Hirschsprung’s Disease in a Twin Neonate With One Suffering From Multple Skip Segments
This is a new case, affecting a twin that both with Hirschsprung’s disease, one was suffering from long-segment Hirschsprung’s disease with skip segmented. Our surgeon suspected the absence of abnormal vessel tortuosity in the transitional zone; thus, the appendix was sent for permanent pathology. T...
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| Format: | Article |
| Language: | English |
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Tehran University of Medical Sciences
2021-10-01
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| Series: | Case Reports in Clinical Practice |
| Subjects: | |
| Online Access: | https://crcp.tums.ac.ir/index.php/crcp/article/view/395 |
| _version_ | 1819242612034371584 |
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| author | razieh sangsari maliheh kadivar maryam saeedi kayvan mirnia maryam ghavami adel moeinedin safavi |
| author_facet | razieh sangsari maliheh kadivar maryam saeedi kayvan mirnia maryam ghavami adel moeinedin safavi |
| author_sort | razieh sangsari |
| collection | DOAJ |
| description | This is a new case, affecting a twin that both with Hirschsprung’s disease, one was suffering from long-segment Hirschsprung’s disease with skip segmented. Our surgeon suspected the absence of abnormal vessel tortuosity in the transitional zone; thus, the appendix was sent for permanent pathology. There were ganglion cells in the colostomy site but no ganglion was found in the appendix. Complete biopsies from different parts of the intestine demonstrated positive ganglion cells in the transverse colon, ascending colon, and the distal ileum, jejunum, and duodenum, and negative ganglion cells in the rectum, sigmoid, descending colon, appendix, and 5 cm far from the ileocecal valve were observed. Therefore, the Kimura procedure was done. The most important key in such cases is the surgeons’ observation during operation. |
| first_indexed | 2024-12-23T14:42:34Z |
| format | Article |
| id | doaj.art-cb0d434d2e494443bfd69df28c40a9de |
| institution | Directory Open Access Journal |
| issn | 2538-2683 2538-2691 |
| language | English |
| last_indexed | 2024-12-23T14:42:34Z |
| publishDate | 2021-10-01 |
| publisher | Tehran University of Medical Sciences |
| record_format | Article |
| series | Case Reports in Clinical Practice |
| spelling | doaj.art-cb0d434d2e494443bfd69df28c40a9de2022-12-21T17:43:11ZengTehran University of Medical SciencesCase Reports in Clinical Practice2538-26832538-26912021-10-016310.18502/crcp.v6i3.7128Hirschsprung’s Disease in a Twin Neonate With One Suffering From Multple Skip Segmentsrazieh sangsari0maliheh kadivar1maryam saeedi2kayvan mirnia3maryam ghavami adel4moeinedin safavi5Divisionof Pediatrics, Departmentof Neonatology, Children’s Medical Center, School of Medicine, Tehran University of Medical Sciences, Tehran, Iran.Divisionof Pediatrics, Departmentof Neonatology, Children’s Medical Center, School of Medicine, Tehran University of Medical Sciences, Tehran, Iran.Divisionof Pediatrics, Departmentof Neonatology, Children’s Medical Center, School of Medicine, Tehran University of Medical Sciences, Tehran, Iran.Divisionof Pediatrics, Departmentof Neonatology, Children’s Medical Center, School of Medicine, Tehran University of Medical Sciences, Tehran, Iran.Divisionof Surgery, Departmentof Pediatrics Surgery, Neonatology, Children’s Medical Center, School of Medicine, Tehran University of Medical Sciences, Tehran, IranDepartment of Pathology, Children’s Medical Center, School of Medicine, Tehran University of Medical Sciences, Tehran, Iran.This is a new case, affecting a twin that both with Hirschsprung’s disease, one was suffering from long-segment Hirschsprung’s disease with skip segmented. Our surgeon suspected the absence of abnormal vessel tortuosity in the transitional zone; thus, the appendix was sent for permanent pathology. There were ganglion cells in the colostomy site but no ganglion was found in the appendix. Complete biopsies from different parts of the intestine demonstrated positive ganglion cells in the transverse colon, ascending colon, and the distal ileum, jejunum, and duodenum, and negative ganglion cells in the rectum, sigmoid, descending colon, appendix, and 5 cm far from the ileocecal valve were observed. Therefore, the Kimura procedure was done. The most important key in such cases is the surgeons’ observation during operation.https://crcp.tums.ac.ir/index.php/crcp/article/view/395Hirschsprung’s diseaseFrozen sectonsMeconium |
| spellingShingle | razieh sangsari maliheh kadivar maryam saeedi kayvan mirnia maryam ghavami adel moeinedin safavi Hirschsprung’s Disease in a Twin Neonate With One Suffering From Multple Skip Segments Case Reports in Clinical Practice Hirschsprung’s disease Frozen sectons Meconium |
| title | Hirschsprung’s Disease in a Twin Neonate With One Suffering From Multple Skip Segments |
| title_full | Hirschsprung’s Disease in a Twin Neonate With One Suffering From Multple Skip Segments |
| title_fullStr | Hirschsprung’s Disease in a Twin Neonate With One Suffering From Multple Skip Segments |
| title_full_unstemmed | Hirschsprung’s Disease in a Twin Neonate With One Suffering From Multple Skip Segments |
| title_short | Hirschsprung’s Disease in a Twin Neonate With One Suffering From Multple Skip Segments |
| title_sort | hirschsprung s disease in a twin neonate with one suffering from multple skip segments |
| topic | Hirschsprung’s disease Frozen sectons Meconium |
| url | https://crcp.tums.ac.ir/index.php/crcp/article/view/395 |
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