Herlyn–Werner–Wünderlich syndrome: An unusual case with presentation of menorrhagia
Objective: Herlyn–Werner–Wünderlich (HWW) syndrome is a rare condition in which patients present with a palpable pelvic mass and pain caused by an obstructed hemivagina. Here we present a case of HWW syndrome characterized by prolonged menstrual bleeding. Case report: A 19-year-old nonsexually activ...
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| Format: | Article |
| Language: | English |
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Elsevier
2020-11-01
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| Series: | Taiwanese Journal of Obstetrics & Gynecology |
| Subjects: | |
| Online Access: | http://www.sciencedirect.com/science/article/pii/S1028455920302370 |
| _version_ | 1818459489504854016 |
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| author | Hsin-I Liang Shao-Chi Fu Chih-Hsiang Yin Cheng-Chang Chang |
| author_facet | Hsin-I Liang Shao-Chi Fu Chih-Hsiang Yin Cheng-Chang Chang |
| author_sort | Hsin-I Liang |
| collection | DOAJ |
| description | Objective: Herlyn–Werner–Wünderlich (HWW) syndrome is a rare condition in which patients present with a palpable pelvic mass and pain caused by an obstructed hemivagina. Here we present a case of HWW syndrome characterized by prolonged menstrual bleeding. Case report: A 19-year-old nonsexually active unmarried women experienced irregular menstrual cycles and menorrhagia. The duration of menstrual bleeding was 10–14 days. She also suffered from mild dysmenorrhea since menarche at the age of 13. Transabdominal sonography revealed a double uterus and a heterogeneous myoma-mimicking mass over the left cervical region. The left kidney was absent. Magnetic resonance imaging revealed a double uterus, a double vagina with an unperforated left hemivagina, and ipsilateral renal agenesis. The patient underwent cervicovaginal orifice reconstruction surgery. Conclusion: Left hematocolpos compression, a partially obstructed right vaginal channel, and an orifice with local venous drainage abnormalities resulted in prolonged menstrual bleeding. In HWW syndrome, the occurrence of a pelvic mass and pain is common; however, prolonged menstrual bleeding is rare. |
| first_indexed | 2024-12-14T23:15:10Z |
| format | Article |
| id | doaj.art-c4ae66cdb66a4ed4b045c28704d82bc0 |
| institution | Directory Open Access Journal |
| issn | 1028-4559 |
| language | English |
| last_indexed | 2024-12-14T23:15:10Z |
| publishDate | 2020-11-01 |
| publisher | Elsevier |
| record_format | Article |
| series | Taiwanese Journal of Obstetrics & Gynecology |
| spelling | doaj.art-c4ae66cdb66a4ed4b045c28704d82bc02022-12-21T22:44:06ZengElsevierTaiwanese Journal of Obstetrics & Gynecology1028-45592020-11-01596948951Herlyn–Werner–Wünderlich syndrome: An unusual case with presentation of menorrhagiaHsin-I Liang0Shao-Chi Fu1Chih-Hsiang Yin2Cheng-Chang Chang3Department of Obstetrics and Gynecology, Taichung Armed Forces General Hospital, Taichung, Taiwan, ROC; Department of Obstetrics and Gynecology, Tri-Service General Hospital, National Defense Medical Center, Taipei, Taiwan, ROCDepartment of Obstetrics and Gynecology, Taichung Armed Forces General Hospital, Taichung, Taiwan, ROC; Department of Obstetrics and Gynecology, Tri-Service General Hospital, National Defense Medical Center, Taipei, Taiwan, ROCDepartment of Obstetrics and Gynecology, Tri-Service General Hospital, National Defense Medical Center, Taipei, Taiwan, ROCDepartment of Obstetrics and Gynecology, Tri-Service General Hospital, National Defense Medical Center, Taipei, Taiwan, ROC; Corresponding author. Department of Obstetrics and Gynecology, Tri-Service General Hospital, National Defense Medical Center, No. 325, Sec. 2, Cheng-gong Rd., Neihu District, Taipei City, 114, Taiwan, ROC. Fax: +886 2 87927207.Objective: Herlyn–Werner–Wünderlich (HWW) syndrome is a rare condition in which patients present with a palpable pelvic mass and pain caused by an obstructed hemivagina. Here we present a case of HWW syndrome characterized by prolonged menstrual bleeding. Case report: A 19-year-old nonsexually active unmarried women experienced irregular menstrual cycles and menorrhagia. The duration of menstrual bleeding was 10–14 days. She also suffered from mild dysmenorrhea since menarche at the age of 13. Transabdominal sonography revealed a double uterus and a heterogeneous myoma-mimicking mass over the left cervical region. The left kidney was absent. Magnetic resonance imaging revealed a double uterus, a double vagina with an unperforated left hemivagina, and ipsilateral renal agenesis. The patient underwent cervicovaginal orifice reconstruction surgery. Conclusion: Left hematocolpos compression, a partially obstructed right vaginal channel, and an orifice with local venous drainage abnormalities resulted in prolonged menstrual bleeding. In HWW syndrome, the occurrence of a pelvic mass and pain is common; however, prolonged menstrual bleeding is rare.http://www.sciencedirect.com/science/article/pii/S1028455920302370Herlyn–Werner–Wünderlich syndromeDouble uterusHematocolposDysmenorrheaPelvic mass |
| spellingShingle | Hsin-I Liang Shao-Chi Fu Chih-Hsiang Yin Cheng-Chang Chang Herlyn–Werner–Wünderlich syndrome: An unusual case with presentation of menorrhagia Taiwanese Journal of Obstetrics & Gynecology Herlyn–Werner–Wünderlich syndrome Double uterus Hematocolpos Dysmenorrhea Pelvic mass |
| title | Herlyn–Werner–Wünderlich syndrome: An unusual case with presentation of menorrhagia |
| title_full | Herlyn–Werner–Wünderlich syndrome: An unusual case with presentation of menorrhagia |
| title_fullStr | Herlyn–Werner–Wünderlich syndrome: An unusual case with presentation of menorrhagia |
| title_full_unstemmed | Herlyn–Werner–Wünderlich syndrome: An unusual case with presentation of menorrhagia |
| title_short | Herlyn–Werner–Wünderlich syndrome: An unusual case with presentation of menorrhagia |
| title_sort | herlyn werner wunderlich syndrome an unusual case with presentation of menorrhagia |
| topic | Herlyn–Werner–Wünderlich syndrome Double uterus Hematocolpos Dysmenorrhea Pelvic mass |
| url | http://www.sciencedirect.com/science/article/pii/S1028455920302370 |
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