Keratosis follicularis spinulosa decalvans associated with acne keloidalis nuchae
Keratosis follicularis spinulosa decalvans (KFSD) is a keratinization disorder characterized by diffuse follicular hyperkeratosis, progressive cicatricial alopecia, corneal dystrophy, and photophobia. Acne keloidalis nuchae (AKN) is a syndrome of chronic folliculitis that manifests as follicular-bas...
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Our Dermatology Online
2014-04-01
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Series: | Nasza Dermatologia Online |
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Online Access: | http://www.odermatol.com/issue-in-html/2014-2-10-kfsd/ |
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author | Ilteris Oguz Topal Ilknur Mansuroglu Sahin Betül Berberoglu Mehmet Ozer |
author_facet | Ilteris Oguz Topal Ilknur Mansuroglu Sahin Betül Berberoglu Mehmet Ozer |
author_sort | Ilteris Oguz Topal |
collection | DOAJ |
description | Keratosis follicularis spinulosa decalvans (KFSD) is a keratinization disorder characterized by diffuse follicular hyperkeratosis, progressive cicatricial alopecia, corneal dystrophy, and photophobia. Acne keloidalis nuchae (AKN) is a syndrome of chronic folliculitis that manifests as follicular-based pustules and papules on the occipital region of the scalp, which may eventually lead to cicatricial alopecia. Various diseases such as cutis laksa, deafness, aminoaciduria, mental retardation, and atopy have been reported to be associated with KFSD, but AKN is a rare cutaneous manifestation. Herein, we report the case of a patient with KFSD associated with AKN. He was presented to our clinic with follicular-based pustules and papules that had been progressively advancing for five years that were now manifesting as cicatricial alopecia. |
first_indexed | 2024-04-13T02:56:18Z |
format | Article |
id | doaj.art-bf52ca63b23d4106a7cd78b46c8c78e5 |
institution | Directory Open Access Journal |
issn | 2081-9390 |
language | English |
last_indexed | 2024-04-13T02:56:18Z |
publishDate | 2014-04-01 |
publisher | Our Dermatology Online |
record_format | Article |
series | Nasza Dermatologia Online |
spelling | doaj.art-bf52ca63b23d4106a7cd78b46c8c78e52022-12-22T03:05:39ZengOur Dermatology OnlineNasza Dermatologia Online2081-93902014-04-015215115410.7241/ourd.20142.36Keratosis follicularis spinulosa decalvans associated with acne keloidalis nuchaeIlteris Oguz Topal0Ilknur Mansuroglu Sahin1Betül Berberoglu2Mehmet Ozer3Department of Dermatology, Okmeydani Research and Training Hospital, Istanbul, Turkey Department of Pathology, Okmeydani Research and Training Hospital, Istanbul, Turkey Department of Pathology, Batman State Hospital, Istanbul, TurkeyDepartment of Pathology, Okmeydani Research and Training Hospital, Istanbul, Turkey Keratosis follicularis spinulosa decalvans (KFSD) is a keratinization disorder characterized by diffuse follicular hyperkeratosis, progressive cicatricial alopecia, corneal dystrophy, and photophobia. Acne keloidalis nuchae (AKN) is a syndrome of chronic folliculitis that manifests as follicular-based pustules and papules on the occipital region of the scalp, which may eventually lead to cicatricial alopecia. Various diseases such as cutis laksa, deafness, aminoaciduria, mental retardation, and atopy have been reported to be associated with KFSD, but AKN is a rare cutaneous manifestation. Herein, we report the case of a patient with KFSD associated with AKN. He was presented to our clinic with follicular-based pustules and papules that had been progressively advancing for five years that were now manifesting as cicatricial alopecia.http://www.odermatol.com/issue-in-html/2014-2-10-kfsd/Keratosis folliculariscicatricial alopeciaacne keloidalis nuchae |
spellingShingle | Ilteris Oguz Topal Ilknur Mansuroglu Sahin Betül Berberoglu Mehmet Ozer Keratosis follicularis spinulosa decalvans associated with acne keloidalis nuchae Nasza Dermatologia Online Keratosis follicularis cicatricial alopecia acne keloidalis nuchae |
title | Keratosis follicularis spinulosa decalvans associated with acne keloidalis nuchae |
title_full | Keratosis follicularis spinulosa decalvans associated with acne keloidalis nuchae |
title_fullStr | Keratosis follicularis spinulosa decalvans associated with acne keloidalis nuchae |
title_full_unstemmed | Keratosis follicularis spinulosa decalvans associated with acne keloidalis nuchae |
title_short | Keratosis follicularis spinulosa decalvans associated with acne keloidalis nuchae |
title_sort | keratosis follicularis spinulosa decalvans associated with acne keloidalis nuchae |
topic | Keratosis follicularis cicatricial alopecia acne keloidalis nuchae |
url | http://www.odermatol.com/issue-in-html/2014-2-10-kfsd/ |
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