Case Report: Integrated echocardiographic assessment guided Liwen procedure for treating obstructive hypertrophic cardiomyopathy with ventricular aneurysm
Hypertrophic cardiomyopathy (HCM) is a genetic myocardial disease, with an estimated incidence of 0.2%–6%, and is the main cause of sudden cardiac death (SCD) in young athletes. Left ventricular apical aneurysm (LVAA) is a rare subtype of HCM, accounting for about 5% of HCM patients, and has a highe...
| Main Authors: | , , , , , |
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| Format: | Article |
| Language: | English |
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Frontiers Media S.A.
2023-11-01
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| Series: | Frontiers in Cardiovascular Medicine |
| Subjects: | |
| Online Access: | https://www.frontiersin.org/articles/10.3389/fcvm.2023.1278457/full |
| _version_ | 1797643289067782144 |
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| author | Rui Zhang Fan Zhao Jing Wang Yahong Qin Tingting Wang Ai-Ai Chu |
| author_facet | Rui Zhang Fan Zhao Jing Wang Yahong Qin Tingting Wang Ai-Ai Chu |
| author_sort | Rui Zhang |
| collection | DOAJ |
| description | Hypertrophic cardiomyopathy (HCM) is a genetic myocardial disease, with an estimated incidence of 0.2%–6%, and is the main cause of sudden cardiac death (SCD) in young athletes. Left ventricular apical aneurysm (LVAA) is a rare subtype of HCM, accounting for about 5% of HCM patients, and has a higher incidence of cardiovascular adverse events. In cases of hypertrophic obstructive cardiomyopathy with LVAA (HOCM-LVAA) that do not respond adequately to optimized medical therapy, the echocardiography-guided percutaneous intra-myocardial septal radiofrequency ablation (PIMSRA, Liwen procedure) emerges as a promising and effective novel therapeutic approach. In this case report, we present for the first time a comprehensive application of echocardiographic techniques, including TTE, 2-D STE, and contrast enhancement, in the diagnosis, treatment, surgical guidance, and assessment of therapeutic outcomes in a case of HOCM-LVAA. |
| first_indexed | 2024-03-11T14:12:34Z |
| format | Article |
| id | doaj.art-ca7c6425c47e4c9ea580f2b3614a0ba5 |
| institution | Directory Open Access Journal |
| issn | 2297-055X |
| language | English |
| last_indexed | 2024-03-11T14:12:34Z |
| publishDate | 2023-11-01 |
| publisher | Frontiers Media S.A. |
| record_format | Article |
| series | Frontiers in Cardiovascular Medicine |
| spelling | doaj.art-ca7c6425c47e4c9ea580f2b3614a0ba52023-11-01T17:33:13ZengFrontiers Media S.A.Frontiers in Cardiovascular Medicine2297-055X2023-11-011010.3389/fcvm.2023.12784571278457Case Report: Integrated echocardiographic assessment guided Liwen procedure for treating obstructive hypertrophic cardiomyopathy with ventricular aneurysmRui ZhangFan ZhaoJing WangYahong QinTingting WangAi-Ai ChuHypertrophic cardiomyopathy (HCM) is a genetic myocardial disease, with an estimated incidence of 0.2%–6%, and is the main cause of sudden cardiac death (SCD) in young athletes. Left ventricular apical aneurysm (LVAA) is a rare subtype of HCM, accounting for about 5% of HCM patients, and has a higher incidence of cardiovascular adverse events. In cases of hypertrophic obstructive cardiomyopathy with LVAA (HOCM-LVAA) that do not respond adequately to optimized medical therapy, the echocardiography-guided percutaneous intra-myocardial septal radiofrequency ablation (PIMSRA, Liwen procedure) emerges as a promising and effective novel therapeutic approach. In this case report, we present for the first time a comprehensive application of echocardiographic techniques, including TTE, 2-D STE, and contrast enhancement, in the diagnosis, treatment, surgical guidance, and assessment of therapeutic outcomes in a case of HOCM-LVAA.https://www.frontiersin.org/articles/10.3389/fcvm.2023.1278457/fullhypertrophic obstructive cardiomyopathyhypertrophic cardiomyopathytransthoracic echocardiographycontrast-enhanced echocardiographyspeckle tracking echocardiography |
| spellingShingle | Rui Zhang Fan Zhao Jing Wang Yahong Qin Tingting Wang Ai-Ai Chu Case Report: Integrated echocardiographic assessment guided Liwen procedure for treating obstructive hypertrophic cardiomyopathy with ventricular aneurysm Frontiers in Cardiovascular Medicine hypertrophic obstructive cardiomyopathy hypertrophic cardiomyopathy transthoracic echocardiography contrast-enhanced echocardiography speckle tracking echocardiography |
| title | Case Report: Integrated echocardiographic assessment guided Liwen procedure for treating obstructive hypertrophic cardiomyopathy with ventricular aneurysm |
| title_full | Case Report: Integrated echocardiographic assessment guided Liwen procedure for treating obstructive hypertrophic cardiomyopathy with ventricular aneurysm |
| title_fullStr | Case Report: Integrated echocardiographic assessment guided Liwen procedure for treating obstructive hypertrophic cardiomyopathy with ventricular aneurysm |
| title_full_unstemmed | Case Report: Integrated echocardiographic assessment guided Liwen procedure for treating obstructive hypertrophic cardiomyopathy with ventricular aneurysm |
| title_short | Case Report: Integrated echocardiographic assessment guided Liwen procedure for treating obstructive hypertrophic cardiomyopathy with ventricular aneurysm |
| title_sort | case report integrated echocardiographic assessment guided liwen procedure for treating obstructive hypertrophic cardiomyopathy with ventricular aneurysm |
| topic | hypertrophic obstructive cardiomyopathy hypertrophic cardiomyopathy transthoracic echocardiography contrast-enhanced echocardiography speckle tracking echocardiography |
| url | https://www.frontiersin.org/articles/10.3389/fcvm.2023.1278457/full |
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