Umbilical Cord Teratoma Presenting as Ruptured Omphalocele

Congenital mature teratomas of the umbilical cord are extremely rare. We report on a girl who presented with a ruptured omphalocele and a 7 cm mass connected to the umbilicus, which we resected on the first day of life. Histology revealed mature umbilical cord teratoma . On the 29th day of life, a s...

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Main Authors: Fabian Doktor, Jan-Hendrik Gosemann, Peter Zimmermann, Manuela Siekmeyer, Holger Stepan, Martin Lacher
Format: Article
Language:English
Published: Georg Thieme Verlag KG 2022-01-01
Series:European Journal of Pediatric Surgery Reports
Subjects:
Online Access:http://www.thieme-connect.de/DOI/DOI?10.1055/s-0041-1741509
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author Fabian Doktor
Jan-Hendrik Gosemann
Peter Zimmermann
Manuela Siekmeyer
Holger Stepan
Martin Lacher
author_facet Fabian Doktor
Jan-Hendrik Gosemann
Peter Zimmermann
Manuela Siekmeyer
Holger Stepan
Martin Lacher
author_sort Fabian Doktor
collection DOAJ
description Congenital mature teratomas of the umbilical cord are extremely rare. We report on a girl who presented with a ruptured omphalocele and a 7 cm mass connected to the umbilicus, which we resected on the first day of life. Histology revealed mature umbilical cord teratoma . On the 29th day of life, a secondary laparotomy was necessary to address the associated intestinal malformations (megaduodenum, stenotic small bowel with duplication and malrotation). After a prolonged hospital stay, we discharged the patient in age-appropriate conditions. Antenatal diagnosis of an umbilical cord tumor can be challenging in the presence of an omphalocele. Given the high prevalence of associated malformations, the finding of umbilical cord teratoma should be followed by a detailed and comprehensive neonatal workup for additional abnormalities.
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spelling doaj.art-b9d8875ecec84263aa0b57083f7deb242022-12-22T04:06:15ZengGeorg Thieme Verlag KGEuropean Journal of Pediatric Surgery Reports2194-76192194-76272022-01-011001e6e810.1055/s-0041-1741509Umbilical Cord Teratoma Presenting as Ruptured OmphaloceleFabian Doktor0Jan-Hendrik Gosemann1Peter Zimmermann2Manuela Siekmeyer3Holger Stepan4Martin Lacher5Department of Pediatric Surgery, University of Leipzig, Leipzig, Saxony, GermanyDepartment of Pediatric Surgery, University of Leipzig, Leipzig, Saxony, GermanyDepartment of Pediatric Surgery, University of Leipzig, Leipzig, Saxony, GermanyDepartment of Pediatrics, University of Leipzig, Leipzig, Saxony, GermanyDivision of Obstetrics, University of Leipzig, Leipzig, Saxony, GermanyDepartment of Pediatric Surgery, University of Leipzig, Leipzig, Saxony, GermanyCongenital mature teratomas of the umbilical cord are extremely rare. We report on a girl who presented with a ruptured omphalocele and a 7 cm mass connected to the umbilicus, which we resected on the first day of life. Histology revealed mature umbilical cord teratoma . On the 29th day of life, a secondary laparotomy was necessary to address the associated intestinal malformations (megaduodenum, stenotic small bowel with duplication and malrotation). After a prolonged hospital stay, we discharged the patient in age-appropriate conditions. Antenatal diagnosis of an umbilical cord tumor can be challenging in the presence of an omphalocele. Given the high prevalence of associated malformations, the finding of umbilical cord teratoma should be followed by a detailed and comprehensive neonatal workup for additional abnormalities.http://www.thieme-connect.de/DOI/DOI?10.1055/s-0041-1741509umbilical cord teratomaomphaloceleabdominal wall defect
spellingShingle Fabian Doktor
Jan-Hendrik Gosemann
Peter Zimmermann
Manuela Siekmeyer
Holger Stepan
Martin Lacher
Umbilical Cord Teratoma Presenting as Ruptured Omphalocele
European Journal of Pediatric Surgery Reports
umbilical cord teratoma
omphalocele
abdominal wall defect
title Umbilical Cord Teratoma Presenting as Ruptured Omphalocele
title_full Umbilical Cord Teratoma Presenting as Ruptured Omphalocele
title_fullStr Umbilical Cord Teratoma Presenting as Ruptured Omphalocele
title_full_unstemmed Umbilical Cord Teratoma Presenting as Ruptured Omphalocele
title_short Umbilical Cord Teratoma Presenting as Ruptured Omphalocele
title_sort umbilical cord teratoma presenting as ruptured omphalocele
topic umbilical cord teratoma
omphalocele
abdominal wall defect
url http://www.thieme-connect.de/DOI/DOI?10.1055/s-0041-1741509
work_keys_str_mv AT fabiandoktor umbilicalcordteratomapresentingasrupturedomphalocele
AT janhendrikgosemann umbilicalcordteratomapresentingasrupturedomphalocele
AT peterzimmermann umbilicalcordteratomapresentingasrupturedomphalocele
AT manuelasiekmeyer umbilicalcordteratomapresentingasrupturedomphalocele
AT holgerstepan umbilicalcordteratomapresentingasrupturedomphalocele
AT martinlacher umbilicalcordteratomapresentingasrupturedomphalocele