Urachal mucinous cystadenoma in infant: First case report in infant and review of literature
Introduction: As only ten cases have been described in current literature, urachal mucinous cystadenoma seems rare. All studied cases concerned adults or adolescents; this paper reports the first infant presenting urachal mucinous cystadenoma. Case report: A seven-month-old boy affected by urachal m...
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| Format: | Article |
| Language: | English |
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Elsevier
2021-08-01
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| Series: | Journal of Pediatric Surgery Case Reports |
| Subjects: | |
| Online Access: | http://www.sciencedirect.com/science/article/pii/S2213576621001639 |
| _version_ | 1819106378336174080 |
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| author | Barbara Bogaert Berenice Tulelli Marine Rodesch Caroline Pregardien Sandrine Rorive Pierre Lingier |
| author_facet | Barbara Bogaert Berenice Tulelli Marine Rodesch Caroline Pregardien Sandrine Rorive Pierre Lingier |
| author_sort | Barbara Bogaert |
| collection | DOAJ |
| description | Introduction: As only ten cases have been described in current literature, urachal mucinous cystadenoma seems rare. All studied cases concerned adults or adolescents; this paper reports the first infant presenting urachal mucinous cystadenoma. Case report: A seven-month-old boy affected by urachal mucinous cystadenoma, presented as only sign persistent purulent umbilical discharge. Ultrasonography showed nodular structure with liquid content evoking urachal cyst. Radical surgical excision was performed. Histopathology proved diagnosis of urachal mucinous cystadenoma. No complications were observed. Follow-up consultation eight days postoperative was reassuring, evaluating infection and recurrence absence, and scar healing. Discussion: Preservation of urachus lumen may lead to urachal diseases: patent, diverticulum, sinus and cyst. Mucinous cystadenoma is rarely found in urachus. Solely umbilical purulent discharge was observed, in contrast to all reported cases. Same type of investigation, ultrasonography, was conducted to evoke diagnosis. Since urachal mucinous cystadenoma may transform into adenocarcinoma, prophylactic excision is recommended, and prognosis depends on its radicalness. No long-term outcome for infants is available in literature. We propose annual follow-up by ultrasonography. Conclusion: Urachal mucinous cystadenoma in infants is uncommon. Umbilical discharge must indicate ultrasonography. Surgical excision is recommended in case of suspicion. Long term outcomes are yet to be evaluated. |
| first_indexed | 2024-12-22T02:37:11Z |
| format | Article |
| id | doaj.art-b5c6effb94ee4f428bf6e2381bef0c44 |
| institution | Directory Open Access Journal |
| issn | 2213-5766 |
| language | English |
| last_indexed | 2024-12-22T02:37:11Z |
| publishDate | 2021-08-01 |
| publisher | Elsevier |
| record_format | Article |
| series | Journal of Pediatric Surgery Case Reports |
| spelling | doaj.art-b5c6effb94ee4f428bf6e2381bef0c442022-12-21T18:41:44ZengElsevierJournal of Pediatric Surgery Case Reports2213-57662021-08-0171101942Urachal mucinous cystadenoma in infant: First case report in infant and review of literatureBarbara Bogaert0Berenice Tulelli1Marine Rodesch2Caroline Pregardien3Sandrine Rorive4Pierre Lingier5Department of Neonatal and Pediatric Surgery, Erasme Hospital, Université Libre de Bruxelles, Route de Lennik 808, 1070, Brussels, BelgiumDepartment of Neonatal and Pediatric Surgery, Erasme Hospital, Université Libre de Bruxelles, Route de Lennik 808, 1070, Brussels, BelgiumDepartment of Pediatrics, Erasme Hospital, Université Libre de Bruxelles, Route de Lennik 808, 1070, Brussels, BelgiumDepartment of Anesthetics, CHIREC Delta, Boulevard du Triomphe 201, 1160, Brussels, BelgiumDepartment of Pathology, Erasme Hospital, Université Libre de Bruxelles, Route de Lennik 808, 1070, Brussels, Belgium; CurePath, “Centre Universitaire Inter Régional d'expertise en Anatomie Pathologique Hospitalière” CHIREC, CHU Tivoli, Université Libre de Bruxelles, Rue de Borfilet 12A, 6040, Jumet, BelgiumDepartment of Neonatal and Pediatric Surgery, Erasme Hospital, Université Libre de Bruxelles, Route de Lennik 808, 1070, Brussels, Belgium; Corresponding author. Route de Lennik 808, 1070, Brussels, Belgium.Introduction: As only ten cases have been described in current literature, urachal mucinous cystadenoma seems rare. All studied cases concerned adults or adolescents; this paper reports the first infant presenting urachal mucinous cystadenoma. Case report: A seven-month-old boy affected by urachal mucinous cystadenoma, presented as only sign persistent purulent umbilical discharge. Ultrasonography showed nodular structure with liquid content evoking urachal cyst. Radical surgical excision was performed. Histopathology proved diagnosis of urachal mucinous cystadenoma. No complications were observed. Follow-up consultation eight days postoperative was reassuring, evaluating infection and recurrence absence, and scar healing. Discussion: Preservation of urachus lumen may lead to urachal diseases: patent, diverticulum, sinus and cyst. Mucinous cystadenoma is rarely found in urachus. Solely umbilical purulent discharge was observed, in contrast to all reported cases. Same type of investigation, ultrasonography, was conducted to evoke diagnosis. Since urachal mucinous cystadenoma may transform into adenocarcinoma, prophylactic excision is recommended, and prognosis depends on its radicalness. No long-term outcome for infants is available in literature. We propose annual follow-up by ultrasonography. Conclusion: Urachal mucinous cystadenoma in infants is uncommon. Umbilical discharge must indicate ultrasonography. Surgical excision is recommended in case of suspicion. Long term outcomes are yet to be evaluated.http://www.sciencedirect.com/science/article/pii/S2213576621001639UrachusMucinous cystadenomaInfant |
| spellingShingle | Barbara Bogaert Berenice Tulelli Marine Rodesch Caroline Pregardien Sandrine Rorive Pierre Lingier Urachal mucinous cystadenoma in infant: First case report in infant and review of literature Journal of Pediatric Surgery Case Reports Urachus Mucinous cystadenoma Infant |
| title | Urachal mucinous cystadenoma in infant: First case report in infant and review of literature |
| title_full | Urachal mucinous cystadenoma in infant: First case report in infant and review of literature |
| title_fullStr | Urachal mucinous cystadenoma in infant: First case report in infant and review of literature |
| title_full_unstemmed | Urachal mucinous cystadenoma in infant: First case report in infant and review of literature |
| title_short | Urachal mucinous cystadenoma in infant: First case report in infant and review of literature |
| title_sort | urachal mucinous cystadenoma in infant first case report in infant and review of literature |
| topic | Urachus Mucinous cystadenoma Infant |
| url | http://www.sciencedirect.com/science/article/pii/S2213576621001639 |
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