Polineuropatia amiloidótica familar (PAF)--tipo português--evolução clínica e neurofisiológica.
Sixteen (16) patients with Familial Amyloidotic Polyneuropathy-Portuguese Type (FAP) were evaluated longitudinally, using the EMG and Clinical protocols with the aim of establishing the clinical and neurophysiological evolution rate of FAP. We conclude that spontaneous evolution of FAP patients show...
| Main Authors: | , , , |
|---|---|
| Format: | Article |
| Language: | English |
| Published: |
Ordem dos Médicos
1993-01-01
|
| Series: | Acta Médica Portuguesa |
| Online Access: | https://www.actamedicaportuguesa.com/revista/index.php/amp/article/view/3051 |
| _version_ | 1797996935339048960 |
|---|---|
| author | I Conceição M Carvalho M Alves M L Luís |
| author_facet | I Conceição M Carvalho M Alves M L Luís |
| author_sort | I Conceição |
| collection | DOAJ |
| description | Sixteen (16) patients with Familial Amyloidotic Polyneuropathy-Portuguese Type (FAP) were evaluated longitudinally, using the EMG and Clinical protocols with the aim of establishing the clinical and neurophysiological evolution rate of FAP. We conclude that spontaneous evolution of FAP patients shows a linear progression. Clinical and neurophysiological evolution times are parallel, with the EMG scores being higher than Clinical ones. We propose that Clinical and EMG scores should be used in the evaluation of future therapeutic trials, namely immunodepuration and liver transplantation. |
| first_indexed | 2024-04-11T10:25:17Z |
| format | Article |
| id | doaj.art-c5cfe41bc5e14bd9a8aa0a0e4f7ed32d |
| institution | Directory Open Access Journal |
| issn | 0870-399X 1646-0758 |
| language | English |
| last_indexed | 2024-04-11T10:25:17Z |
| publishDate | 1993-01-01 |
| publisher | Ordem dos Médicos |
| record_format | Article |
| series | Acta Médica Portuguesa |
| spelling | doaj.art-c5cfe41bc5e14bd9a8aa0a0e4f7ed32d2022-12-22T04:29:38ZengOrdem dos MédicosActa Médica Portuguesa0870-399X1646-07581993-01-016110.20344/amp.3051Polineuropatia amiloidótica familar (PAF)--tipo português--evolução clínica e neurofisiológica.I Conceição0M CarvalhoM AlvesM L LuísServiço de Neurologia, Centro de Estudos Egas Moniz, Hospital de Santa Maria, Lisboa.Sixteen (16) patients with Familial Amyloidotic Polyneuropathy-Portuguese Type (FAP) were evaluated longitudinally, using the EMG and Clinical protocols with the aim of establishing the clinical and neurophysiological evolution rate of FAP. We conclude that spontaneous evolution of FAP patients shows a linear progression. Clinical and neurophysiological evolution times are parallel, with the EMG scores being higher than Clinical ones. We propose that Clinical and EMG scores should be used in the evaluation of future therapeutic trials, namely immunodepuration and liver transplantation.https://www.actamedicaportuguesa.com/revista/index.php/amp/article/view/3051 |
| spellingShingle | I Conceição M Carvalho M Alves M L Luís Polineuropatia amiloidótica familar (PAF)--tipo português--evolução clínica e neurofisiológica. Acta Médica Portuguesa |
| title | Polineuropatia amiloidótica familar (PAF)--tipo português--evolução clínica e neurofisiológica. |
| title_full | Polineuropatia amiloidótica familar (PAF)--tipo português--evolução clínica e neurofisiológica. |
| title_fullStr | Polineuropatia amiloidótica familar (PAF)--tipo português--evolução clínica e neurofisiológica. |
| title_full_unstemmed | Polineuropatia amiloidótica familar (PAF)--tipo português--evolução clínica e neurofisiológica. |
| title_short | Polineuropatia amiloidótica familar (PAF)--tipo português--evolução clínica e neurofisiológica. |
| title_sort | polineuropatia amiloidotica familar paf tipo portugues evolucao clinica e neurofisiologica |
| url | https://www.actamedicaportuguesa.com/revista/index.php/amp/article/view/3051 |
| work_keys_str_mv | AT iconceicao polineuropatiaamiloidoticafamilarpaftipoportuguesevolucaoclinicaeneurofisiologica AT mcarvalho polineuropatiaamiloidoticafamilarpaftipoportuguesevolucaoclinicaeneurofisiologica AT malves polineuropatiaamiloidoticafamilarpaftipoportuguesevolucaoclinicaeneurofisiologica AT mlluis polineuropatiaamiloidoticafamilarpaftipoportuguesevolucaoclinicaeneurofisiologica |