Soft tissue sarcoma in neurofibromatosis type 1: A rare case of malignant peripheral nerve sheath tumor of the skin
Malignant peripheral nerve sheath tumor (MPNST) is a rare and often aggressive soft tissue sarcoma originating from the sheaths of peripheral nerves. Approximately 50% of MPNSTs occur in patients with neurofibromatosis (NF). These tumors often present as deep soft tissue lesions, arising from the ne...
| Main Authors: | , , |
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| Format: | Article |
| Language: | English |
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Thieme Medical Publishers, Inc.
2020-01-01
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| Series: | Archives of Plastic Surgery |
| Subjects: | |
| Online Access: | http://www.thieme-connect.de/DOI/DOI?10.5999/aps.2019.01529 |
| _version_ | 1798026261280325632 |
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| author | Young Hun Chung Jin Woo Jang Jae Young Cho |
| author_facet | Young Hun Chung Jin Woo Jang Jae Young Cho |
| author_sort | Young Hun Chung |
| collection | DOAJ |
| description | Malignant peripheral nerve sheath tumor (MPNST) is a rare and often aggressive soft tissue sarcoma originating from the sheaths of peripheral nerves. Approximately 50% of MPNSTs occur in patients with neurofibromatosis (NF). These tumors often present as deep soft tissue lesions, arising from the nerve plexuses of the extremities or from the nerves extending from the trunk. They rarely occur in the skin, especially in patients with NF. Herein, we report our experience with an MPNST of the skin in a patient with NF. |
| first_indexed | 2024-04-11T18:32:26Z |
| format | Article |
| id | doaj.art-bc2d83bf1ad44038a1e7bb15a0086ef0 |
| institution | Directory Open Access Journal |
| issn | 2234-6163 2234-6171 |
| language | English |
| last_indexed | 2024-04-11T18:32:26Z |
| publishDate | 2020-01-01 |
| publisher | Thieme Medical Publishers, Inc. |
| record_format | Article |
| series | Archives of Plastic Surgery |
| spelling | doaj.art-bc2d83bf1ad44038a1e7bb15a0086ef02022-12-22T04:09:25ZengThieme Medical Publishers, Inc.Archives of Plastic Surgery2234-61632234-61712020-01-014701929610.5999/aps.2019.015293706Soft tissue sarcoma in neurofibromatosis type 1: A rare case of malignant peripheral nerve sheath tumor of the skinYoung Hun Chung0Jin Woo Jang1Jae Young Cho2Department of Plastic Surgery, Kyung Hee University Graduate School, Seoul, KoreaDepartment of Plastic Surgery, Kyung Hee University Medical Center, Seoul, KoreaDepartment of Plastic Surgery, Kyung Hee University Medical Center, Seoul, KoreaMalignant peripheral nerve sheath tumor (MPNST) is a rare and often aggressive soft tissue sarcoma originating from the sheaths of peripheral nerves. Approximately 50% of MPNSTs occur in patients with neurofibromatosis (NF). These tumors often present as deep soft tissue lesions, arising from the nerve plexuses of the extremities or from the nerves extending from the trunk. They rarely occur in the skin, especially in patients with NF. Herein, we report our experience with an MPNST of the skin in a patient with NF.http://www.thieme-connect.de/DOI/DOI?10.5999/aps.2019.01529neurofibromatosis 1nerve sheath neoplasmskin neoplasm |
| spellingShingle | Young Hun Chung Jin Woo Jang Jae Young Cho Soft tissue sarcoma in neurofibromatosis type 1: A rare case of malignant peripheral nerve sheath tumor of the skin Archives of Plastic Surgery neurofibromatosis 1 nerve sheath neoplasm skin neoplasm |
| title | Soft tissue sarcoma in neurofibromatosis type 1: A rare case of malignant peripheral nerve sheath tumor of the skin |
| title_full | Soft tissue sarcoma in neurofibromatosis type 1: A rare case of malignant peripheral nerve sheath tumor of the skin |
| title_fullStr | Soft tissue sarcoma in neurofibromatosis type 1: A rare case of malignant peripheral nerve sheath tumor of the skin |
| title_full_unstemmed | Soft tissue sarcoma in neurofibromatosis type 1: A rare case of malignant peripheral nerve sheath tumor of the skin |
| title_short | Soft tissue sarcoma in neurofibromatosis type 1: A rare case of malignant peripheral nerve sheath tumor of the skin |
| title_sort | soft tissue sarcoma in neurofibromatosis type 1 a rare case of malignant peripheral nerve sheath tumor of the skin |
| topic | neurofibromatosis 1 nerve sheath neoplasm skin neoplasm |
| url | http://www.thieme-connect.de/DOI/DOI?10.5999/aps.2019.01529 |
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