Severe Hepatic and Pulmonary Involvement in Rendu-Osler-Weber Syndrome

We report the case of a young woman with hereditary hemorrhagic telangiectasia (HHT) with severe liver involvement and pulmonary shunting. The medical imaging in this patient illustrates the severe shunting that can occur in these patients who often are asymptomatic. By showing this case, we want to...

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Main Authors: Xavier Verhelst, Anja Geerts, Hans Van Vlierberghe, Peter Smeets, Clarisse Lecluyse
Format: Article
Language:English
Published: Karger Publishers 2018-01-01
Series:Case Reports in Gastroenterology
Subjects:
Online Access:https://www.karger.com/Article/FullText/486189
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author Xavier Verhelst
Anja Geerts
Hans Van Vlierberghe
Peter Smeets
Clarisse Lecluyse
author_facet Xavier Verhelst
Anja Geerts
Hans Van Vlierberghe
Peter Smeets
Clarisse Lecluyse
author_sort Xavier Verhelst
collection DOAJ
description We report the case of a young woman with hereditary hemorrhagic telangiectasia (HHT) with severe liver involvement and pulmonary shunting. The medical imaging in this patient illustrates the severe shunting that can occur in these patients who often are asymptomatic. By showing this case, we want to highlight the role of liver transplantation in HHT with hepatic involvement.
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spelling doaj.art-cd4883948092449c86651497c08db0fb2022-12-21T18:14:57ZengKarger PublishersCase Reports in Gastroenterology1662-06312018-01-01121131810.1159/000486189486189Severe Hepatic and Pulmonary Involvement in Rendu-Osler-Weber SyndromeXavier VerhelstAnja GeertsHans Van VlierberghePeter SmeetsClarisse LecluyseWe report the case of a young woman with hereditary hemorrhagic telangiectasia (HHT) with severe liver involvement and pulmonary shunting. The medical imaging in this patient illustrates the severe shunting that can occur in these patients who often are asymptomatic. By showing this case, we want to highlight the role of liver transplantation in HHT with hepatic involvement.https://www.karger.com/Article/FullText/486189Hepatic involvementPulmonary involvementRendu-Osler-Weber syndrome
spellingShingle Xavier Verhelst
Anja Geerts
Hans Van Vlierberghe
Peter Smeets
Clarisse Lecluyse
Severe Hepatic and Pulmonary Involvement in Rendu-Osler-Weber Syndrome
Case Reports in Gastroenterology
Hepatic involvement
Pulmonary involvement
Rendu-Osler-Weber syndrome
title Severe Hepatic and Pulmonary Involvement in Rendu-Osler-Weber Syndrome
title_full Severe Hepatic and Pulmonary Involvement in Rendu-Osler-Weber Syndrome
title_fullStr Severe Hepatic and Pulmonary Involvement in Rendu-Osler-Weber Syndrome
title_full_unstemmed Severe Hepatic and Pulmonary Involvement in Rendu-Osler-Weber Syndrome
title_short Severe Hepatic and Pulmonary Involvement in Rendu-Osler-Weber Syndrome
title_sort severe hepatic and pulmonary involvement in rendu osler weber syndrome
topic Hepatic involvement
Pulmonary involvement
Rendu-Osler-Weber syndrome
url https://www.karger.com/Article/FullText/486189
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AT anjageerts severehepaticandpulmonaryinvolvementinrenduoslerwebersyndrome
AT hansvanvlierberghe severehepaticandpulmonaryinvolvementinrenduoslerwebersyndrome
AT petersmeets severehepaticandpulmonaryinvolvementinrenduoslerwebersyndrome
AT clarisselecluyse severehepaticandpulmonaryinvolvementinrenduoslerwebersyndrome