Paraneoplastic progressive encephalomyelitis with rigidity and myoclonus associated with monoclonal B-cell lymphocytosis in the setting of longstanding methotrexate use: case report

Progressive encephalomyelitis with rigidity and myoclonus (PERM) is a rare but debilitating disease within the stiff person syndrome (SPS) spectrum characterised by muscle rigidity, spasms, myoclonus, dysautonomia, and brainstem dysfunction. The exact pathogenetic mechanism is unclear, although ther...

Szczegółowa specyfikacja

Opis bibliograficzny
Główni autorzy: Fangzhi (Frank) Jia, Mohammad Ruhul Amin, Gi Tae Kwon, Amir Mousapasandi, Pei Dai, Jed Kitson, Adrian Selim, Jerome Ip
Format: Artykuł
Język:English
Wydane: Frontiers Media S.A. 2024-10-01
Seria:Frontiers in Immunology
Hasła przedmiotowe:
Dostęp online:https://www.frontiersin.org/articles/10.3389/fimmu.2024.1436733/full