First case of neurofibromatosis with posterior reversible encephalopathy syndrome showing spinal cord involvement
Posterior reversible encephalopathy syndrome (PRES) is a well-documented pathology of the brain in systemic upsets. Majority of PRES cases present with edema in the cerebrum, most commonly in the territory of posterior circulation. It has been reported to show spinal cord involvement in a rare subgr...
| Main Authors: | , , , |
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| Format: | Article |
| Language: | English |
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Thieme Medical and Scientific Publishers Pvt. Ltd.
2018-04-01
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| Series: | Indian Journal of Radiology and Imaging |
| Subjects: | |
| Online Access: | http://www.thieme-connect.de/DOI/DOI?10.4103/ijri.IJRI_320_17 |
| _version_ | 1818455531606507520 |
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| author | Pui Kwan Joyce Chan Kin Sun Tse Wing Shan Elaine Fok Wai Lun Poon |
| author_facet | Pui Kwan Joyce Chan Kin Sun Tse Wing Shan Elaine Fok Wai Lun Poon |
| author_sort | Pui Kwan Joyce Chan |
| collection | DOAJ |
| description | Posterior reversible encephalopathy syndrome (PRES) is a well-documented pathology of the brain in systemic upsets. Majority of PRES cases present with edema in the cerebrum, most commonly in the territory of posterior circulation. It has been reported to show spinal cord involvement in a rare subgroup known as PRES with spinal cord involvement (PRES-SCI), with very limited existing literature even in adult patients. Our institution recently encountered a pediatric case with neurofibromatosis type I (NF 1) showing PRES with extensive reversible spinal cord changes. This case illustrates the features of this rare entity in the pediatric group of patients, and is the first reported case in NF 1 patients. |
| first_indexed | 2024-12-14T22:12:16Z |
| format | Article |
| id | doaj.art-c30d3b474c0a495c8b371596fda3550e |
| institution | Directory Open Access Journal |
| issn | 0971-3026 1998-3808 |
| language | English |
| last_indexed | 2024-12-14T22:12:16Z |
| publishDate | 2018-04-01 |
| publisher | Thieme Medical and Scientific Publishers Pvt. Ltd. |
| record_format | Article |
| series | Indian Journal of Radiology and Imaging |
| spelling | doaj.art-c30d3b474c0a495c8b371596fda3550e2022-12-21T22:45:43ZengThieme Medical and Scientific Publishers Pvt. Ltd.Indian Journal of Radiology and Imaging0971-30261998-38082018-04-01280216116410.4103/ijri.IJRI_320_17First case of neurofibromatosis with posterior reversible encephalopathy syndrome showing spinal cord involvementPui Kwan Joyce Chan0Kin Sun Tse1Wing Shan Elaine Fok2Wai Lun Poon3Department of Radiology and Imaging, Queen Elizabeth Hospital, Kowloon, Hong Kong (SAR), People’s Republic of ChinaDepartment of Radiology and Imaging, Queen Elizabeth Hospital, Kowloon, Hong Kong (SAR), People’s Republic of ChinaDepartment of Radiology and Imaging, Queen Elizabeth Hospital, Kowloon, Hong Kong (SAR), People’s Republic of ChinaDepartment of Radiology and Imaging, Queen Elizabeth Hospital, Kowloon, Hong Kong (SAR), People’s Republic of ChinaPosterior reversible encephalopathy syndrome (PRES) is a well-documented pathology of the brain in systemic upsets. Majority of PRES cases present with edema in the cerebrum, most commonly in the territory of posterior circulation. It has been reported to show spinal cord involvement in a rare subgroup known as PRES with spinal cord involvement (PRES-SCI), with very limited existing literature even in adult patients. Our institution recently encountered a pediatric case with neurofibromatosis type I (NF 1) showing PRES with extensive reversible spinal cord changes. This case illustrates the features of this rare entity in the pediatric group of patients, and is the first reported case in NF 1 patients.http://www.thieme-connect.de/DOI/DOI?10.4103/ijri.IJRI_320_17hypertensive crisisneurofibromatosispediatric posterior reversible encephalopathy syndromeposterior reversible encephalopathy syndromespinal cord edema |
| spellingShingle | Pui Kwan Joyce Chan Kin Sun Tse Wing Shan Elaine Fok Wai Lun Poon First case of neurofibromatosis with posterior reversible encephalopathy syndrome showing spinal cord involvement Indian Journal of Radiology and Imaging hypertensive crisis neurofibromatosis pediatric posterior reversible encephalopathy syndrome posterior reversible encephalopathy syndrome spinal cord edema |
| title | First case of neurofibromatosis with posterior reversible encephalopathy syndrome showing spinal cord involvement |
| title_full | First case of neurofibromatosis with posterior reversible encephalopathy syndrome showing spinal cord involvement |
| title_fullStr | First case of neurofibromatosis with posterior reversible encephalopathy syndrome showing spinal cord involvement |
| title_full_unstemmed | First case of neurofibromatosis with posterior reversible encephalopathy syndrome showing spinal cord involvement |
| title_short | First case of neurofibromatosis with posterior reversible encephalopathy syndrome showing spinal cord involvement |
| title_sort | first case of neurofibromatosis with posterior reversible encephalopathy syndrome showing spinal cord involvement |
| topic | hypertensive crisis neurofibromatosis pediatric posterior reversible encephalopathy syndrome posterior reversible encephalopathy syndrome spinal cord edema |
| url | http://www.thieme-connect.de/DOI/DOI?10.4103/ijri.IJRI_320_17 |
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