Epithelioid hemangioendothelioma of the forearm with radius involvement. Case report
<p>Abstract</p> <p>Epithelioid hemangioendothelioma (EHE) is a rare, well-differentiated endothelial tumor with intermediate malignancy which develops more frequently from the peripheral veins, generally in the lower limb. Bone EHE comprises less than 1% of the bone neoplasms. We p...
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Format: | Article |
Language: | English |
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BMC
2011-12-01
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Series: | Diagnostic Pathology |
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Online Access: | http://www.diagnosticpathology.org/content/6/1/120 |
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author | Gherman Claudia D Fodor Daniela |
author_facet | Gherman Claudia D Fodor Daniela |
author_sort | Gherman Claudia D |
collection | DOAJ |
description | <p>Abstract</p> <p>Epithelioid hemangioendothelioma (EHE) is a rare, well-differentiated endothelial tumor with intermediate malignancy which develops more frequently from the peripheral veins, generally in the lower limb. Bone EHE comprises less than 1% of the bone neoplasms. We present the case of a young man, 24-year-old, with EHE of the forearm with secondary involvement of the distal radius. The location and the extension of the tumor allowed a wide excision, without the reconstruction of radius, followed by adjuvant radiotherapy, with a subsequent favorable evolution. Based on the clinical, radiographic, and pathological features of the EHE review, we concluded that it is difficult to adopt a standardized therapeutic approach due to the extremely low incidence of the bone involvement in EHE and the variable tendencies towards malignancy of this tumor. To our knowledge this is the third case of EHE with the involvement of the radius.</p> |
first_indexed | 2024-04-12T14:52:00Z |
format | Article |
id | doaj.art-c5bd2081e1ba468795ccdd434b3897a1 |
institution | Directory Open Access Journal |
issn | 1746-1596 |
language | English |
last_indexed | 2024-04-12T14:52:00Z |
publishDate | 2011-12-01 |
publisher | BMC |
record_format | Article |
series | Diagnostic Pathology |
spelling | doaj.art-c5bd2081e1ba468795ccdd434b3897a12022-12-22T03:28:24ZengBMCDiagnostic Pathology1746-15962011-12-016112010.1186/1746-1596-6-120Epithelioid hemangioendothelioma of the forearm with radius involvement. Case reportGherman Claudia DFodor Daniela<p>Abstract</p> <p>Epithelioid hemangioendothelioma (EHE) is a rare, well-differentiated endothelial tumor with intermediate malignancy which develops more frequently from the peripheral veins, generally in the lower limb. Bone EHE comprises less than 1% of the bone neoplasms. We present the case of a young man, 24-year-old, with EHE of the forearm with secondary involvement of the distal radius. The location and the extension of the tumor allowed a wide excision, without the reconstruction of radius, followed by adjuvant radiotherapy, with a subsequent favorable evolution. Based on the clinical, radiographic, and pathological features of the EHE review, we concluded that it is difficult to adopt a standardized therapeutic approach due to the extremely low incidence of the bone involvement in EHE and the variable tendencies towards malignancy of this tumor. To our knowledge this is the third case of EHE with the involvement of the radius.</p>http://www.diagnosticpathology.org/content/6/1/120vascular tumorintermediate-malignant tumorsecondary bone involvement |
spellingShingle | Gherman Claudia D Fodor Daniela Epithelioid hemangioendothelioma of the forearm with radius involvement. Case report Diagnostic Pathology vascular tumor intermediate-malignant tumor secondary bone involvement |
title | Epithelioid hemangioendothelioma of the forearm with radius involvement. Case report |
title_full | Epithelioid hemangioendothelioma of the forearm with radius involvement. Case report |
title_fullStr | Epithelioid hemangioendothelioma of the forearm with radius involvement. Case report |
title_full_unstemmed | Epithelioid hemangioendothelioma of the forearm with radius involvement. Case report |
title_short | Epithelioid hemangioendothelioma of the forearm with radius involvement. Case report |
title_sort | epithelioid hemangioendothelioma of the forearm with radius involvement case report |
topic | vascular tumor intermediate-malignant tumor secondary bone involvement |
url | http://www.diagnosticpathology.org/content/6/1/120 |
work_keys_str_mv | AT ghermanclaudiad epithelioidhemangioendotheliomaoftheforearmwithradiusinvolvementcasereport AT fodordaniela epithelioidhemangioendotheliomaoftheforearmwithradiusinvolvementcasereport |