Pulmonary alveolar proteinosis in children: A case series
Pulmonary alveolar proteinosis, (PAP) is a rare disease of unknown etiology, characterized by accumulation of intraalveolar proteinaceous material which is rich in lipid and positive on periodic acid-Schiff stain. Two clinically different pediatric types have been defined as congenital PAP which is...
| Main Authors: | , , , , , , |
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| Format: | Article |
| Language: | English |
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Wolters Kluwer Medknow Publications
2010-01-01
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| Series: | Journal of Research in Medical Sciences |
| Subjects: | |
| Online Access: | http://www.jmsjournal.net/article.asp?issn=1735-1995;year=2010;volume=15;issue=2;spage=120;epage=124;aulast=Tabatabaei |
| _version_ | 1818696050178785280 |
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| author | Seyyed Ahmad Tabatabaei Abdollah Karimi Sedigheh Rafiee Tabatabaei Badiozzaman Radpay Farzaneh Jadali Farideh Shiva Mana Hadipour Jahromy |
| author_facet | Seyyed Ahmad Tabatabaei Abdollah Karimi Sedigheh Rafiee Tabatabaei Badiozzaman Radpay Farzaneh Jadali Farideh Shiva Mana Hadipour Jahromy |
| author_sort | Seyyed Ahmad Tabatabaei |
| collection | DOAJ |
| description | Pulmonary alveolar proteinosis, (PAP) is a rare disease of unknown etiology, characterized by accumulation of intraalveolar proteinaceous material which is rich in lipid and positive on periodic acid-Schiff stain. Two clinically different pediatric types have been defined as congenital PAP which is fulminant and fatal, and a late-onset PAP which is similar to the adult form and less severe. Eight children with late-onset PAP were hospitalized from 1998 to 2005 in Mofid Children Hospital. Characteristics of these patients and the methods of diagnosis and treatment are presented in this case series. |
| first_indexed | 2024-12-17T13:55:12Z |
| format | Article |
| id | doaj.art-bbd6a1172b8f46ceae3587343739fde6 |
| institution | Directory Open Access Journal |
| issn | 1735-1995 1735-7136 |
| language | English |
| last_indexed | 2024-12-17T13:55:12Z |
| publishDate | 2010-01-01 |
| publisher | Wolters Kluwer Medknow Publications |
| record_format | Article |
| series | Journal of Research in Medical Sciences |
| spelling | doaj.art-bbd6a1172b8f46ceae3587343739fde62022-12-21T21:45:57ZengWolters Kluwer Medknow PublicationsJournal of Research in Medical Sciences1735-19951735-71362010-01-01152120124Pulmonary alveolar proteinosis in children: A case seriesSeyyed Ahmad TabatabaeiAbdollah KarimiSedigheh Rafiee TabatabaeiBadiozzaman RadpayFarzaneh JadaliFarideh ShivaMana Hadipour JahromyPulmonary alveolar proteinosis, (PAP) is a rare disease of unknown etiology, characterized by accumulation of intraalveolar proteinaceous material which is rich in lipid and positive on periodic acid-Schiff stain. Two clinically different pediatric types have been defined as congenital PAP which is fulminant and fatal, and a late-onset PAP which is similar to the adult form and less severe. Eight children with late-onset PAP were hospitalized from 1998 to 2005 in Mofid Children Hospital. Characteristics of these patients and the methods of diagnosis and treatment are presented in this case series.http://www.jmsjournal.net/article.asp?issn=1735-1995;year=2010;volume=15;issue=2;spage=120;epage=124;aulast=TabatabaeiPulmonary Alveolar ProteinosisRespiratory FailureRespiratory DistressChildren |
| spellingShingle | Seyyed Ahmad Tabatabaei Abdollah Karimi Sedigheh Rafiee Tabatabaei Badiozzaman Radpay Farzaneh Jadali Farideh Shiva Mana Hadipour Jahromy Pulmonary alveolar proteinosis in children: A case series Journal of Research in Medical Sciences Pulmonary Alveolar Proteinosis Respiratory Failure Respiratory Distress Children |
| title | Pulmonary alveolar proteinosis in children: A case series |
| title_full | Pulmonary alveolar proteinosis in children: A case series |
| title_fullStr | Pulmonary alveolar proteinosis in children: A case series |
| title_full_unstemmed | Pulmonary alveolar proteinosis in children: A case series |
| title_short | Pulmonary alveolar proteinosis in children: A case series |
| title_sort | pulmonary alveolar proteinosis in children a case series |
| topic | Pulmonary Alveolar Proteinosis Respiratory Failure Respiratory Distress Children |
| url | http://www.jmsjournal.net/article.asp?issn=1735-1995;year=2010;volume=15;issue=2;spage=120;epage=124;aulast=Tabatabaei |
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