Univentricular heart - perioperative management strategy
The term univentricular heart encompasses a wide variety ofheart defects that functionally andphysiologically. constitute a single ventricle chamber. The disease variants comprising this spectrum are not amenable to biventricular repair, and require staged palliation culminating in cavopulmonary con...
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| Format: | Article |
| Language: | English |
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Wolters Kluwer Medknow Publications
2014-01-01
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| Series: | Journal of Pediatric Critical Care |
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| Online Access: | http://www.jpcc.org.in/article.asp?issn=2349-6592;year=2014;volume=1;issue=3;spage=173;epage=185;aulast=Singh |
| Summary: | The term univentricular heart encompasses a wide variety ofheart defects that functionally andphysiologically. constitute a single ventricle chamber. The disease variants comprising this spectrum are not amenable to biventricular repair, and require staged palliation culminating in cavopulmonary connection. Broadly, the management hinges on controlling pulmonary blood flow in early infancy, by means of aortopulmonary shunting in pulmonary atresia or stenosis or pulmonary artery banding for excess pulmonary blood flow situations. Concomitant repair of associated anomalies, requires addressal. Neonates and early infancy patients with hypoplastic left heart syndrome(HLHS), undergo staged Norwood procedine, resulting in eventual total cavo pulmonary connection with the right ventricle as the functional systemic chamber. The current review focuses on basics of univentricular physiology, perioperative management and with a brief discussion on the current guidelines for medical management. |
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| ISSN: | 2349-6592 2455-7099 |