with features of FD in facial and skull bones on Computed Tomography
(CT). CT findings of CFD in relation to lesion location, number, appearance, and gender of the patient were documented. Out of
the 18 patients, 10 were males and eight were females. The mean age was 36.4 years with a range of 13 to 77 years. Single bone
involvement was seen in 15 patients, and multiple bone involvement was seen in three patients. Among the cases with single bone
involvement, the ethmoid bone was involved in the majority of the cases (n=5), while the sphenoid and temporal bones were equally
involved in four patients. Two cases showed lesions in the frontal bone. Ground glass attenuation was seen in the majority (n=13)
of the cases. Four cases showed mixed attenuation, and sclerosis was seen in one patient. CT is the investigation of choice for
craniofacial dysplasia, which can help in the diagnosis and extent of the disease. Apart from diagnosis, CT is helpful in monitoring
progression and treatment planning of the disease. CT is the first investigation of choice for craniofacial dysplasia since a plain
radiograph of the skull can show a complex appearance due to overlapping structures. |
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| format | Article |
| id | doaj.art-b1cb1ef391624f60abc939feb5b7c326 |
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| issn | 2249-782X 0973-709X |
| language | English |
| last_indexed | 2024-03-12T13:59:04Z |
| publishDate | 2023-08-01 |
| publisher | JCDR Research and Publications Private Limited |
| record_format | Article |
| series | Journal of Clinical and Diagnostic Research |
| spelling | doaj.art-b1cb1ef391624f60abc939feb5b7c3262023-08-22T10:17:57ZengJCDR Research and Publications Private LimitedJournal of Clinical and Diagnostic Research2249-782X0973-709X2023-08-01178010410.7860/JCDR/2023/62563.18276Computed Tomographic findings in Patients with Craniofacial Fibrous Dysplasia: A Case SeriesRoopa K Tandur0Revanasiddappa Kalyani1Ashok Kumar Kattimani2Santosh P Patil3Professor, Department of Radiodignosis, Khaja Banda Nawaz University- Faculty of Medical Sciences, Kalaburagi, Karnataka, India.Associate Professor, Department of Radiodignosis, Khaja Banda Nawaz University- Faculty of Medical Sciences, Kalaburagi, Karnataka, India.Assistant Professor, Department of Radiodignosis, Bidar Institute of Medical Sciences, Bidar, Karnataka, India.Junior Professor, Department of Radiodignosis, Khaja Banda Nawaz University- Faculty of Medical Sciences, Kalaburagi, Karnataka, India.Craniofacial Fibrous Dysplasia (CFD) is a rare developmental non inheritable, non neoplastic fibro-osseous disease of the bone, which can be monostotic or polyostotic. The term CFD is used to describe FD where the lesions are confined to contiguous bones of the craniofacial skeleton. This is a case series of 18 patients with features of FD in facial and skull bones on Computed Tomography (CT). CT findings of CFD in relation to lesion location, number, appearance, and gender of the patient were documented. Out of the 18 patients, 10 were males and eight were females. The mean age was 36.4 years with a range of 13 to 77 years. Single bone involvement was seen in 15 patients, and multiple bone involvement was seen in three patients. Among the cases with single bone involvement, the ethmoid bone was involved in the majority of the cases (n=5), while the sphenoid and temporal bones were equally involved in four patients. Two cases showed lesions in the frontal bone. Ground glass attenuation was seen in the majority (n=13) of the cases. Four cases showed mixed attenuation, and sclerosis was seen in one patient. CT is the investigation of choice for craniofacial dysplasia, which can help in the diagnosis and extent of the disease. Apart from diagnosis, CT is helpful in monitoring progression and treatment planning of the disease. CT is the first investigation of choice for craniofacial dysplasia since a plain radiograph of the skull can show a complex appearance due to overlapping structures.https://www.jcdr.net/articles/PDF/18276/62563_CE[Ra1]_F(IS)_QC(SHK_OM_IS)_PF1(AG_KM)_PFA(AG_KM)_PN(KM).pdfethmoid bonefibro-osseous diseaseground glass attenuation |
| spellingShingle | Roopa K Tandur Revanasiddappa Kalyani Ashok Kumar Kattimani Santosh P Patil Computed Tomographic findings in Patients with Craniofacial Fibrous Dysplasia: A Case Series Journal of Clinical and Diagnostic Research ethmoid bone fibro-osseous disease ground glass attenuation |
| title | Computed Tomographic findings in Patients with Craniofacial Fibrous Dysplasia: A Case Series |
| title_full | Computed Tomographic findings in Patients with Craniofacial Fibrous Dysplasia: A Case Series |
| title_fullStr | Computed Tomographic findings in Patients with Craniofacial Fibrous Dysplasia: A Case Series |
| title_full_unstemmed | Computed Tomographic findings in Patients with Craniofacial Fibrous Dysplasia: A Case Series |
| title_short | Computed Tomographic findings in Patients with Craniofacial Fibrous Dysplasia: A Case Series |
| title_sort | computed tomographic findings in patients with craniofacial fibrous dysplasia a case series |
| topic | ethmoid bone fibro-osseous disease ground glass attenuation |
| url | https://www.jcdr.net/articles/PDF/18276/62563_CE[Ra1]_F(IS)_QC(SHK_OM_IS)_PF1(AG_KM)_PFA(AG_KM)_PN(KM).pdf |
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