Type IVA choledochal cyst: a rare cause of cirrhosis in adults
Abstract Background Choledochal cysts (CDCs) are characterized by congenital cystic dilations of the intrahepatic or extrahepatic bile ducts or both. CDCs are very rarely reported in sub-Saharan Africa. This congenital anomaly of the bile ducts is rarely discovered at the stage of advanced chronic l...
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| Format: | Article |
| Language: | English |
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SpringerOpen
2022-01-01
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| Series: | The Egyptian Journal of Internal Medicine |
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| Online Access: | https://doi.org/10.1186/s43162-022-00102-2 |
| _version_ | 1819261206257467392 |
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| author | Chantelli Iamblaudiot Razafindrazoto Andry Lalaina Rinà Rakotozafindrabe Sakaiza Malala Randrianambininjanahary Nitah Harivony Randriamifidy Domoina Harivonjy Hasina Laingonirina Sonny Maherison Lova Hasina Ny Ony Narindra Rajaonarison Tovo Harimanana Rabenjanahary Soloniaina Hélio Razafimahefa Rado Manitrala Ramanampamonjy |
| author_facet | Chantelli Iamblaudiot Razafindrazoto Andry Lalaina Rinà Rakotozafindrabe Sakaiza Malala Randrianambininjanahary Nitah Harivony Randriamifidy Domoina Harivonjy Hasina Laingonirina Sonny Maherison Lova Hasina Ny Ony Narindra Rajaonarison Tovo Harimanana Rabenjanahary Soloniaina Hélio Razafimahefa Rado Manitrala Ramanampamonjy |
| author_sort | Chantelli Iamblaudiot Razafindrazoto |
| collection | DOAJ |
| description | Abstract Background Choledochal cysts (CDCs) are characterized by congenital cystic dilations of the intrahepatic or extrahepatic bile ducts or both. CDCs are very rarely reported in sub-Saharan Africa. This congenital anomaly of the bile ducts is rarely discovered at the stage of advanced chronic liver disease with portal hypertension. We report the first Malagasy case of a type IVA choledochal cyst discovered during an etiological work-up of cirrhosis. Case presentation A 23-year-old woman was hospitalized for jaundice and ascites. Biological and radiological investigations have led to the diagnosis of secondary biliary cirrhosis due to type IVA choledochal cyst. In view of the severity of the liver damage (Child-Pugh C score), a collegial decision (hepato-gastroenterologists and visceral surgeons) had rejected surgical intervention and opted only for the management of cirrhotic decompensation. Conclusion A type IVA choledochal cyst is a possible etiology of advanced chronic liver disease. |
| first_indexed | 2024-12-23T19:38:07Z |
| format | Article |
| id | doaj.art-c04b228e64e140c891854db21b142dd6 |
| institution | Directory Open Access Journal |
| issn | 1110-7782 2090-9098 |
| language | English |
| last_indexed | 2024-12-23T19:38:07Z |
| publishDate | 2022-01-01 |
| publisher | SpringerOpen |
| record_format | Article |
| series | The Egyptian Journal of Internal Medicine |
| spelling | doaj.art-c04b228e64e140c891854db21b142dd62022-12-21T17:33:45ZengSpringerOpenThe Egyptian Journal of Internal Medicine1110-77822090-90982022-01-013411510.1186/s43162-022-00102-2Type IVA choledochal cyst: a rare cause of cirrhosis in adultsChantelli Iamblaudiot Razafindrazoto0Andry Lalaina Rinà Rakotozafindrabe1Sakaiza Malala Randrianambininjanahary2Nitah Harivony Randriamifidy3Domoina Harivonjy Hasina Laingonirina4Sonny Maherison5Lova Hasina Ny Ony Narindra Rajaonarison6Tovo Harimanana Rabenjanahary7Soloniaina Hélio Razafimahefa8Rado Manitrala Ramanampamonjy9Unity of Gastroenterology, University Hospital Joseph Raseta BefelatananaUnity of Gastroenterology, University Hospital Joseph Raseta BefelatananaUnity of Radiology, University Hospital Joseph Ravoahangy AndrianavalonaUnity of Gastroenterology, University Hospital Joseph Raseta BefelatananaUnity of Gastroenterology, University Hospital Joseph Raseta BefelatananaUnity of Gastroenterology, University Hospital Joseph Raseta BefelatananaUnity of Radiology, University Hospital Joseph Ravoahangy AndrianavalonaUnity of Gastroenterology, University Hospital Joseph Raseta BefelatananaUnity of Hepato-Gastroenterology, University Hospital AndrainjatoUnity of Gastroenterology, University Hospital Joseph Raseta BefelatananaAbstract Background Choledochal cysts (CDCs) are characterized by congenital cystic dilations of the intrahepatic or extrahepatic bile ducts or both. CDCs are very rarely reported in sub-Saharan Africa. This congenital anomaly of the bile ducts is rarely discovered at the stage of advanced chronic liver disease with portal hypertension. We report the first Malagasy case of a type IVA choledochal cyst discovered during an etiological work-up of cirrhosis. Case presentation A 23-year-old woman was hospitalized for jaundice and ascites. Biological and radiological investigations have led to the diagnosis of secondary biliary cirrhosis due to type IVA choledochal cyst. In view of the severity of the liver damage (Child-Pugh C score), a collegial decision (hepato-gastroenterologists and visceral surgeons) had rejected surgical intervention and opted only for the management of cirrhotic decompensation. Conclusion A type IVA choledochal cyst is a possible etiology of advanced chronic liver disease.https://doi.org/10.1186/s43162-022-00102-2Choledochal cystCirrhosisadultsMadagascarCase report |
| spellingShingle | Chantelli Iamblaudiot Razafindrazoto Andry Lalaina Rinà Rakotozafindrabe Sakaiza Malala Randrianambininjanahary Nitah Harivony Randriamifidy Domoina Harivonjy Hasina Laingonirina Sonny Maherison Lova Hasina Ny Ony Narindra Rajaonarison Tovo Harimanana Rabenjanahary Soloniaina Hélio Razafimahefa Rado Manitrala Ramanampamonjy Type IVA choledochal cyst: a rare cause of cirrhosis in adults The Egyptian Journal of Internal Medicine Choledochal cyst Cirrhosis adults Madagascar Case report |
| title | Type IVA choledochal cyst: a rare cause of cirrhosis in adults |
| title_full | Type IVA choledochal cyst: a rare cause of cirrhosis in adults |
| title_fullStr | Type IVA choledochal cyst: a rare cause of cirrhosis in adults |
| title_full_unstemmed | Type IVA choledochal cyst: a rare cause of cirrhosis in adults |
| title_short | Type IVA choledochal cyst: a rare cause of cirrhosis in adults |
| title_sort | type iva choledochal cyst a rare cause of cirrhosis in adults |
| topic | Choledochal cyst Cirrhosis adults Madagascar Case report |
| url | https://doi.org/10.1186/s43162-022-00102-2 |
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