Focus on Paediatric Restrictive Cardiomyopathy: Frequently Asked Questions
Restrictive cardiomyopathy (RCM) is characterized by restrictive ventricular pathophysiology determined by increased myocardial stiffness. While suspicion of RCM is initially raised by clinical evaluation and supported by electrocardiographic and echocardiographic findings, invasive hemodynamic eval...
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| Format: | Article |
| Language: | English |
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MDPI AG
2023-12-01
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| Series: | Diagnostics |
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| Online Access: | https://www.mdpi.com/2075-4418/13/24/3666 |
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| author | Mattia Zampieri Chiara Di Filippo Chiara Zocchi Vera Fico Cristina Golinelli Gaia Spaziani Giovanni Calabri Elena Bennati Francesca Girolami Alberto Marchi Silvia Passantino Giulio Porcedda Guglielmo Capponi Alessia Gozzini Iacopo Olivotto Luca Ragni Silvia Favilli |
| author_facet | Mattia Zampieri Chiara Di Filippo Chiara Zocchi Vera Fico Cristina Golinelli Gaia Spaziani Giovanni Calabri Elena Bennati Francesca Girolami Alberto Marchi Silvia Passantino Giulio Porcedda Guglielmo Capponi Alessia Gozzini Iacopo Olivotto Luca Ragni Silvia Favilli |
| author_sort | Mattia Zampieri |
| collection | DOAJ |
| description | Restrictive cardiomyopathy (RCM) is characterized by restrictive ventricular pathophysiology determined by increased myocardial stiffness. While suspicion of RCM is initially raised by clinical evaluation and supported by electrocardiographic and echocardiographic findings, invasive hemodynamic evaluation is often required for diagnosis and management of patients during follow-up. RCM is commonly associated with a poor prognosis and a high incidence of heart failure, and PH is reported in paediatric patients with RCM. Currently, only a few therapies are available for specific RCM aetiologies. Early referral to centres for advanced heart failure treatment is often necessary. The aim of this review is to address questions frequently asked when facing paediatric patients with RCM, including issues related to aetiologies, clinical presentation, diagnostic process and prognosis. |
| first_indexed | 2024-03-08T20:52:02Z |
| format | Article |
| id | doaj.art-b2e23465e3ef4ea9ad46560ae4c1eb94 |
| institution | Directory Open Access Journal |
| issn | 2075-4418 |
| language | English |
| last_indexed | 2024-03-08T20:52:02Z |
| publishDate | 2023-12-01 |
| publisher | MDPI AG |
| record_format | Article |
| series | Diagnostics |
| spelling | doaj.art-b2e23465e3ef4ea9ad46560ae4c1eb942023-12-22T14:03:16ZengMDPI AGDiagnostics2075-44182023-12-011324366610.3390/diagnostics13243666Focus on Paediatric Restrictive Cardiomyopathy: Frequently Asked QuestionsMattia Zampieri0Chiara Di Filippo1Chiara Zocchi2Vera Fico3Cristina Golinelli4Gaia Spaziani5Giovanni Calabri6Elena Bennati7Francesca Girolami8Alberto Marchi9Silvia Passantino10Giulio Porcedda11Guglielmo Capponi12Alessia Gozzini13Iacopo Olivotto14Luca Ragni15Silvia Favilli16Pediatric Cardiology, Meyer Children’s University Hospital IRCCS, 50134 Florence, ItalyLocal Health Unit, Outpatient Cardiology Clinic, 84131 Salerno, ItalyCardiovascular Department, San Donato Hospital, 52100 Arezzo, ItalyPediatric Cardiology, Meyer Children’s University Hospital IRCCS, 50134 Florence, ItalyPediatric Cardiology and Adult Congenital Heart Disease Program, Department of Cardio—Thoracic and Vascular Medicine, IRCCS Azienda Ospedaliero—Universitaria di Bologna, 40138 Bologna, ItalyPediatric Cardiology, Meyer Children’s University Hospital IRCCS, 50134 Florence, ItalyPediatric Cardiology, Meyer Children’s University Hospital IRCCS, 50134 Florence, ItalyPediatric Cardiology, Meyer Children’s University Hospital IRCCS, 50134 Florence, ItalyPediatric Cardiology, Meyer Children’s University Hospital IRCCS, 50134 Florence, ItalyPediatric Cardiology, Meyer Children’s University Hospital IRCCS, 50134 Florence, ItalyPediatric Cardiology, Meyer Children’s University Hospital IRCCS, 50134 Florence, ItalyPediatric Cardiology, Meyer Children’s University Hospital IRCCS, 50134 Florence, ItalyPediatric Cardiology, Meyer Children’s University Hospital IRCCS, 50134 Florence, ItalyPediatric Cardiology, Meyer Children’s University Hospital IRCCS, 50134 Florence, ItalyPediatric Cardiology, Meyer Children’s University Hospital IRCCS, 50134 Florence, ItalyPediatric Cardiology and Adult Congenital Heart Disease Program, Department of Cardio—Thoracic and Vascular Medicine, IRCCS Azienda Ospedaliero—Universitaria di Bologna, 40138 Bologna, ItalyPediatric Cardiology, Meyer Children’s University Hospital IRCCS, 50134 Florence, ItalyRestrictive cardiomyopathy (RCM) is characterized by restrictive ventricular pathophysiology determined by increased myocardial stiffness. While suspicion of RCM is initially raised by clinical evaluation and supported by electrocardiographic and echocardiographic findings, invasive hemodynamic evaluation is often required for diagnosis and management of patients during follow-up. RCM is commonly associated with a poor prognosis and a high incidence of heart failure, and PH is reported in paediatric patients with RCM. Currently, only a few therapies are available for specific RCM aetiologies. Early referral to centres for advanced heart failure treatment is often necessary. The aim of this review is to address questions frequently asked when facing paediatric patients with RCM, including issues related to aetiologies, clinical presentation, diagnostic process and prognosis.https://www.mdpi.com/2075-4418/13/24/3666restrictive cardiomyopathypaediatric |
| spellingShingle | Mattia Zampieri Chiara Di Filippo Chiara Zocchi Vera Fico Cristina Golinelli Gaia Spaziani Giovanni Calabri Elena Bennati Francesca Girolami Alberto Marchi Silvia Passantino Giulio Porcedda Guglielmo Capponi Alessia Gozzini Iacopo Olivotto Luca Ragni Silvia Favilli Focus on Paediatric Restrictive Cardiomyopathy: Frequently Asked Questions Diagnostics restrictive cardiomyopathy paediatric |
| title | Focus on Paediatric Restrictive Cardiomyopathy: Frequently Asked Questions |
| title_full | Focus on Paediatric Restrictive Cardiomyopathy: Frequently Asked Questions |
| title_fullStr | Focus on Paediatric Restrictive Cardiomyopathy: Frequently Asked Questions |
| title_full_unstemmed | Focus on Paediatric Restrictive Cardiomyopathy: Frequently Asked Questions |
| title_short | Focus on Paediatric Restrictive Cardiomyopathy: Frequently Asked Questions |
| title_sort | focus on paediatric restrictive cardiomyopathy frequently asked questions |
| topic | restrictive cardiomyopathy paediatric |
| url | https://www.mdpi.com/2075-4418/13/24/3666 |
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