Progressive familial intrahepatic cholestasis—outcome and time to transplant after biliary diversion according to genetic subtypes

Progressive familial intrahepatic cholestasis—outcome and time to transplant after biliary diversion according to genetic subtypes

BackgroundProgressive familial intrahepatic cholestasis (PFIC) is a heterogeneous disease characterized by progressive cholestasis in early childhood. Surgical therapy aims at preventing bile absorption either by external or internal biliary diversion (BD). Several different genetic subtypes encode...

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Bibliographic Details
Main Authors: Abdulla Sahloul, Elke Lainka, Simone Kathemann, Sandra Swoboda, Carola Dröge, Verena Keitel, Yahya Saleh Al-Matary, Michael Berger, Maren Schulze
Format: Article
Language:English
Published: Frontiers Media S.A. 2023-06-01
Series:Frontiers in Surgery
Subjects:
biliary diversion
morbus byler
pediatric liver transplantation (pediatric LT)
progressive familial intrahepatic cholestasis (PFIC)
pediatric surgery
liver disease
Online Access:https://www.frontiersin.org/articles/10.3389/fsurg.2023.1074229/full

Internet

https://www.frontiersin.org/articles/10.3389/fsurg.2023.1074229/full

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