Double valve replacement in a case of Hedinger syndrome
Abstract Hedinger Syndrome or carcinoid heart disease is a rare cardiac complication of neuroendocrine tumors (NET) affecting the tricuspid and pulmonary valves. Following is a case description of a patient undergoing treatment for a neuroendocrine tumor with liver metastasis, referred with symptoma...
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Format: | Article |
Language: | English |
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Wiley
2023-01-01
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Series: | Clinical Case Reports |
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Online Access: | https://doi.org/10.1002/ccr3.6836 |
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author | Presheet Pathare Michael Weyand Christian Heim |
author_facet | Presheet Pathare Michael Weyand Christian Heim |
author_sort | Presheet Pathare |
collection | DOAJ |
description | Abstract Hedinger Syndrome or carcinoid heart disease is a rare cardiac complication of neuroendocrine tumors (NET) affecting the tricuspid and pulmonary valves. Following is a case description of a patient undergoing treatment for a neuroendocrine tumor with liver metastasis, referred with symptomatic tricuspid valve regurgitation and pulmonary valve stenosis for surgical valve replacement. Planned surgical valve replacement was successfully performed before the onset of severe right ventricular failure or pulmonary hypertension in this case of carcinoid heart disease. An interdisciplinary approach and regular follow up is recommended in such cases. |
first_indexed | 2024-04-10T06:31:12Z |
format | Article |
id | doaj.art-cfb8cafbdb894c8baaa83efbe9a54d12 |
institution | Directory Open Access Journal |
issn | 2050-0904 |
language | English |
last_indexed | 2024-04-10T06:31:12Z |
publishDate | 2023-01-01 |
publisher | Wiley |
record_format | Article |
series | Clinical Case Reports |
spelling | doaj.art-cfb8cafbdb894c8baaa83efbe9a54d122023-03-01T07:50:57ZengWileyClinical Case Reports2050-09042023-01-01111n/an/a10.1002/ccr3.6836Double valve replacement in a case of Hedinger syndromePresheet Pathare0Michael Weyand1Christian Heim2Department of Cardiac Surgery University of Erlangen Erlangen GermanyDepartment of Cardiac Surgery University of Erlangen Erlangen GermanyDepartment of Cardiac Surgery University of Erlangen Erlangen GermanyAbstract Hedinger Syndrome or carcinoid heart disease is a rare cardiac complication of neuroendocrine tumors (NET) affecting the tricuspid and pulmonary valves. Following is a case description of a patient undergoing treatment for a neuroendocrine tumor with liver metastasis, referred with symptomatic tricuspid valve regurgitation and pulmonary valve stenosis for surgical valve replacement. Planned surgical valve replacement was successfully performed before the onset of severe right ventricular failure or pulmonary hypertension in this case of carcinoid heart disease. An interdisciplinary approach and regular follow up is recommended in such cases.https://doi.org/10.1002/ccr3.6836hedinger syndromeneuroendocrine tumorspulmonary stenosissurgical valve replacementtricuspid regurgitation |
spellingShingle | Presheet Pathare Michael Weyand Christian Heim Double valve replacement in a case of Hedinger syndrome Clinical Case Reports hedinger syndrome neuroendocrine tumors pulmonary stenosis surgical valve replacement tricuspid regurgitation |
title | Double valve replacement in a case of Hedinger syndrome |
title_full | Double valve replacement in a case of Hedinger syndrome |
title_fullStr | Double valve replacement in a case of Hedinger syndrome |
title_full_unstemmed | Double valve replacement in a case of Hedinger syndrome |
title_short | Double valve replacement in a case of Hedinger syndrome |
title_sort | double valve replacement in a case of hedinger syndrome |
topic | hedinger syndrome neuroendocrine tumors pulmonary stenosis surgical valve replacement tricuspid regurgitation |
url | https://doi.org/10.1002/ccr3.6836 |
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