Paraneoplastic progressive encephalomyelitis with rigidity and myoclonus associated with monoclonal B-cell lymphocytosis in the setting of longstanding methotrexate use: case report
Progressive encephalomyelitis with rigidity and myoclonus (PERM) is a rare but debilitating disease within the stiff person syndrome (SPS) spectrum characterised by muscle rigidity, spasms, myoclonus, dysautonomia, and brainstem dysfunction. The exact pathogenetic mechanism is unclear, although ther...
Główni autorzy: | , , , , , , , |
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Format: | Artykuł |
Język: | English |
Wydane: |
Frontiers Media S.A.
2024-10-01
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Seria: | Frontiers in Immunology |
Hasła przedmiotowe: | |
Dostęp online: | https://www.frontiersin.org/articles/10.3389/fimmu.2024.1436733/full |