A Unique Case of Primary Cutaneous Adenoid Cystic Carcinoma Associated with Aplasia Cutis Congenita in a Four-Year-Old Female: A Case Report

Introduction: Primary cutaneous adenoid-cystic carcinoma (PCACC) is a rare malignant tumour reported in only about 450 cases in the literature, with only two adolescent cases reported. PCACC seems to occur between the fifth and seventh decade of life, and the most frequent regions involved are head...

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Bibliographic Details
Main Authors: Andrea Zulli, Alessandra Martin, Flavio Facchini, Riccardo Coletta, Angela Tamburini, Teresa Oranges, Cesare Filippeschi, Andrea Bassi, Anna Maria Buccoliero, Antonino Morabito
Format: Article
Language:English
Published: MDPI AG 2022-02-01
Series:Children
Subjects:
Online Access:https://www.mdpi.com/2227-9067/9/2/292