Acute Respiratory Failure as Initial Presentation of Amyotrophic Lateral Sclerosis Onset

Amyotrophic lateral sclerosis (ALS) is a progressive, unrelenting and presently incurable neurodegenerative disorder. Respiratory muscle involvement is often a late complication of ALS. Only 1–3% of patients with ALS presenting to a tertiary care center had respiratory symptoms as their initial clin...

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Main Authors: Chien-Tsun Chou, Chun-Hao Lin, Wai-Mau Choi
Format: Article
Language:English
Published: Taiwan Society of Geriatric Emergency and Critical Medicine (TSGECM) 2008-06-01
Series:International Journal of Gerontology
Subjects:
Online Access:http://www.sciencedirect.com/science/article/pii/S1873959808700140
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author Chien-Tsun Chou
Chun-Hao Lin
Wai-Mau Choi
author_facet Chien-Tsun Chou
Chun-Hao Lin
Wai-Mau Choi
author_sort Chien-Tsun Chou
collection DOAJ
description Amyotrophic lateral sclerosis (ALS) is a progressive, unrelenting and presently incurable neurodegenerative disorder. Respiratory muscle involvement is often a late complication of ALS. Only 1–3% of patients with ALS presenting to a tertiary care center had respiratory symptoms as their initial clinical symptom. In addition, only 14% of these individuals presented acutely and required emergency intubation. We report a 75-year-old female whose initial presentation at our emergency department was dyspnea. Dyspnea worsened and progressed to acute respiratory failure. There was no definite cause of respiratory failure found initially. However, ALS was diagnosed after physical and neurologic examination and electrodiagnostic studies. Respiratory muscle weakness was her first presentation of ALS.
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spelling doaj.art-c2c47872653c4d87ba703ee5a74d90942022-12-21T23:49:56ZengTaiwan Society of Geriatric Emergency and Critical Medicine (TSGECM)International Journal of Gerontology1873-95982008-06-0122727510.1016/S1873-9598(08)70014-0Acute Respiratory Failure as Initial Presentation of Amyotrophic Lateral Sclerosis OnsetChien-Tsun Chou0Chun-Hao Lin1Wai-Mau Choi2Department of Emergency Medicine, Hsinchu Branch, TaiwanDepartment of Neurology, Mackay Memorial Hospital, Hsinchu Branch, TaiwanDepartment of Emergency Medicine, Hsinchu Branch, TaiwanAmyotrophic lateral sclerosis (ALS) is a progressive, unrelenting and presently incurable neurodegenerative disorder. Respiratory muscle involvement is often a late complication of ALS. Only 1–3% of patients with ALS presenting to a tertiary care center had respiratory symptoms as their initial clinical symptom. In addition, only 14% of these individuals presented acutely and required emergency intubation. We report a 75-year-old female whose initial presentation at our emergency department was dyspnea. Dyspnea worsened and progressed to acute respiratory failure. There was no definite cause of respiratory failure found initially. However, ALS was diagnosed after physical and neurologic examination and electrodiagnostic studies. Respiratory muscle weakness was her first presentation of ALS.http://www.sciencedirect.com/science/article/pii/S1873959808700140amyotrophic lateral sclerosisrespiratory failure
spellingShingle Chien-Tsun Chou
Chun-Hao Lin
Wai-Mau Choi
Acute Respiratory Failure as Initial Presentation of Amyotrophic Lateral Sclerosis Onset
International Journal of Gerontology
amyotrophic lateral sclerosis
respiratory failure
title Acute Respiratory Failure as Initial Presentation of Amyotrophic Lateral Sclerosis Onset
title_full Acute Respiratory Failure as Initial Presentation of Amyotrophic Lateral Sclerosis Onset
title_fullStr Acute Respiratory Failure as Initial Presentation of Amyotrophic Lateral Sclerosis Onset
title_full_unstemmed Acute Respiratory Failure as Initial Presentation of Amyotrophic Lateral Sclerosis Onset
title_short Acute Respiratory Failure as Initial Presentation of Amyotrophic Lateral Sclerosis Onset
title_sort acute respiratory failure as initial presentation of amyotrophic lateral sclerosis onset
topic amyotrophic lateral sclerosis
respiratory failure
url http://www.sciencedirect.com/science/article/pii/S1873959808700140
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