Surgical Repair of Atrial Septal Defect and Lung Lobe Resection for Pulmonary Sequestration and Cystic Malformation in One Stage: A Case Report
Incidence of congenital cystic malformation of lungs ranges from 1 in 11,000 to 1 in 35,000 live birth. Concurrence of Congenital Pulmonary Airway Malformation (CPAM) with congenital heart disease is even infrequent. Even rarer, is the incidence of congenital pulmonary vascular and cystic parenchy...
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JCDR Research and Publications Private Limited
2022-10-01
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| Series: | Journal of Clinical and Diagnostic Research |
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| Online Access: | https://jcdr.net/articles/PDF/16921/56689_CE(AnK)_F(KM)_PF1(SC_SS)_PFA(SS)_PB(SC_SS)_PN(SS).pdf |
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| author | Lakshmi Sinha Debmalya Saha Sayyed Ehtesham Hussain Naqvi Muhammad Abid Geelani Vishnu Datt |
| author_facet | Lakshmi Sinha Debmalya Saha Sayyed Ehtesham Hussain Naqvi Muhammad Abid Geelani Vishnu Datt |
| author_sort | Lakshmi Sinha |
| collection | DOAJ |
| description | Incidence of congenital cystic malformation of lungs ranges from 1 in 11,000 to 1 in 35,000 live birth. Concurrence of Congenital
Pulmonary Airway Malformation (CPAM) with congenital heart disease is even infrequent. Even rarer, is the incidence of congenital
pulmonary vascular and cystic parenchymal lesions with cardiac defects. The non functioning lung tissue is separated from
bronchial tree and vascularised by aberrant artery from the systemic circulation. Simultaneous repair of cardiac and pulmonary
defects, though challenging, but are preferable because of surgery being done in single stage with better cosmesis. A 10-yearold
female child presented to the hospital with recurrent chest infections and respiratory distress while running since five years
of age. The patient underwent atrial septal defect closure and right lower lobectomy for CPAM in one stage through midline
sternotomy. We conclude that such complex cases can be managed successfully with meticulous planning and multidisciplinary
team approach. |
| first_indexed | 2024-04-10T07:26:44Z |
| format | Article |
| id | doaj.art-bfaab1ad1dd9435ea3e43e64d4abd083 |
| institution | Directory Open Access Journal |
| issn | 2249-782X 0973-709X |
| language | English |
| last_indexed | 2024-04-10T07:26:44Z |
| publishDate | 2022-10-01 |
| publisher | JCDR Research and Publications Private Limited |
| record_format | Article |
| series | Journal of Clinical and Diagnostic Research |
| spelling | doaj.art-bfaab1ad1dd9435ea3e43e64d4abd0832023-02-24T05:59:23ZengJCDR Research and Publications Private LimitedJournal of Clinical and Diagnostic Research2249-782X0973-709X2022-10-011610PD04PD0610.7860/JCDR/2022/56689.16921Surgical Repair of Atrial Septal Defect and Lung Lobe Resection for Pulmonary Sequestration and Cystic Malformation in One Stage: A Case ReportLakshmi Sinha0Debmalya Saha1Sayyed Ehtesham Hussain Naqvi2Muhammad Abid Geelani3Vishnu Datt4Resident, Department of Cardiothoracic Vascular Surgery, Govind Ballabh Pant Hospital, New Delhi, India.Resident, Department of Cardiothoracic Vascular Surgery, Govind Ballabh Pant Hospital New Delhi, India.Associate Professor, Department of Cardiothoracic Vascular Surgery, Govind Ballabh Pant Hospital, New Delhi, India.Professor, Director and Head, Department of Cardiothoracic Vascular Surgery, Govind Ballabh Pant Hospital, New Delhi, India.Professor, Director and Head Department of Anaesthesiology, Govind Ballabh Pant Hospital, New Delhi, India.Incidence of congenital cystic malformation of lungs ranges from 1 in 11,000 to 1 in 35,000 live birth. Concurrence of Congenital Pulmonary Airway Malformation (CPAM) with congenital heart disease is even infrequent. Even rarer, is the incidence of congenital pulmonary vascular and cystic parenchymal lesions with cardiac defects. The non functioning lung tissue is separated from bronchial tree and vascularised by aberrant artery from the systemic circulation. Simultaneous repair of cardiac and pulmonary defects, though challenging, but are preferable because of surgery being done in single stage with better cosmesis. A 10-yearold female child presented to the hospital with recurrent chest infections and respiratory distress while running since five years of age. The patient underwent atrial septal defect closure and right lower lobectomy for CPAM in one stage through midline sternotomy. We conclude that such complex cases can be managed successfully with meticulous planning and multidisciplinary team approach.https://jcdr.net/articles/PDF/16921/56689_CE(AnK)_F(KM)_PF1(SC_SS)_PFA(SS)_PB(SC_SS)_PN(SS).pdfcongenital pulmonary airway malformationcongenital heart diseasecongenital cystic adenomatoid malformationright lower lobectomy |
| spellingShingle | Lakshmi Sinha Debmalya Saha Sayyed Ehtesham Hussain Naqvi Muhammad Abid Geelani Vishnu Datt Surgical Repair of Atrial Septal Defect and Lung Lobe Resection for Pulmonary Sequestration and Cystic Malformation in One Stage: A Case Report Journal of Clinical and Diagnostic Research congenital pulmonary airway malformation congenital heart disease congenital cystic adenomatoid malformation right lower lobectomy |
| title | Surgical Repair of Atrial Septal Defect and Lung Lobe Resection for Pulmonary Sequestration and Cystic Malformation in One Stage: A Case Report |
| title_full | Surgical Repair of Atrial Septal Defect and Lung Lobe Resection for Pulmonary Sequestration and Cystic Malformation in One Stage: A Case Report |
| title_fullStr | Surgical Repair of Atrial Septal Defect and Lung Lobe Resection for Pulmonary Sequestration and Cystic Malformation in One Stage: A Case Report |
| title_full_unstemmed | Surgical Repair of Atrial Septal Defect and Lung Lobe Resection for Pulmonary Sequestration and Cystic Malformation in One Stage: A Case Report |
| title_short | Surgical Repair of Atrial Septal Defect and Lung Lobe Resection for Pulmonary Sequestration and Cystic Malformation in One Stage: A Case Report |
| title_sort | surgical repair of atrial septal defect and lung lobe resection for pulmonary sequestration and cystic malformation in one stage a case report |
| topic | congenital pulmonary airway malformation congenital heart disease congenital cystic adenomatoid malformation right lower lobectomy |
| url | https://jcdr.net/articles/PDF/16921/56689_CE(AnK)_F(KM)_PF1(SC_SS)_PFA(SS)_PB(SC_SS)_PN(SS).pdf |
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