The Heart in Fabry Disease: Mechanisms Beyond Storage and Forthcoming Therapies
In patients with Fabry disease (FD), cardiovascular involvement is the main cause of death and reduction of quality of life. Left ventricular hypertrophy mimicking hypertrophic cardiomyopathy is the main feature of FD cardiac involvement although glycolipid storage occurs in all cardiac cellular typ...
Main Authors: | , , , , , , , |
---|---|
Format: | Article |
Language: | English |
Published: |
IMR Press
2022-05-01
|
Series: | Reviews in Cardiovascular Medicine |
Subjects: | |
Online Access: | https://www.imrpress.com/journal/RCM/23/6/10.31083/j.rcm2306196 |