Scleredema associated with Sjögren’s syndrome
AbstractScleredema adultorum of Buschke is a rare disorder characterized by diffuse swelling and non-pitting induration of the skin usually involving the face, neck, arms and upper trunk. It has been associated with previous infectious diseases, diabetes, paraproteinemia and, more rarely, malignant...
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Format: | Article |
Language: | English |
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Sociedade Brasileira de Dermatologia
2015-06-01
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Series: | Anais Brasileiros de Dermatologia |
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Online Access: | http://www.scielo.br/pdf/abd/v90n3s1/0365-0596-abd-90-03-s1-0081.pdf |
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author | João Alves Tiago Judas Tiago Ferreira Diogo Matos Elvira Bártolo |
author_facet | João Alves Tiago Judas Tiago Ferreira Diogo Matos Elvira Bártolo |
author_sort | João Alves |
collection | DOAJ |
description | AbstractScleredema adultorum of Buschke is a rare disorder characterized by diffuse swelling and non-pitting induration of the skin usually involving the face, neck, arms and upper trunk. It has been associated with previous infectious diseases, diabetes, paraproteinemia and, more rarely, malignant neoplasms or autoimmune disorders. We report the case of a 30-year-old man who presented with a 2-year history of scleredema. Further investigation led to the diagnosis of primary Sjögren’s syndrome. The association between scleredema and autoimmune disorders has been rarely seen. To our knowledge, there are no other reports describing the association between primary Sjögren’s syndrome and scleredema adultorum of Buschke. |
first_indexed | 2024-12-20T23:24:03Z |
format | Article |
id | doaj.art-be34c9c2e73e4126ad31cbd3e4782c2a |
institution | Directory Open Access Journal |
issn | 0365-0596 |
language | English |
last_indexed | 2024-12-20T23:24:03Z |
publishDate | 2015-06-01 |
publisher | Sociedade Brasileira de Dermatologia |
record_format | Article |
series | Anais Brasileiros de Dermatologia |
spelling | doaj.art-be34c9c2e73e4126ad31cbd3e4782c2a2022-12-21T19:23:27ZengSociedade Brasileira de DermatologiaAnais Brasileiros de Dermatologia0365-05962015-06-01903 suppl 1818310.1590/abd1806-4841.20153779Scleredema associated with Sjögren’s syndromeJoão AlvesTiago JudasTiago FerreiraDiogo MatosElvira BártoloAbstractScleredema adultorum of Buschke is a rare disorder characterized by diffuse swelling and non-pitting induration of the skin usually involving the face, neck, arms and upper trunk. It has been associated with previous infectious diseases, diabetes, paraproteinemia and, more rarely, malignant neoplasms or autoimmune disorders. We report the case of a 30-year-old man who presented with a 2-year history of scleredema. Further investigation led to the diagnosis of primary Sjögren’s syndrome. The association between scleredema and autoimmune disorders has been rarely seen. To our knowledge, there are no other reports describing the association between primary Sjögren’s syndrome and scleredema adultorum of Buschke.http://www.scielo.br/pdf/abd/v90n3s1/0365-0596-abd-90-03-s1-0081.pdfAutoimmune diseasesMucinosesScleredema adultorum |
spellingShingle | João Alves Tiago Judas Tiago Ferreira Diogo Matos Elvira Bártolo Scleredema associated with Sjögren’s syndrome Anais Brasileiros de Dermatologia Autoimmune diseases Mucinoses Scleredema adultorum |
title | Scleredema associated with Sjögren’s syndrome |
title_full | Scleredema associated with Sjögren’s syndrome |
title_fullStr | Scleredema associated with Sjögren’s syndrome |
title_full_unstemmed | Scleredema associated with Sjögren’s syndrome |
title_short | Scleredema associated with Sjögren’s syndrome |
title_sort | scleredema associated with sjogren s syndrome |
topic | Autoimmune diseases Mucinoses Scleredema adultorum |
url | http://www.scielo.br/pdf/abd/v90n3s1/0365-0596-abd-90-03-s1-0081.pdf |
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