Treatment of paroxysmal nocturnal hemoglobinuria

Treatment of paroxysmal nocturnal hemoglobinuria

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Paroxysmal nocturnal hemoglobinuria (PNH) is a rare, life‑threatening clonal hematological disorder caused by an acquired mutation in the phosphatidylinositol glucan (PIG)-A gene. PNH is characterized by chronic intravascular hemolysis, marrow failure, thrombophilia and other severe clinical syndrom...

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Bibliographic Details
Main Authors:	I. A. Lisukov, A. D. Kulagin, B. V. Afanasyev
Format:	Article
Language:	Russian
Published:	ABV-press 2014-07-01
Series:	Онкогематология
Subjects:	paroxysmal nocturnal hemoglobinuria allogeneic bone marrow transplantation eculizumab
Online Access:	https://oncohematology.abvpress.ru/ongm/article/view/54

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