Transpalatine Route for the Correction of Transsphenoidal Encephalocele in a Child: A Case Report and Literature Review
Abstract Introduction Transsphenoidal encephalocele is a rare neural tube defect characterized by the herniation of meninges and eventually of parts of the brain through a bony defect in the sphenoid bone. The clinical presentation is variable, and surgical treatment is controversial....
| Main Authors: | , |
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| Format: | Article |
| Language: | English |
| Published: |
Thieme Revinter Publicações Ltda.
2017-12-01
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| Series: | Brazilian Neurosurgery |
| Subjects: | |
| Online Access: | http://www.thieme-connect.de/DOI/DOI?10.1055/s-0037-1607999 |
| _version_ | 1818320721670045696 |
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| author | Aldo José F. da Silva Fabrício A. C. Lopes |
| author_facet | Aldo José F. da Silva Fabrício A. C. Lopes |
| author_sort | Aldo José F. da Silva |
| collection | DOAJ |
| description | Abstract
Introduction Transsphenoidal encephalocele is a rare neural tube defect characterized by the herniation of meninges and eventually of parts of the brain through a bony defect in the sphenoid bone. The clinical presentation is variable, and surgical treatment is controversial.
Case Report This report describes the case of an 8-month-old female child diagnosed with transsphenoidal encephalocele. The child presented with obstruction of the upper airways and was fed via a nasogastric tube but did not present changes in the hypothalamic-pituitary-axis. The patient underwent surgery with the transsphenoidal–transpalatine route, with an excellent outcome and without fistulas or infections.
Conclusions Although transsphenoidal encephalocele is a rare congenital anomaly, the transsphenoidal–transpalatine route for the correction of this type of encephalocele is a safe option and produces a favorable outcome in pediatric patients. |
| first_indexed | 2024-12-13T10:29:31Z |
| format | Article |
| id | doaj.art-bd1dbc45252948fe9c12c046b9ad59a7 |
| institution | Directory Open Access Journal |
| issn | 0103-5355 2359-5922 |
| language | English |
| last_indexed | 2024-12-13T10:29:31Z |
| publishDate | 2017-12-01 |
| publisher | Thieme Revinter Publicações Ltda. |
| record_format | Article |
| series | Brazilian Neurosurgery |
| spelling | doaj.art-bd1dbc45252948fe9c12c046b9ad59a72022-12-21T23:50:55ZengThieme Revinter Publicações Ltda.Brazilian Neurosurgery0103-53552359-59222017-12-01360423423710.1055/s-0037-1607999Transpalatine Route for the Correction of Transsphenoidal Encephalocele in a Child: A Case Report and Literature ReviewAldo José F. da Silva0Fabrício A. C. Lopes1Division of Pediatric Neurosurgery, General State Hospital (GSH), Maceió, AL, BrazilDivision of Pediatric Neurosurgery, General State Hospital (GSH), Maceió, AL, BrazilAbstract Introduction Transsphenoidal encephalocele is a rare neural tube defect characterized by the herniation of meninges and eventually of parts of the brain through a bony defect in the sphenoid bone. The clinical presentation is variable, and surgical treatment is controversial. Case Report This report describes the case of an 8-month-old female child diagnosed with transsphenoidal encephalocele. The child presented with obstruction of the upper airways and was fed via a nasogastric tube but did not present changes in the hypothalamic-pituitary-axis. The patient underwent surgery with the transsphenoidal–transpalatine route, with an excellent outcome and without fistulas or infections. Conclusions Although transsphenoidal encephalocele is a rare congenital anomaly, the transsphenoidal–transpalatine route for the correction of this type of encephalocele is a safe option and produces a favorable outcome in pediatric patients.http://www.thieme-connect.de/DOI/DOI?10.1055/s-0037-1607999encephaloceletranspalatinetranssphenoidalmeningoceles |
| spellingShingle | Aldo José F. da Silva Fabrício A. C. Lopes Transpalatine Route for the Correction of Transsphenoidal Encephalocele in a Child: A Case Report and Literature Review Brazilian Neurosurgery encephalocele transpalatine transsphenoidal meningoceles |
| title | Transpalatine Route for the Correction of Transsphenoidal Encephalocele in a Child: A Case Report and Literature Review |
| title_full | Transpalatine Route for the Correction of Transsphenoidal Encephalocele in a Child: A Case Report and Literature Review |
| title_fullStr | Transpalatine Route for the Correction of Transsphenoidal Encephalocele in a Child: A Case Report and Literature Review |
| title_full_unstemmed | Transpalatine Route for the Correction of Transsphenoidal Encephalocele in a Child: A Case Report and Literature Review |
| title_short | Transpalatine Route for the Correction of Transsphenoidal Encephalocele in a Child: A Case Report and Literature Review |
| title_sort | transpalatine route for the correction of transsphenoidal encephalocele in a child a case report and literature review |
| topic | encephalocele transpalatine transsphenoidal meningoceles |
| url | http://www.thieme-connect.de/DOI/DOI?10.1055/s-0037-1607999 |
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