Left ventricular non-compaction in a patient with ankylosing spondylitis
A 58 years old male with a long-standing history of HLA-B27 positive ankylosing spondylitis presented with increasing fatigue and dyspnea on exertion. He had left ventricular dysfunction and enlargement, flail right coronary leaflet of aortic valve with severe eccentric aortic insufficiency along wi...
Main Authors: | , , |
---|---|
Format: | Article |
Language: | English |
Published: |
Tabriz University of Medical Sciences
2016-12-01
|
Series: | Journal of Cardiovascular and Thoracic Research |
Subjects: | |
Online Access: | http://jcvtr.tbzmed.ac.ir/PDF/JCVTR-8-188.pdf |
_version_ | 1818509427821510656 |
---|---|
author | Mehrnoush Toufan Leili Pourafkari Nader D Nader |
author_facet | Mehrnoush Toufan Leili Pourafkari Nader D Nader |
author_sort | Mehrnoush Toufan |
collection | DOAJ |
description | A 58 years old male with a long-standing history of HLA-B27 positive ankylosing spondylitis presented with increasing fatigue and dyspnea on exertion. He had left ventricular dysfunction and enlargement, flail right coronary leaflet of aortic valve with severe eccentric aortic insufficiency along with left ventricular non-compaction in echocardiography. The most common cardiac manifestations of ankylosing spondylitis are aortic insufficiency and conduction disturbances. Involvement of myocardium, in the form of dilated cardiomyopathy and restrictive cardiomyopathy, has also been reported. This case presents a very rare association of ankylosing spondylitis with non-compaction cardiomyopathy. |
first_indexed | 2024-12-10T22:45:19Z |
format | Article |
id | doaj.art-b2159b4641d040f98537e38417f350f8 |
institution | Directory Open Access Journal |
issn | 2008-5117 2008-6830 |
language | English |
last_indexed | 2024-12-10T22:45:19Z |
publishDate | 2016-12-01 |
publisher | Tabriz University of Medical Sciences |
record_format | Article |
series | Journal of Cardiovascular and Thoracic Research |
spelling | doaj.art-b2159b4641d040f98537e38417f350f82022-12-22T01:30:35ZengTabriz University of Medical SciencesJournal of Cardiovascular and Thoracic Research2008-51172008-68302016-12-018418818910.15171/jcvtr.2016.37JCVTR_1786_20160627054100Left ventricular non-compaction in a patient with ankylosing spondylitisMehrnoush Toufan0Leili Pourafkari1Nader D Nader2Cardiovascular Research Center, Tabriz University of Medical Sciences,Tabriz, IranCardiovascular Research Center, Tabriz University of Medical Sciences,Tabriz, IranUniversity at Buffalo, Buffalo, New York, 14214, USAA 58 years old male with a long-standing history of HLA-B27 positive ankylosing spondylitis presented with increasing fatigue and dyspnea on exertion. He had left ventricular dysfunction and enlargement, flail right coronary leaflet of aortic valve with severe eccentric aortic insufficiency along with left ventricular non-compaction in echocardiography. The most common cardiac manifestations of ankylosing spondylitis are aortic insufficiency and conduction disturbances. Involvement of myocardium, in the form of dilated cardiomyopathy and restrictive cardiomyopathy, has also been reported. This case presents a very rare association of ankylosing spondylitis with non-compaction cardiomyopathy.http://jcvtr.tbzmed.ac.ir/PDF/JCVTR-8-188.pdfAnkylosing SpondylitisNoncompaction CardiomyopathyAortic Valve |
spellingShingle | Mehrnoush Toufan Leili Pourafkari Nader D Nader Left ventricular non-compaction in a patient with ankylosing spondylitis Journal of Cardiovascular and Thoracic Research Ankylosing Spondylitis Noncompaction Cardiomyopathy Aortic Valve |
title | Left ventricular non-compaction in a patient with ankylosing spondylitis |
title_full | Left ventricular non-compaction in a patient with ankylosing spondylitis |
title_fullStr | Left ventricular non-compaction in a patient with ankylosing spondylitis |
title_full_unstemmed | Left ventricular non-compaction in a patient with ankylosing spondylitis |
title_short | Left ventricular non-compaction in a patient with ankylosing spondylitis |
title_sort | left ventricular non compaction in a patient with ankylosing spondylitis |
topic | Ankylosing Spondylitis Noncompaction Cardiomyopathy Aortic Valve |
url | http://jcvtr.tbzmed.ac.ir/PDF/JCVTR-8-188.pdf |
work_keys_str_mv | AT mehrnoushtoufan leftventricularnoncompactioninapatientwithankylosingspondylitis AT leilipourafkari leftventricularnoncompactioninapatientwithankylosingspondylitis AT naderdnader leftventricularnoncompactioninapatientwithankylosingspondylitis |