Extra-Hepatic Biliary Atresia in Association with Polysplenia and Intestinal Malrotation
The syndromic form of biliary atresia accounts for 10-25% and is associated with a poor prognosis due to associated anomalies. We report a case of extrahepatic biliary atresia and polysplenia syndrome with jaundice since 19th day of life and who had undergone surgical correction of malrotation in th...
| Main Authors: | , , , |
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| Format: | Article |
| Language: | English |
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EL-Med-Pub
2013-09-01
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| Series: | Journal of Neonatal Surgery |
| Subjects: | |
| Online Access: | https://jneonatalsurg.com/ojs/index.php/jns/article/view/56 |
| _version_ | 1819058600728854528 |
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| author | Jaishri Ramji Rakesh S Joshi Mitesh Bachani Dungarsingh Rathore |
| author_facet | Jaishri Ramji Rakesh S Joshi Mitesh Bachani Dungarsingh Rathore |
| author_sort | Jaishri Ramji |
| collection | DOAJ |
| description | The syndromic form of biliary atresia accounts for 10-25% and is associated with a poor prognosis due to associated anomalies. We report a case of extrahepatic biliary atresia and polysplenia syndrome with jaundice since 19th day of life and who had undergone surgical correction of malrotation in the neonatal period. Inspite of successful Kasai’s portoenterostomy at 52nd day of life, the child succumbed to post-operative sepsis. |
| first_indexed | 2024-12-21T13:57:47Z |
| format | Article |
| id | doaj.art-c57d9e9eff664dcea9feed70c98353c2 |
| institution | Directory Open Access Journal |
| issn | 2226-0439 |
| language | English |
| last_indexed | 2024-12-21T13:57:47Z |
| publishDate | 2013-09-01 |
| publisher | EL-Med-Pub |
| record_format | Article |
| series | Journal of Neonatal Surgery |
| spelling | doaj.art-c57d9e9eff664dcea9feed70c98353c22022-12-21T19:01:29ZengEL-Med-PubJournal of Neonatal Surgery2226-04392013-09-012410.21699/jns.v2i4.85Extra-Hepatic Biliary Atresia in Association with Polysplenia and Intestinal MalrotationJaishri Ramji0Rakesh S JoshiMitesh BachaniDungarsingh RathoreB.J.Medical College, Gujarat University, Ahmedabad, GujaratThe syndromic form of biliary atresia accounts for 10-25% and is associated with a poor prognosis due to associated anomalies. We report a case of extrahepatic biliary atresia and polysplenia syndrome with jaundice since 19th day of life and who had undergone surgical correction of malrotation in the neonatal period. Inspite of successful Kasai’s portoenterostomy at 52nd day of life, the child succumbed to post-operative sepsis.https://jneonatalsurg.com/ojs/index.php/jns/article/view/56Extra-hepatic biliary atresiaPolyspleniaIntestinal malrotation |
| spellingShingle | Jaishri Ramji Rakesh S Joshi Mitesh Bachani Dungarsingh Rathore Extra-Hepatic Biliary Atresia in Association with Polysplenia and Intestinal Malrotation Journal of Neonatal Surgery Extra-hepatic biliary atresia Polysplenia Intestinal malrotation |
| title | Extra-Hepatic Biliary Atresia in Association with Polysplenia and Intestinal Malrotation |
| title_full | Extra-Hepatic Biliary Atresia in Association with Polysplenia and Intestinal Malrotation |
| title_fullStr | Extra-Hepatic Biliary Atresia in Association with Polysplenia and Intestinal Malrotation |
| title_full_unstemmed | Extra-Hepatic Biliary Atresia in Association with Polysplenia and Intestinal Malrotation |
| title_short | Extra-Hepatic Biliary Atresia in Association with Polysplenia and Intestinal Malrotation |
| title_sort | extra hepatic biliary atresia in association with polysplenia and intestinal malrotation |
| topic | Extra-hepatic biliary atresia Polysplenia Intestinal malrotation |
| url | https://jneonatalsurg.com/ojs/index.php/jns/article/view/56 |
| work_keys_str_mv | AT jaishriramji extrahepaticbiliaryatresiainassociationwithpolyspleniaandintestinalmalrotation AT rakeshsjoshi extrahepaticbiliaryatresiainassociationwithpolyspleniaandintestinalmalrotation AT miteshbachani extrahepaticbiliaryatresiainassociationwithpolyspleniaandintestinalmalrotation AT dungarsinghrathore extrahepaticbiliaryatresiainassociationwithpolyspleniaandintestinalmalrotation |