Aortic valve replacement surgery for a case of infantile Takayasu arteritis
Takayasu arteritis is a chronic inflammatory disease of unknown etiology primarily affecting the aorta and its major branches and usually occurring in the second or third decade of life. Here, we report a case of Takayasu arteritis in a 10-month-old patient. The infant presented with signs of conges...
| Main Authors: | , , , , , , , |
|---|---|
| Format: | Article |
| Language: | English |
| Published: |
Korean Pediatric Society
2012-07-01
|
| Series: | Korean Journal of Pediatrics |
| Subjects: | |
| Online Access: | http://kjp.or.kr/upload/pdf/kjped-55-254.pdf |
| _version_ | 1818943763651756032 |
|---|---|
| author | Hye Won Kwon Yoon Jung Suh Ji Seok Bang Bo Sang Kwon Gi Beom Kim Eun Jung Bae Woong Han Kim Chung Il Noh |
| author_facet | Hye Won Kwon Yoon Jung Suh Ji Seok Bang Bo Sang Kwon Gi Beom Kim Eun Jung Bae Woong Han Kim Chung Il Noh |
| author_sort | Hye Won Kwon |
| collection | DOAJ |
| description | Takayasu arteritis is a chronic inflammatory disease of unknown etiology primarily affecting the aorta and its major branches and usually occurring in the second or third decade of life. Here, we report a case of Takayasu arteritis in a 10-month-old patient. The infant presented with signs of congestive heart failure and severe aortic regurgitation. Echocardiography and computed tomography angiography showed an abnormally dilated thoracic and abdominal aorta. The infant was initially treated with prednisolone, followed by commissuroplasty of the aortic valve but neither approach ameliorated the heart failure. The patient was eventually treated with a mechanical aortic valve replacement surgery at the age of 12 months, and her condition stabilized. Although unusual, this case indicates that the diagnosis of Takayasu arteritis should be considered in children with unexplained systemic symptoms, aortic valve regurgitation, and heart failure. Because severe aortic regurgitation may be a fatal complication of Takayasu arteritis, early aortic valve replacement surgery should be considered, even in very young children. |
| first_indexed | 2024-12-20T07:32:30Z |
| format | Article |
| id | doaj.art-cb748ad2a8a141558f0852079d4ada68 |
| institution | Directory Open Access Journal |
| issn | 1738-1061 2092-7258 |
| language | English |
| last_indexed | 2024-12-20T07:32:30Z |
| publishDate | 2012-07-01 |
| publisher | Korean Pediatric Society |
| record_format | Article |
| series | Korean Journal of Pediatrics |
| spelling | doaj.art-cb748ad2a8a141558f0852079d4ada682022-12-21T19:48:23ZengKorean Pediatric SocietyKorean Journal of Pediatrics1738-10612092-72582012-07-0155725425810.3345/kjp.2012.55.7.2542012600018Aortic valve replacement surgery for a case of infantile Takayasu arteritisHye Won Kwon0Yoon Jung Suh1Ji Seok Bang2Bo Sang Kwon3Gi Beom Kim4Eun Jung Bae5Woong Han Kim6Chung Il Noh7Department of Pediatrics, Seoul National University Children's Hospital, Seoul, Korea.Department of Pediatrics, Seoul National University Children's Hospital, Seoul, Korea.Department of Pediatrics, Seoul National University Children's Hospital, Seoul, Korea.Department of Pediatrics, Seoul National University Children's Hospital, Seoul, Korea.Department of Pediatrics, Seoul National University Children's Hospital, Seoul, Korea.Department of Pediatrics, Seoul National University Children's Hospital, Seoul, Korea.Department of Thoracic and Cardiovascular Surgery, Seoul National University Children's Hospital, Seoul, Korea.Department of Pediatrics, Seoul National University Children's Hospital, Seoul, Korea.Takayasu arteritis is a chronic inflammatory disease of unknown etiology primarily affecting the aorta and its major branches and usually occurring in the second or third decade of life. Here, we report a case of Takayasu arteritis in a 10-month-old patient. The infant presented with signs of congestive heart failure and severe aortic regurgitation. Echocardiography and computed tomography angiography showed an abnormally dilated thoracic and abdominal aorta. The infant was initially treated with prednisolone, followed by commissuroplasty of the aortic valve but neither approach ameliorated the heart failure. The patient was eventually treated with a mechanical aortic valve replacement surgery at the age of 12 months, and her condition stabilized. Although unusual, this case indicates that the diagnosis of Takayasu arteritis should be considered in children with unexplained systemic symptoms, aortic valve regurgitation, and heart failure. Because severe aortic regurgitation may be a fatal complication of Takayasu arteritis, early aortic valve replacement surgery should be considered, even in very young children.http://kjp.or.kr/upload/pdf/kjped-55-254.pdfAortic valve insufficiencyTakayasu arteritis |
| spellingShingle | Hye Won Kwon Yoon Jung Suh Ji Seok Bang Bo Sang Kwon Gi Beom Kim Eun Jung Bae Woong Han Kim Chung Il Noh Aortic valve replacement surgery for a case of infantile Takayasu arteritis Korean Journal of Pediatrics Aortic valve insufficiency Takayasu arteritis |
| title | Aortic valve replacement surgery for a case of infantile Takayasu arteritis |
| title_full | Aortic valve replacement surgery for a case of infantile Takayasu arteritis |
| title_fullStr | Aortic valve replacement surgery for a case of infantile Takayasu arteritis |
| title_full_unstemmed | Aortic valve replacement surgery for a case of infantile Takayasu arteritis |
| title_short | Aortic valve replacement surgery for a case of infantile Takayasu arteritis |
| title_sort | aortic valve replacement surgery for a case of infantile takayasu arteritis |
| topic | Aortic valve insufficiency Takayasu arteritis |
| url | http://kjp.or.kr/upload/pdf/kjped-55-254.pdf |
| work_keys_str_mv | AT hyewonkwon aorticvalvereplacementsurgeryforacaseofinfantiletakayasuarteritis AT yoonjungsuh aorticvalvereplacementsurgeryforacaseofinfantiletakayasuarteritis AT jiseokbang aorticvalvereplacementsurgeryforacaseofinfantiletakayasuarteritis AT bosangkwon aorticvalvereplacementsurgeryforacaseofinfantiletakayasuarteritis AT gibeomkim aorticvalvereplacementsurgeryforacaseofinfantiletakayasuarteritis AT eunjungbae aorticvalvereplacementsurgeryforacaseofinfantiletakayasuarteritis AT woonghankim aorticvalvereplacementsurgeryforacaseofinfantiletakayasuarteritis AT chungilnoh aorticvalvereplacementsurgeryforacaseofinfantiletakayasuarteritis |