Unilateral Perisylvian Syndrome with Subcortical Heterotopia: A Case Report
Perisylvian syndrome is a neurological disorder in which a specific area of the brain (called the perisylvian area) develops abnormally, with polymicrogyria as the underlying developmental abnormality. A 21-year-old female reported to the department with complaint of two episodes of seizures per d...
| Main Authors: | , , |
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| Format: | Article |
| Language: | English |
| Published: |
JCDR Research and Publications Pvt. Ltd.
2022-01-01
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| Series: | International Journal of Anatomy Radiology and Surgery |
| Subjects: | |
| Online Access: | https://www.ijars.net/articles/PDF/2741/49499_CE[Ra1]_F(SHU)_GC(AnK)_PF1(MG_AnK_KM)_PN(KM).pdf |
| Summary: | Perisylvian syndrome is a neurological disorder in which a specific area of the brain (called the perisylvian area) develops abnormally,
with polymicrogyria as the underlying developmental abnormality. A 21-year-old female reported to the department with complaint
of two episodes of seizures per day since six months. Magnetic Resonance Imaging (MRI) revealed multiple small gyri with few
sulci noted in the right perisylvian cortex and right frontal lobe, suggesting polymicrogyria. Mild volume loss of right frontoparietal
lobes was seen. The small subcortical focus of grey matter signal was noted in the right frontal lobe suggesting of heterotopia. The
diagnosis of the perisylvian syndrome is mainly based on the clinical and radiologic features which are treated symptomatically and
by multidisciplinary rehabilitative measures as there is no cure for this syndrome. |
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| ISSN: | 2277-8543 2455-6874 |