A Rare Case of Prurigo Pigmentosa in a Danish Sibling Couple

Prurigo pigmentosa (PP) is probably underdiagnosed due to lack of awareness. Previously, it was assumed that PP primarily affected Japanese females; however, more cases are reported worldwide, and the pathogenesis is still not completely understood. In this case report, we present two healthy Danish...

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Bibliographic Details
Main Authors: Maria Danielsen, Kristine Pallesen, Rikke Riber-Hansen, Anne Bregnhøj
Format: Article
Language:English
Published: Karger Publishers 2023-01-01
Series:Case Reports in Dermatology
Subjects:
Online Access:https://www.karger.com/Article/FullText/528422
Description
Summary:Prurigo pigmentosa (PP) is probably underdiagnosed due to lack of awareness. Previously, it was assumed that PP primarily affected Japanese females; however, more cases are reported worldwide, and the pathogenesis is still not completely understood. In this case report, we present two healthy Danish siblings, who developed PP approximately 2 weeks after starting a ketogenic diet, suggesting that both increased levels of ketone bodies in the blood together with a genetic predisposition might play a role in the development of PP.
ISSN:1662-6567