Solitary extranodal Rosai-Dorfman disease of the mandible: an exceedingly rare presentation

Sinus histiocytosis with massive lymphadenopathy, generally known by the name of Rosai-Dorfman disease is a rare benign condition principally affecting cervical lymph nodes. Concurrent extra-nodal disease frequently occurs, however, solitary extra-nodal disease involving the mandible is exceedingly...

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Main Authors: Ameer Hamza, Zhifei Zhang, Basim Al-Khafaji
Format: Article
Language:English
Published: University of São Paulo 2018-08-01
Series:Autopsy and Case Reports
Subjects:
Online Access:http://www.revistas.usp.br/autopsy/article/view/149967
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author Ameer Hamza
Zhifei Zhang
Basim Al-Khafaji
author_facet Ameer Hamza
Zhifei Zhang
Basim Al-Khafaji
author_sort Ameer Hamza
collection DOAJ
description Sinus histiocytosis with massive lymphadenopathy, generally known by the name of Rosai-Dorfman disease is a rare benign condition principally affecting cervical lymph nodes. Concurrent extra-nodal disease frequently occurs, however, solitary extra-nodal disease involving the mandible is exceedingly rare with less than five reported cases in the English literature. We describe a case of primary involvement of the mandible in a 27-year-old female, and discuss the differential diagnosis of this disease with other histiocytic lesions.
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spelling doaj.art-b335159cbf6043f49afd45c5ce46d6b72022-12-21T21:20:30ZengUniversity of São PauloAutopsy and Case Reports2236-19602018-08-018310.4322/acr.2018.036Solitary extranodal Rosai-Dorfman disease of the mandible: an exceedingly rare presentationAmeer Hamza0Zhifei Zhang1Basim Al-Khafaji2St. John Hospital and Medical Center, Department of Pathology.St. John Hospital and Medical Center, Department of Pathology.St. John Hospital and Medical Center, Department of Pathology.Sinus histiocytosis with massive lymphadenopathy, generally known by the name of Rosai-Dorfman disease is a rare benign condition principally affecting cervical lymph nodes. Concurrent extra-nodal disease frequently occurs, however, solitary extra-nodal disease involving the mandible is exceedingly rare with less than five reported cases in the English literature. We describe a case of primary involvement of the mandible in a 27-year-old female, and discuss the differential diagnosis of this disease with other histiocytic lesions.http://www.revistas.usp.br/autopsy/article/view/149967Histiocytosis, Sinus; Histiocytosis, NonLangerhan-cell; Mandible.
spellingShingle Ameer Hamza
Zhifei Zhang
Basim Al-Khafaji
Solitary extranodal Rosai-Dorfman disease of the mandible: an exceedingly rare presentation
Autopsy and Case Reports
Histiocytosis, Sinus; Histiocytosis, NonLangerhan-cell; Mandible.
title Solitary extranodal Rosai-Dorfman disease of the mandible: an exceedingly rare presentation
title_full Solitary extranodal Rosai-Dorfman disease of the mandible: an exceedingly rare presentation
title_fullStr Solitary extranodal Rosai-Dorfman disease of the mandible: an exceedingly rare presentation
title_full_unstemmed Solitary extranodal Rosai-Dorfman disease of the mandible: an exceedingly rare presentation
title_short Solitary extranodal Rosai-Dorfman disease of the mandible: an exceedingly rare presentation
title_sort solitary extranodal rosai dorfman disease of the mandible an exceedingly rare presentation
topic Histiocytosis, Sinus; Histiocytosis, NonLangerhan-cell; Mandible.
url http://www.revistas.usp.br/autopsy/article/view/149967
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AT zhifeizhang solitaryextranodalrosaidorfmandiseaseofthemandibleanexceedinglyrarepresentation
AT basimalkhafaji solitaryextranodalrosaidorfmandiseaseofthemandibleanexceedinglyrarepresentation