Scleredema associated with Sjögren’s syndrome

AbstractScleredema adultorum of Buschke is a rare disorder characterized by diffuse swelling and non-pitting induration of the skin usually involving the face, neck, arms and upper trunk. It has been associated with previous infectious diseases, diabetes, paraproteinemia and, more rarely, malignant...

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Main Authors: João Alves, Tiago Judas, Tiago Ferreira, Diogo Matos, Elvira Bártolo
Format: Article
Language:English
Published: Sociedade Brasileira de Dermatologia 2015-06-01
Series:Anais Brasileiros de Dermatologia
Subjects:
Online Access:http://www.scielo.br/pdf/abd/v90n3s1/0365-0596-abd-90-03-s1-0081.pdf
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author João Alves
Tiago Judas
Tiago Ferreira
Diogo Matos
Elvira Bártolo
author_facet João Alves
Tiago Judas
Tiago Ferreira
Diogo Matos
Elvira Bártolo
author_sort João Alves
collection DOAJ
description AbstractScleredema adultorum of Buschke is a rare disorder characterized by diffuse swelling and non-pitting induration of the skin usually involving the face, neck, arms and upper trunk. It has been associated with previous infectious diseases, diabetes, paraproteinemia and, more rarely, malignant neoplasms or autoimmune disorders. We report the case of a 30-year-old man who presented with a 2-year history of scleredema. Further investigation led to the diagnosis of primary Sjögren’s syndrome. The association between scleredema and autoimmune disorders has been rarely seen. To our knowledge, there are no other reports describing the association between primary Sjögren’s syndrome and scleredema adultorum of Buschke.
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spelling doaj.art-be34c9c2e73e4126ad31cbd3e4782c2a2022-12-21T19:23:27ZengSociedade Brasileira de DermatologiaAnais Brasileiros de Dermatologia0365-05962015-06-01903 suppl 1818310.1590/abd1806-4841.20153779Scleredema associated with Sjögren’s syndromeJoão AlvesTiago JudasTiago FerreiraDiogo MatosElvira BártoloAbstractScleredema adultorum of Buschke is a rare disorder characterized by diffuse swelling and non-pitting induration of the skin usually involving the face, neck, arms and upper trunk. It has been associated with previous infectious diseases, diabetes, paraproteinemia and, more rarely, malignant neoplasms or autoimmune disorders. We report the case of a 30-year-old man who presented with a 2-year history of scleredema. Further investigation led to the diagnosis of primary Sjögren’s syndrome. The association between scleredema and autoimmune disorders has been rarely seen. To our knowledge, there are no other reports describing the association between primary Sjögren’s syndrome and scleredema adultorum of Buschke.http://www.scielo.br/pdf/abd/v90n3s1/0365-0596-abd-90-03-s1-0081.pdfAutoimmune diseasesMucinosesScleredema adultorum
spellingShingle João Alves
Tiago Judas
Tiago Ferreira
Diogo Matos
Elvira Bártolo
Scleredema associated with Sjögren’s syndrome
Anais Brasileiros de Dermatologia
Autoimmune diseases
Mucinoses
Scleredema adultorum
title Scleredema associated with Sjögren’s syndrome
title_full Scleredema associated with Sjögren’s syndrome
title_fullStr Scleredema associated with Sjögren’s syndrome
title_full_unstemmed Scleredema associated with Sjögren’s syndrome
title_short Scleredema associated with Sjögren’s syndrome
title_sort scleredema associated with sjogren s syndrome
topic Autoimmune diseases
Mucinoses
Scleredema adultorum
url http://www.scielo.br/pdf/abd/v90n3s1/0365-0596-abd-90-03-s1-0081.pdf
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