Anesthetic management of a 12-year-old child with Kagami-Ogata syndrome for pectus excavatum: a case report
Abstract Background Kagami-Ogata syndrome (KOS) is due to abnormal gene expression in the 14q32.2 imprinted region. Laryngomalacia and bell-shaped thorax of children with KOS can affect airway management of general anesthesia. Case presentation A 12-year-old girl with KOS had a mechanical ventilatio...
| Main Authors: | , , , |
|---|---|
| Format: | Article |
| Language: | English |
| Published: |
SpringerOpen
2020-11-01
|
| Series: | JA Clinical Reports |
| Subjects: | |
| Online Access: | http://link.springer.com/article/10.1186/s40981-020-00397-6 |
| _version_ | 1818968682868506624 |
|---|---|
| author | Hisako Nishimoto Masahiro Yagihara Aki Uemura Yoshiki Nakajima |
| author_facet | Hisako Nishimoto Masahiro Yagihara Aki Uemura Yoshiki Nakajima |
| author_sort | Hisako Nishimoto |
| collection | DOAJ |
| description | Abstract Background Kagami-Ogata syndrome (KOS) is due to abnormal gene expression in the 14q32.2 imprinted region. Laryngomalacia and bell-shaped thorax of children with KOS can affect airway management of general anesthesia. Case presentation A 12-year-old girl with KOS had a mechanical ventilation history and underwent pectus excavatum repair for cosmetic reasons. Although she had undergone invasive thoracic surgery under general and epidural anesthesia, her respiratory rate and tidal volume were stable with adequate pain control mainly through epidural analgesia at the end of the surgery. We examined her larynx by a bronchoscope. Then, we successfully extubated her after confirming the normal movement of her larynx. Conclusions When patients with KOS undergo pectus excavatum repair, anesthesiologists should prevent postoperative respiratory failure by providing adequate postoperative analgesia. Evaluation of airway patency and respiratory pattern before extubation is critical. |
| first_indexed | 2024-12-20T14:08:35Z |
| format | Article |
| id | doaj.art-c66d2e0b23534fc1829140d47fef4966 |
| institution | Directory Open Access Journal |
| issn | 2363-9024 |
| language | English |
| last_indexed | 2024-12-20T14:08:35Z |
| publishDate | 2020-11-01 |
| publisher | SpringerOpen |
| record_format | Article |
| series | JA Clinical Reports |
| spelling | doaj.art-c66d2e0b23534fc1829140d47fef49662022-12-21T19:38:12ZengSpringerOpenJA Clinical Reports2363-90242020-11-01611410.1186/s40981-020-00397-6Anesthetic management of a 12-year-old child with Kagami-Ogata syndrome for pectus excavatum: a case reportHisako Nishimoto0Masahiro Yagihara1Aki Uemura2Yoshiki Nakajima3Department of Anesthesiology and Intensive Care, Hamamatsu University HospitalDepartment of Anesthesiology and Intensive Care, Hamamatsu University HospitalDepartment of Anesthesiology, Anshin HospitalDepartment of Anesthesiology and Intensive Care, Hamamatsu University HospitalAbstract Background Kagami-Ogata syndrome (KOS) is due to abnormal gene expression in the 14q32.2 imprinted region. Laryngomalacia and bell-shaped thorax of children with KOS can affect airway management of general anesthesia. Case presentation A 12-year-old girl with KOS had a mechanical ventilation history and underwent pectus excavatum repair for cosmetic reasons. Although she had undergone invasive thoracic surgery under general and epidural anesthesia, her respiratory rate and tidal volume were stable with adequate pain control mainly through epidural analgesia at the end of the surgery. We examined her larynx by a bronchoscope. Then, we successfully extubated her after confirming the normal movement of her larynx. Conclusions When patients with KOS undergo pectus excavatum repair, anesthesiologists should prevent postoperative respiratory failure by providing adequate postoperative analgesia. Evaluation of airway patency and respiratory pattern before extubation is critical.http://link.springer.com/article/10.1186/s40981-020-00397-6Kagami-Ogata syndromePectus excavatum repairAnesthetic managementPostoperative respiratory failure |
| spellingShingle | Hisako Nishimoto Masahiro Yagihara Aki Uemura Yoshiki Nakajima Anesthetic management of a 12-year-old child with Kagami-Ogata syndrome for pectus excavatum: a case report JA Clinical Reports Kagami-Ogata syndrome Pectus excavatum repair Anesthetic management Postoperative respiratory failure |
| title | Anesthetic management of a 12-year-old child with Kagami-Ogata syndrome for pectus excavatum: a case report |
| title_full | Anesthetic management of a 12-year-old child with Kagami-Ogata syndrome for pectus excavatum: a case report |
| title_fullStr | Anesthetic management of a 12-year-old child with Kagami-Ogata syndrome for pectus excavatum: a case report |
| title_full_unstemmed | Anesthetic management of a 12-year-old child with Kagami-Ogata syndrome for pectus excavatum: a case report |
| title_short | Anesthetic management of a 12-year-old child with Kagami-Ogata syndrome for pectus excavatum: a case report |
| title_sort | anesthetic management of a 12 year old child with kagami ogata syndrome for pectus excavatum a case report |
| topic | Kagami-Ogata syndrome Pectus excavatum repair Anesthetic management Postoperative respiratory failure |
| url | http://link.springer.com/article/10.1186/s40981-020-00397-6 |
| work_keys_str_mv | AT hisakonishimoto anestheticmanagementofa12yearoldchildwithkagamiogatasyndromeforpectusexcavatumacasereport AT masahiroyagihara anestheticmanagementofa12yearoldchildwithkagamiogatasyndromeforpectusexcavatumacasereport AT akiuemura anestheticmanagementofa12yearoldchildwithkagamiogatasyndromeforpectusexcavatumacasereport AT yoshikinakajima anestheticmanagementofa12yearoldchildwithkagamiogatasyndromeforpectusexcavatumacasereport |