Characterization of the PF-ILD phenotype in patients with advanced pulmonary sarcoidosis

Abstract Background Advanced pulmonary sarcoidosis causes significant morbidity and can lead to death. Large trials demonstrated efficacy of antifibrotics in patients with progressive fibrosing interstitial lung diseases (PF-ILD), including a few with sarcoidosis. To date, little is known about this...

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Main Authors: M. C. Schimmelpennink, D. B. Meek, A. D. M. Vorselaars, L. C. M. Langezaal, C. H. M. van Moorsel, J. J. van der Vis, M. Veltkamp, J. C. Grutters
Format: Article
Language:English
Published: BMC 2022-06-01
Series:Respiratory Research
Subjects:
Online Access:https://doi.org/10.1186/s12931-022-02094-7