Cytomegalovirus pneumonia in an immunocompetent host with primary ciliary dyskinesia: A case report

Primary ciliary dyskinesia (PCD) is an autosomal-recessive inherited disease caused by mutations in genes involved in ciliary structure and function leading to impaired mucociliary clearance and repeated or chronic, usually bacterial, infections of the upper and lower airways and decreased lung func...

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Main Authors: Vasiliki Epameinondas Georgakopoulou, Dimitrios Mermigkis, Despoina Melemeni, Aikaterini Gkoufa, Christos Damaskos, Nikolaos Garmpis, Anna Garmpi, Nikolaos Trakas, Xanthi Tsiafaki
Format: Article
Language:English
Published: PAGEPress Publications 2021-04-01
Series:Monaldi Archives for Chest Disease
Subjects:
Online Access:https://www.monaldi-archives.org/index.php/macd/article/view/1638
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author Vasiliki Epameinondas Georgakopoulou
Dimitrios Mermigkis
Despoina Melemeni
Aikaterini Gkoufa
Christos Damaskos
Nikolaos Garmpis
Anna Garmpi
Nikolaos Trakas
Xanthi Tsiafaki
author_facet Vasiliki Epameinondas Georgakopoulou
Dimitrios Mermigkis
Despoina Melemeni
Aikaterini Gkoufa
Christos Damaskos
Nikolaos Garmpis
Anna Garmpi
Nikolaos Trakas
Xanthi Tsiafaki
author_sort Vasiliki Epameinondas Georgakopoulou
collection DOAJ
description Primary ciliary dyskinesia (PCD) is an autosomal-recessive inherited disease caused by mutations in genes involved in ciliary structure and function leading to impaired mucociliary clearance and repeated or chronic, usually bacterial, infections of the upper and lower airways and decreased lung function and bronchiectasis. Cytomegalovirus (CMV) is a DNA virus that usually causes subclinical infection and in 10% of the patients causes a mononucleosis-like syndrome. CMV is a causative agent of serious illness in vulnerable immunocompromised groups such as transplant recipients, patients with immunodeficiency or malignancy and neonates. Life-threatening infection due to CMV, including CMV pneumonia, is not common in immunocompetent patients. In this report we describe a case of an otherwise immunocompetent woman, suffering from PCD, who developed severe CMV pneumonia.
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spelling doaj.art-bcb125c5c35f496b970ef5134d9fd66d2022-12-21T17:43:40ZengPAGEPress PublicationsMonaldi Archives for Chest Disease1122-06432532-52642021-04-0110.4081/monaldi.2021.1638Cytomegalovirus pneumonia in an immunocompetent host with primary ciliary dyskinesia: A case reportVasiliki Epameinondas Georgakopoulou0Dimitrios Mermigkis1Despoina Melemeni2Aikaterini Gkoufa3Christos Damaskos4Nikolaos Garmpis5Anna Garmpi6Nikolaos Trakas7Xanthi Tsiafaki8Pulmonology Department, Laiko General Hospital, Athens1st Pulmonology Department Sismanogleio Hospital, Athens1st Pulmonology Department Sismanogleio Hospital, AthensFirst Department of Internal Medicine, Laiko General Hospital, Medical School, National and Kapodistrian University of Athens, AthensSecond Department of Propedeutic Surgery, Laiko General Hospital, Medical School, National and Kapodistrian University of Athens, AthensSecond Department of Propedeutic Surgery, Laiko General Hospital, Medical School, National and Kapodistrian University of Athens, AthensFirst Department of Propedeutic Internal Medicine, Laiko General Hospital, Medical School, National and Kapodistrian University of Athens, AthensBiochemistry Department, Sismanogleio Hospital, Athens1st Pulmonology Department Sismanogleio Hospital, AthensPrimary ciliary dyskinesia (PCD) is an autosomal-recessive inherited disease caused by mutations in genes involved in ciliary structure and function leading to impaired mucociliary clearance and repeated or chronic, usually bacterial, infections of the upper and lower airways and decreased lung function and bronchiectasis. Cytomegalovirus (CMV) is a DNA virus that usually causes subclinical infection and in 10% of the patients causes a mononucleosis-like syndrome. CMV is a causative agent of serious illness in vulnerable immunocompromised groups such as transplant recipients, patients with immunodeficiency or malignancy and neonates. Life-threatening infection due to CMV, including CMV pneumonia, is not common in immunocompetent patients. In this report we describe a case of an otherwise immunocompetent woman, suffering from PCD, who developed severe CMV pneumonia.https://www.monaldi-archives.org/index.php/macd/article/view/1638CMV infectionpneumoniaprimary ciliary dyskinesia
spellingShingle Vasiliki Epameinondas Georgakopoulou
Dimitrios Mermigkis
Despoina Melemeni
Aikaterini Gkoufa
Christos Damaskos
Nikolaos Garmpis
Anna Garmpi
Nikolaos Trakas
Xanthi Tsiafaki
Cytomegalovirus pneumonia in an immunocompetent host with primary ciliary dyskinesia: A case report
Monaldi Archives for Chest Disease
CMV infection
pneumonia
primary ciliary dyskinesia
title Cytomegalovirus pneumonia in an immunocompetent host with primary ciliary dyskinesia: A case report
title_full Cytomegalovirus pneumonia in an immunocompetent host with primary ciliary dyskinesia: A case report
title_fullStr Cytomegalovirus pneumonia in an immunocompetent host with primary ciliary dyskinesia: A case report
title_full_unstemmed Cytomegalovirus pneumonia in an immunocompetent host with primary ciliary dyskinesia: A case report
title_short Cytomegalovirus pneumonia in an immunocompetent host with primary ciliary dyskinesia: A case report
title_sort cytomegalovirus pneumonia in an immunocompetent host with primary ciliary dyskinesia a case report
topic CMV infection
pneumonia
primary ciliary dyskinesia
url https://www.monaldi-archives.org/index.php/macd/article/view/1638
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