Malignant Evolution of Schnitzler Syndrome to Waldenström Macroglobulinemia: a Case Report
Introduction: Schnitzler syndrome (SchS), first described in 1972, is a rare autoinflammatory condition characterized by chronic urticaria and monoclonal gammopathy of IgM or, exceptionally, IgG profile. Additional features include recurrent fever, evidence of abnormal bone remodeling, a neutrophili...
| Main Authors: | , , , |
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| Format: | Article |
| Language: | English |
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Sciendo
2022-09-01
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| Series: | Journal of Interdisciplinary Medicine |
| Subjects: | |
| Online Access: | https://doi.org/10.2478/jim-2022-0011 |
| _version_ | 1828180408065327104 |
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| author | Man Cristina-Alexandra László Nimród Horváth Emőke Demian Smaranda |
| author_facet | Man Cristina-Alexandra László Nimród Horváth Emőke Demian Smaranda |
| author_sort | Man Cristina-Alexandra |
| collection | DOAJ |
| description | Introduction: Schnitzler syndrome (SchS), first described in 1972, is a rare autoinflammatory condition characterized by chronic urticaria and monoclonal gammopathy of IgM or, exceptionally, IgG profile. Additional features include recurrent fever, evidence of abnormal bone remodeling, a neutrophilic dermal infiltrate on skin biopsy, leukocytosis or elevated C-reactive protein, according to the Strasbourg criteria. |
| first_indexed | 2024-04-12T05:44:32Z |
| format | Article |
| id | doaj.art-bf4160cec4134b9c95962d0f1d9c8820 |
| institution | Directory Open Access Journal |
| issn | 2501-8132 |
| language | English |
| last_indexed | 2024-04-12T05:44:32Z |
| publishDate | 2022-09-01 |
| publisher | Sciendo |
| record_format | Article |
| series | Journal of Interdisciplinary Medicine |
| spelling | doaj.art-bf4160cec4134b9c95962d0f1d9c88202022-12-22T03:45:29ZengSciendoJournal of Interdisciplinary Medicine2501-81322022-09-0173747710.2478/jim-2022-0011Malignant Evolution of Schnitzler Syndrome to Waldenström Macroglobulinemia: a Case ReportMan Cristina-Alexandra0László Nimród1Horváth Emőke2Demian Smaranda3Pneumology Clinic, County Clinical Hospital, Târgu Mureș, RomaniaPneumology Clinic, County Clinical Hospital, Târgu Mureș, RomaniaDepartment of Morphopathology, Emergency County Clinical Hospital, Târgu Mureș, Romania“George Emil Palade” University of Medicine, Pharmacy, Science and Technology, Târgu Mureș, RomaniaIntroduction: Schnitzler syndrome (SchS), first described in 1972, is a rare autoinflammatory condition characterized by chronic urticaria and monoclonal gammopathy of IgM or, exceptionally, IgG profile. Additional features include recurrent fever, evidence of abnormal bone remodeling, a neutrophilic dermal infiltrate on skin biopsy, leukocytosis or elevated C-reactive protein, according to the Strasbourg criteria.https://doi.org/10.2478/jim-2022-0011schnitzler syndromewaldenström macroglobulinemiaigm monoclonal gammopathyautoinflammatory diseasechronic urticaria |
| spellingShingle | Man Cristina-Alexandra László Nimród Horváth Emőke Demian Smaranda Malignant Evolution of Schnitzler Syndrome to Waldenström Macroglobulinemia: a Case Report Journal of Interdisciplinary Medicine schnitzler syndrome waldenström macroglobulinemia igm monoclonal gammopathy autoinflammatory disease chronic urticaria |
| title | Malignant Evolution of Schnitzler Syndrome to Waldenström Macroglobulinemia: a Case Report |
| title_full | Malignant Evolution of Schnitzler Syndrome to Waldenström Macroglobulinemia: a Case Report |
| title_fullStr | Malignant Evolution of Schnitzler Syndrome to Waldenström Macroglobulinemia: a Case Report |
| title_full_unstemmed | Malignant Evolution of Schnitzler Syndrome to Waldenström Macroglobulinemia: a Case Report |
| title_short | Malignant Evolution of Schnitzler Syndrome to Waldenström Macroglobulinemia: a Case Report |
| title_sort | malignant evolution of schnitzler syndrome to waldenstrom macroglobulinemia a case report |
| topic | schnitzler syndrome waldenström macroglobulinemia igm monoclonal gammopathy autoinflammatory disease chronic urticaria |
| url | https://doi.org/10.2478/jim-2022-0011 |
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