Pleuroparenchymal Fibroelastosis-like Lesions in Clinical Practice: A Rare Entity? Review of a Radiological Database

<b><i>Background:</i></b> Pleuroparenchymal Fibroelastosis (PPFE) is a rare disease that consists of elastofibrosis that involves the pleura and subpleural lung parenchyma; it is an unusual pulmonary disease with unique clinical, radiological and pathological characteristics....

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Main Authors: Francesco Gentili, Vito Di Martino, Marta Forestieri, Francesco Mazzei, Susanna Guerrini, Elena Bargagli, Antonietta Gerardina Sisinni, Luca Volterrani, Maria Antonietta Mazzei
Format: Article
Language:English
Published: MDPI AG 2023-05-01
Series:Diagnostics
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Online Access:https://www.mdpi.com/2075-4418/13/9/1627

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