An ex vivo model contributing to the diagnosis and evaluation of new drugs in cystic fibrosis

An ex vivo model contributing to the diagnosis and evaluation of new drugs in cystic fibrosis

La fibrosi cistica (FC) è una malattia autosomica recessiva causata da mutazioni nel gene CFTR (Cystic Fibrosis Transmembrane conductance Regulator). Finora sono state descritte circa 2000 mutazioni, ma per la maggior parte di esse è difficile definirne leffetto senza complesse procedure in vi...

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Bibliographic Details
Main Authors:	A.M. Di Lullo, M. Scorza, F. Amato, M. Comegna, V. Raia, L. Maiuri, G. Ilardi, E. Cantone, G. Castaldo, M. Iengo
Format:	Article
Language:	English
Published:	Pacini Editore Srl 2017-06-01
Series:	Acta Otorhinolaryngologica Italica
Online Access:	https://www.actaitalica.it/issues/2017/3-2017/06_DiLullo.pdf

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