Effects of CFTR modulators on serum biomarkers of liver fibrosis in children with cystic fibrosis

Effects of CFTR modulators on serum biomarkers of liver fibrosis in children with cystic fibrosis

The cystic fibrosis (CF) transmembrane conductance regulator corrector/potentiator combinations lumacaftor/ivacaftor and elexacaftor/tezacaftor/ivacaftor improve sweat chloride, pulmonary function, and nutrition. Yet it is unclear whether they may also impact the progression of liver fibrosis, which...

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Bibliographic Details
Main Authors:	Steven Levitte, Yonathan Fuchs, Russell Wise, Zachary M. Sellers
Format:	Article
Language:	English
Published:	Wolters Kluwer Health/LWW 2023-02-01
Series:	Hepatology Communications
Online Access:	http://journals.lww.com/10.1097/HC9.0000000000000010

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