CLINICAL, LABORATORIAL AND EVOLUTIONARY ASPECTS OF PEDIATRIC PATIENTS WITH LIVER DISEASE DUE TO ALPHA 1-ANTITRYPSIN DEFICIENCY
ABSTRACT Background: Alpha 1-antitrypsin deficiency (AATD) is a hereditary codominant autosomal disease. This liver disease ranges from asymptomatic cases to terminal illness, which makes early recognition and diagnosis challenging. It is the main cause of pediatric liver transplantation after bili...
Main Authors: | Mariana Pena COSTA, Alexandre Rodrigues FERREIRA, Adriana Teixeira RODRIGUES, Eleonora Druve Tavares FAGUNDES, Thais Costa Nascentes QUEIROZ |
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Format: | Article |
Language: | English |
Published: |
Instituto Brasileiro de Estudos e Pesquisas de Gastroenterologia (IBEPEGE)
2023-11-01
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Series: | Arquivos de Gastroenterologia |
Subjects: | |
Online Access: | http://www.scielo.br/scielo.php?script=sci_arttext&pid=S0004-28032023000400438&lng=en&tlng=en |
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