Pulmonary capillary hemangiomatosis-predominant vasculopathy in a patient with rheumatoid arthritis-associated interstitial lung disease: An autopsy report

Pulmonary capillary hemangiomatosis-predominant vasculopathy in a patient with rheumatoid arthritis-associated interstitial lung disease: An autopsy report

Pulmonary capillary hemangiomatosis (PCH) is a rare cause of pulmonary hypertension (PH) associated with poor prognosis. Clinically, it is characterized by severe hypoxemia, centrilobular ground-glass opacities on computed tomography, and pulmonary congestion triggered by pulmonary vasodilating ther...

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Bibliographic Details
Main Authors:	Junichi Nakamura, Ichizo Tsujino, Gaku Yamamoto, Toshitaka Nakaya, Kei Takahashi, Hirokazu Kimura, Takahiro Sato, Taku Watanabe, Shimpei Nakagawa, Noriyuki Otsuka, Hiroshi Ohira, Satoshi Konno
Format:	Article
Language:	English
Published:	Elsevier 2020-01-01
Series:	Respiratory Medicine Case Reports
Subjects:	Computed tomography diffusion capacity of the lung for carbon monoxide Pulmonary capillary hemangiomatosis Pulmonary hypertension Pulmonary veno-occlusive disease
Online Access:	http://www.sciencedirect.com/science/article/pii/S2213007120304299

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