Double valve replacement in a case of Hedinger syndrome

Abstract Hedinger Syndrome or carcinoid heart disease is a rare cardiac complication of neuroendocrine tumors (NET) affecting the tricuspid and pulmonary valves. Following is a case description of a patient undergoing treatment for a neuroendocrine tumor with liver metastasis, referred with symptoma...

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Main Authors: Presheet Pathare, Michael Weyand, Christian Heim
Format: Article
Language:English
Published: Wiley 2023-01-01
Series:Clinical Case Reports
Subjects:
Online Access:https://doi.org/10.1002/ccr3.6836
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author Presheet Pathare
Michael Weyand
Christian Heim
author_facet Presheet Pathare
Michael Weyand
Christian Heim
author_sort Presheet Pathare
collection DOAJ
description Abstract Hedinger Syndrome or carcinoid heart disease is a rare cardiac complication of neuroendocrine tumors (NET) affecting the tricuspid and pulmonary valves. Following is a case description of a patient undergoing treatment for a neuroendocrine tumor with liver metastasis, referred with symptomatic tricuspid valve regurgitation and pulmonary valve stenosis for surgical valve replacement. Planned surgical valve replacement was successfully performed before the onset of severe right ventricular failure or pulmonary hypertension in this case of carcinoid heart disease. An interdisciplinary approach and regular follow up is recommended in such cases.
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spelling doaj.art-cfb8cafbdb894c8baaa83efbe9a54d122023-03-01T07:50:57ZengWileyClinical Case Reports2050-09042023-01-01111n/an/a10.1002/ccr3.6836Double valve replacement in a case of Hedinger syndromePresheet Pathare0Michael Weyand1Christian Heim2Department of Cardiac Surgery University of Erlangen Erlangen GermanyDepartment of Cardiac Surgery University of Erlangen Erlangen GermanyDepartment of Cardiac Surgery University of Erlangen Erlangen GermanyAbstract Hedinger Syndrome or carcinoid heart disease is a rare cardiac complication of neuroendocrine tumors (NET) affecting the tricuspid and pulmonary valves. Following is a case description of a patient undergoing treatment for a neuroendocrine tumor with liver metastasis, referred with symptomatic tricuspid valve regurgitation and pulmonary valve stenosis for surgical valve replacement. Planned surgical valve replacement was successfully performed before the onset of severe right ventricular failure or pulmonary hypertension in this case of carcinoid heart disease. An interdisciplinary approach and regular follow up is recommended in such cases.https://doi.org/10.1002/ccr3.6836hedinger syndromeneuroendocrine tumorspulmonary stenosissurgical valve replacementtricuspid regurgitation
spellingShingle Presheet Pathare
Michael Weyand
Christian Heim
Double valve replacement in a case of Hedinger syndrome
Clinical Case Reports
hedinger syndrome
neuroendocrine tumors
pulmonary stenosis
surgical valve replacement
tricuspid regurgitation
title Double valve replacement in a case of Hedinger syndrome
title_full Double valve replacement in a case of Hedinger syndrome
title_fullStr Double valve replacement in a case of Hedinger syndrome
title_full_unstemmed Double valve replacement in a case of Hedinger syndrome
title_short Double valve replacement in a case of Hedinger syndrome
title_sort double valve replacement in a case of hedinger syndrome
topic hedinger syndrome
neuroendocrine tumors
pulmonary stenosis
surgical valve replacement
tricuspid regurgitation
url https://doi.org/10.1002/ccr3.6836
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