Left Main Stem Compression by Intrapericardial Paraganglioma Associated With Succinate Dehydrogenase Mutation

Paragangliomas are rare extra-adrenal tumors originating from chromaffin cells. We discovered a large intrapericardial mass confirmed to be a primary cardiac paraganglioma encasing the left main stem coronary artery in a 38-year-old woman who presented with dyspnea and subscapular pain. Genetic pred...

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Main Authors: Xue Wang, MB BChir, Mohsin Gondal, MBBS, Samer Alabed, MD, Catherine Hill, MB ChB, David Barmby, MB ChB
Format: Article
Language:English
Published: Elsevier 2024-03-01
Series:JACC: Case Reports
Subjects:
Online Access:http://www.sciencedirect.com/science/article/pii/S2666084924000135
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author Xue Wang, MB BChir
Mohsin Gondal, MBBS
Samer Alabed, MD
Catherine Hill, MB ChB
David Barmby, MB ChB
author_facet Xue Wang, MB BChir
Mohsin Gondal, MBBS
Samer Alabed, MD
Catherine Hill, MB ChB
David Barmby, MB ChB
author_sort Xue Wang, MB BChir
collection DOAJ
description Paragangliomas are rare extra-adrenal tumors originating from chromaffin cells. We discovered a large intrapericardial mass confirmed to be a primary cardiac paraganglioma encasing the left main stem coronary artery in a 38-year-old woman who presented with dyspnea and subscapular pain. Genetic predisposition related to succinate dehydrogenase A mutation was identified.
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spelling doaj.art-c3a1e78c01dd4ba8bfc6dde542963f252024-02-04T04:46:34ZengElsevierJACC: Case Reports2666-08492024-03-01295102232Left Main Stem Compression by Intrapericardial Paraganglioma Associated With Succinate Dehydrogenase MutationXue Wang, MB BChir0Mohsin Gondal, MBBS1Samer Alabed, MD2Catherine Hill, MB ChB3David Barmby, MB ChB4Division of Clinical Medicine, University of Sheffield, Sheffield, United Kingdom; Address for correspondence: Dr Xue Wang, Division of Clinical Medicine, School of Medicine and Population Health, University of Sheffield, Beech Hill Road, Sheffield S10 2RX, United Kingdom.Department of Cardiology, Sheffield Teaching Hospitals National Health Service Foundation Trust, Sheffield, United KingdomDepartment of Radiology, Sheffield Teaching Hospitals National Health Service Foundation Trust, Sheffield, United KingdomDepartment of Radiology, Sheffield Teaching Hospitals National Health Service Foundation Trust, Sheffield, United KingdomDepartment of Cardiology, Sheffield Teaching Hospitals National Health Service Foundation Trust, Sheffield, United KingdomParagangliomas are rare extra-adrenal tumors originating from chromaffin cells. We discovered a large intrapericardial mass confirmed to be a primary cardiac paraganglioma encasing the left main stem coronary artery in a 38-year-old woman who presented with dyspnea and subscapular pain. Genetic predisposition related to succinate dehydrogenase A mutation was identified.http://www.sciencedirect.com/science/article/pii/S2666084924000135cardiac magnetic resonancecomputed tomographycoronary angiographycoronary artery bypassgeneticsimaging
spellingShingle Xue Wang, MB BChir
Mohsin Gondal, MBBS
Samer Alabed, MD
Catherine Hill, MB ChB
David Barmby, MB ChB
Left Main Stem Compression by Intrapericardial Paraganglioma Associated With Succinate Dehydrogenase Mutation
JACC: Case Reports
cardiac magnetic resonance
computed tomography
coronary angiography
coronary artery bypass
genetics
imaging
title Left Main Stem Compression by Intrapericardial Paraganglioma Associated With Succinate Dehydrogenase Mutation
title_full Left Main Stem Compression by Intrapericardial Paraganglioma Associated With Succinate Dehydrogenase Mutation
title_fullStr Left Main Stem Compression by Intrapericardial Paraganglioma Associated With Succinate Dehydrogenase Mutation
title_full_unstemmed Left Main Stem Compression by Intrapericardial Paraganglioma Associated With Succinate Dehydrogenase Mutation
title_short Left Main Stem Compression by Intrapericardial Paraganglioma Associated With Succinate Dehydrogenase Mutation
title_sort left main stem compression by intrapericardial paraganglioma associated with succinate dehydrogenase mutation
topic cardiac magnetic resonance
computed tomography
coronary angiography
coronary artery bypass
genetics
imaging
url http://www.sciencedirect.com/science/article/pii/S2666084924000135
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