Case report: Giant congenital pulmonary airway malformation initially managed and resected on ECMO
Congenital pulmonary airway malformations (CPAM) are a common congenital anomaly, occurring as a result of aberrant formation of pulmonary lobes or segments. Many patients with CPAM are treated with postnatal surgical excision within 1-year of age. CPAM that are enlarged to the point of causing an i...
| Main Authors: | , , , |
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| Format: | Article |
| Language: | English |
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Elsevier
2016-06-01
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| Series: | Journal of Pediatric Surgery Case Reports |
| Subjects: | |
| Online Access: | http://www.sciencedirect.com/science/article/pii/S2213576615300634 |
| _version_ | 1818912207837069312 |
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| author | Richard Yeker Bradley Segura Daniel Saltzman Donavon Hess Jr. |
| author_facet | Richard Yeker Bradley Segura Daniel Saltzman Donavon Hess Jr. |
| author_sort | Richard Yeker |
| collection | DOAJ |
| description | Congenital pulmonary airway malformations (CPAM) are a common congenital anomaly, occurring as a result of aberrant formation of pulmonary lobes or segments. Many patients with CPAM are treated with postnatal surgical excision within 1-year of age. CPAM that are enlarged to the point of causing an intrathoracic mass effect may cause hydrops fetalis. Fetuses affected in this way may require prenatal intervention and immediate postnatal intervention. We herein report a case of a large CPAM causing hydrops fetalis and postnatal respiratory failure, treated by an aggressive prenatal and postnatal multidisciplinary approach, culminating in resection of the lesion while on extracorporeal membrane oxygenation (ECMO) support. |
| first_indexed | 2024-12-19T23:10:56Z |
| format | Article |
| id | doaj.art-b3107d00f24f476fbca0b10154d071fa |
| institution | Directory Open Access Journal |
| issn | 2213-5766 |
| language | English |
| last_indexed | 2024-12-19T23:10:56Z |
| publishDate | 2016-06-01 |
| publisher | Elsevier |
| record_format | Article |
| series | Journal of Pediatric Surgery Case Reports |
| spelling | doaj.art-b3107d00f24f476fbca0b10154d071fa2022-12-21T20:02:14ZengElsevierJournal of Pediatric Surgery Case Reports2213-57662016-06-019C434410.1016/j.epsc.2016.04.003Case report: Giant congenital pulmonary airway malformation initially managed and resected on ECMORichard YekerBradley SeguraDaniel SaltzmanDonavon Hess Jr.Congenital pulmonary airway malformations (CPAM) are a common congenital anomaly, occurring as a result of aberrant formation of pulmonary lobes or segments. Many patients with CPAM are treated with postnatal surgical excision within 1-year of age. CPAM that are enlarged to the point of causing an intrathoracic mass effect may cause hydrops fetalis. Fetuses affected in this way may require prenatal intervention and immediate postnatal intervention. We herein report a case of a large CPAM causing hydrops fetalis and postnatal respiratory failure, treated by an aggressive prenatal and postnatal multidisciplinary approach, culminating in resection of the lesion while on extracorporeal membrane oxygenation (ECMO) support.http://www.sciencedirect.com/science/article/pii/S2213576615300634CPAMEarly resectionECMO |
| spellingShingle | Richard Yeker Bradley Segura Daniel Saltzman Donavon Hess Jr. Case report: Giant congenital pulmonary airway malformation initially managed and resected on ECMO Journal of Pediatric Surgery Case Reports CPAM Early resection ECMO |
| title | Case report: Giant congenital pulmonary airway malformation initially managed and resected on ECMO |
| title_full | Case report: Giant congenital pulmonary airway malformation initially managed and resected on ECMO |
| title_fullStr | Case report: Giant congenital pulmonary airway malformation initially managed and resected on ECMO |
| title_full_unstemmed | Case report: Giant congenital pulmonary airway malformation initially managed and resected on ECMO |
| title_short | Case report: Giant congenital pulmonary airway malformation initially managed and resected on ECMO |
| title_sort | case report giant congenital pulmonary airway malformation initially managed and resected on ecmo |
| topic | CPAM Early resection ECMO |
| url | http://www.sciencedirect.com/science/article/pii/S2213576615300634 |
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