Left Main Stem Compression by Intrapericardial Paraganglioma Associated With Succinate Dehydrogenase Mutation
Paragangliomas are rare extra-adrenal tumors originating from chromaffin cells. We discovered a large intrapericardial mass confirmed to be a primary cardiac paraganglioma encasing the left main stem coronary artery in a 38-year-old woman who presented with dyspnea and subscapular pain. Genetic pred...
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Elsevier
2024-03-01
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Series: | JACC: Case Reports |
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Online Access: | http://www.sciencedirect.com/science/article/pii/S2666084924000135 |
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author | Xue Wang, MB BChir Mohsin Gondal, MBBS Samer Alabed, MD Catherine Hill, MB ChB David Barmby, MB ChB |
author_facet | Xue Wang, MB BChir Mohsin Gondal, MBBS Samer Alabed, MD Catherine Hill, MB ChB David Barmby, MB ChB |
author_sort | Xue Wang, MB BChir |
collection | DOAJ |
description | Paragangliomas are rare extra-adrenal tumors originating from chromaffin cells. We discovered a large intrapericardial mass confirmed to be a primary cardiac paraganglioma encasing the left main stem coronary artery in a 38-year-old woman who presented with dyspnea and subscapular pain. Genetic predisposition related to succinate dehydrogenase A mutation was identified. |
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format | Article |
id | doaj.art-c3a1e78c01dd4ba8bfc6dde542963f25 |
institution | Directory Open Access Journal |
issn | 2666-0849 |
language | English |
last_indexed | 2024-03-08T06:20:43Z |
publishDate | 2024-03-01 |
publisher | Elsevier |
record_format | Article |
series | JACC: Case Reports |
spelling | doaj.art-c3a1e78c01dd4ba8bfc6dde542963f252024-02-04T04:46:34ZengElsevierJACC: Case Reports2666-08492024-03-01295102232Left Main Stem Compression by Intrapericardial Paraganglioma Associated With Succinate Dehydrogenase MutationXue Wang, MB BChir0Mohsin Gondal, MBBS1Samer Alabed, MD2Catherine Hill, MB ChB3David Barmby, MB ChB4Division of Clinical Medicine, University of Sheffield, Sheffield, United Kingdom; Address for correspondence: Dr Xue Wang, Division of Clinical Medicine, School of Medicine and Population Health, University of Sheffield, Beech Hill Road, Sheffield S10 2RX, United Kingdom.Department of Cardiology, Sheffield Teaching Hospitals National Health Service Foundation Trust, Sheffield, United KingdomDepartment of Radiology, Sheffield Teaching Hospitals National Health Service Foundation Trust, Sheffield, United KingdomDepartment of Radiology, Sheffield Teaching Hospitals National Health Service Foundation Trust, Sheffield, United KingdomDepartment of Cardiology, Sheffield Teaching Hospitals National Health Service Foundation Trust, Sheffield, United KingdomParagangliomas are rare extra-adrenal tumors originating from chromaffin cells. We discovered a large intrapericardial mass confirmed to be a primary cardiac paraganglioma encasing the left main stem coronary artery in a 38-year-old woman who presented with dyspnea and subscapular pain. Genetic predisposition related to succinate dehydrogenase A mutation was identified.http://www.sciencedirect.com/science/article/pii/S2666084924000135cardiac magnetic resonancecomputed tomographycoronary angiographycoronary artery bypassgeneticsimaging |
spellingShingle | Xue Wang, MB BChir Mohsin Gondal, MBBS Samer Alabed, MD Catherine Hill, MB ChB David Barmby, MB ChB Left Main Stem Compression by Intrapericardial Paraganglioma Associated With Succinate Dehydrogenase Mutation JACC: Case Reports cardiac magnetic resonance computed tomography coronary angiography coronary artery bypass genetics imaging |
title | Left Main Stem Compression by Intrapericardial Paraganglioma Associated With Succinate Dehydrogenase Mutation |
title_full | Left Main Stem Compression by Intrapericardial Paraganglioma Associated With Succinate Dehydrogenase Mutation |
title_fullStr | Left Main Stem Compression by Intrapericardial Paraganglioma Associated With Succinate Dehydrogenase Mutation |
title_full_unstemmed | Left Main Stem Compression by Intrapericardial Paraganglioma Associated With Succinate Dehydrogenase Mutation |
title_short | Left Main Stem Compression by Intrapericardial Paraganglioma Associated With Succinate Dehydrogenase Mutation |
title_sort | left main stem compression by intrapericardial paraganglioma associated with succinate dehydrogenase mutation |
topic | cardiac magnetic resonance computed tomography coronary angiography coronary artery bypass genetics imaging |
url | http://www.sciencedirect.com/science/article/pii/S2666084924000135 |
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