Pilosidade púbica na criança e hiperplasia congénita supra-renal não clássica.
Before the age of 8 in females and 9 in males, the presence of pubic hair can be the first sign of a gonadal or adrenal disease. In order to identify the late onset type of congenital adrenal hyperplasia in premature pubescence, we did the adrenal short stimulation test with Synacthen, on 30 childre...
Main Authors: | , , , |
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Format: | Article |
Language: | English |
Published: |
Ordem dos Médicos
1991-08-01
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Series: | Acta Médica Portuguesa |
Online Access: | https://www.actamedicaportuguesa.com/revista/index.php/amp/article/view/3357 |
Summary: | Before the age of 8 in females and 9 in males, the presence of pubic hair can be the first sign of a gonadal or adrenal disease. In order to identify the late onset type of congenital adrenal hyperplasia in premature pubescence, we did the adrenal short stimulation test with Synacthen, on 30 children. Five girls and one boy showed a 21-hydroxylase deficiency, in which the seric 17-OH Progesterone at 60 minutes is 28.8 +/- 15.2 ng/ml, being in a control group 2.30 +/- 0.8 ng/ml [p less than 0.01]. The 20% incidence we have found, justifies the testing of every premature pubescent child. |
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ISSN: | 0870-399X 1646-0758 |