Doença pulmonar intersticial associada a bronquiolite respiratória Respiratory bronchilitis-associated interstitial lung disease

A doença pulmonar intersticial associada a bronquiolite respiratória faz parte do espectro anatomopatológico das lesões pulmonares infiltrativas difusas induzidas pela fumaça de cigarro. Raramente tem apresentação clínico-funcional exuberante. Descrevemos dois casos diagnosticados por biópsia pulmon...

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Main Authors: Sílvia CS. Rodrigues, Mauri M. Rodrigues, Ester MC Colleta, Nailê S Rocha, Carlos AC Pereira
Format: Article
Language:English
Published: Sociedade Brasileira de Pneumologia e Tisiologia 2004-12-01
Series:Jornal Brasileiro de Pneumologia
Subjects:
Online Access:http://www.scielo.br/scielo.php?script=sci_arttext&pid=S1806-37132004000600013
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author Sílvia CS. Rodrigues
Mauri M. Rodrigues
Ester MC Colleta
Nailê S Rocha
Carlos AC Pereira
author_facet Sílvia CS. Rodrigues
Mauri M. Rodrigues
Ester MC Colleta
Nailê S Rocha
Carlos AC Pereira
author_sort Sílvia CS. Rodrigues
collection DOAJ
description A doença pulmonar intersticial associada a bronquiolite respiratória faz parte do espectro anatomopatológico das lesões pulmonares infiltrativas difusas induzidas pela fumaça de cigarro. Raramente tem apresentação clínico-funcional exuberante. Descrevemos dois casos diagnosticados por biópsia pulmonar aberta, caracterizados por dispnéia de evolução insidiosa, baqueteamento digital, lesões císticas à tomografia computadorizada e hipoxemia ao exercício. Enfatizamos considerar, em indivíduos tabagistas, a doença pulmonar intersticial associada a bronquiolite respiratória no contexto das pneumopatias intersticiais císticas, juntamente com a linfangioleiomiomatose, o granuloma eosinofílico e a fibrose pulmonar idiopática.<br>Respiratory bronchiolitis-associated interstitial lung disease is one of many within the spectrum of smoking-related diffuse infiltrative lung diseases. The clinical and functional characteristics are typically subtle. Herein, we describe two cases of diagnosed through open-lung biopsy, and characterized by insidious evolution of dyspnea, digital clubbing, cystic lesions on computed tomography scans, and hipoxemia upon exertion. We emphasize that, when smokers are evaluated, it is imprtant to consider a diagnosis of respiratory bronchiolitis-associated interstitial lung disease in the context of interstitial cystitis, as well as in that of lymphangioleiomyomatosis, eosinophilic granuloma and idiophatic pulmonary fibrosis.
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spelling doaj.art-bcab9a22bd4b40e38871e122137a5e7c2022-12-21T17:58:07ZengSociedade Brasileira de Pneumologia e TisiologiaJornal Brasileiro de Pneumologia1806-37131806-37562004-12-0130657458010.1590/S1806-37132004000600013Doença pulmonar intersticial associada a bronquiolite respiratória Respiratory bronchilitis-associated interstitial lung diseaseSílvia CS. RodriguesMauri M. RodriguesEster MC ColletaNailê S RochaCarlos AC PereiraA doença pulmonar intersticial associada a bronquiolite respiratória faz parte do espectro anatomopatológico das lesões pulmonares infiltrativas difusas induzidas pela fumaça de cigarro. Raramente tem apresentação clínico-funcional exuberante. Descrevemos dois casos diagnosticados por biópsia pulmonar aberta, caracterizados por dispnéia de evolução insidiosa, baqueteamento digital, lesões císticas à tomografia computadorizada e hipoxemia ao exercício. Enfatizamos considerar, em indivíduos tabagistas, a doença pulmonar intersticial associada a bronquiolite respiratória no contexto das pneumopatias intersticiais císticas, juntamente com a linfangioleiomiomatose, o granuloma eosinofílico e a fibrose pulmonar idiopática.<br>Respiratory bronchiolitis-associated interstitial lung disease is one of many within the spectrum of smoking-related diffuse infiltrative lung diseases. The clinical and functional characteristics are typically subtle. Herein, we describe two cases of diagnosed through open-lung biopsy, and characterized by insidious evolution of dyspnea, digital clubbing, cystic lesions on computed tomography scans, and hipoxemia upon exertion. We emphasize that, when smokers are evaluated, it is imprtant to consider a diagnosis of respiratory bronchiolitis-associated interstitial lung disease in the context of interstitial cystitis, as well as in that of lymphangioleiomyomatosis, eosinophilic granuloma and idiophatic pulmonary fibrosis.http://www.scielo.br/scielo.php?script=sci_arttext&pid=S1806-37132004000600013TabagismoDoenças pulmonares intersticiaisSmokingInterstitial lung diseasesBronchiolitis
spellingShingle Sílvia CS. Rodrigues
Mauri M. Rodrigues
Ester MC Colleta
Nailê S Rocha
Carlos AC Pereira
Doença pulmonar intersticial associada a bronquiolite respiratória Respiratory bronchilitis-associated interstitial lung disease
Jornal Brasileiro de Pneumologia
Tabagismo
Doenças pulmonares intersticiais
Smoking
Interstitial lung diseases
Bronchiolitis
title Doença pulmonar intersticial associada a bronquiolite respiratória Respiratory bronchilitis-associated interstitial lung disease
title_full Doença pulmonar intersticial associada a bronquiolite respiratória Respiratory bronchilitis-associated interstitial lung disease
title_fullStr Doença pulmonar intersticial associada a bronquiolite respiratória Respiratory bronchilitis-associated interstitial lung disease
title_full_unstemmed Doença pulmonar intersticial associada a bronquiolite respiratória Respiratory bronchilitis-associated interstitial lung disease
title_short Doença pulmonar intersticial associada a bronquiolite respiratória Respiratory bronchilitis-associated interstitial lung disease
title_sort doenca pulmonar intersticial associada a bronquiolite respiratoria respiratory bronchilitis associated interstitial lung disease
topic Tabagismo
Doenças pulmonares intersticiais
Smoking
Interstitial lung diseases
Bronchiolitis
url http://www.scielo.br/scielo.php?script=sci_arttext&pid=S1806-37132004000600013
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