Progressive hemifacial atrophy

Progressive hemifacial atrophy, also known as Parry-Romberg Syndrome, is an uncommon degenerative and poorly understood condition. It is characterized by a slow and progressive but self-limited atrophy affecting one side of the face. The incidence and the cause of this alteration are unknown. A cere...

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Main Authors: Abhijeet Sande, Mukund Risbud, Avinash Kshar, Arati Oka Paranjpe
Format: Article
Language:English
Published: Wolters Kluwer Medknow Publications 2013-01-01
Series:Dental Research Journal
Subjects:
Online Access:http://www.drjjournal.net/article.asp?issn=1735-3327;year=2013;volume=10;issue=1;spage=108;epage=111;aulast=Sande
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author Abhijeet Sande
Mukund Risbud
Avinash Kshar
Arati Oka Paranjpe
author_facet Abhijeet Sande
Mukund Risbud
Avinash Kshar
Arati Oka Paranjpe
author_sort Abhijeet Sande
collection DOAJ
description Progressive hemifacial atrophy, also known as Parry-Romberg Syndrome, is an uncommon degenerative and poorly understood condition. It is characterized by a slow and progressive but self-limited atrophy affecting one side of the face. The incidence and the cause of this alteration are unknown. A cerebral disturbance of fat metabolism has been proposed as a primary cause. Possible factors that are involved in the pathogenesis include trauma, viral infections, heredity, endocrine disturbances and auto-immunity. The most common complications that appear in association to this disorder are: trigeminal neuralgia, facial paresthesia, severe headache and epilepsy. Characteristically, the atrophy progresses slowly for several years and, it becomes stable. The objective of this work is, through the presentation of a clinical case, to accomplish a literature review concerning general characteristics, etiology, physiopathology and treatment of progressive hemifacial atrophy.
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spelling doaj.art-cfd27ddbf41f446eacf0acc321ead8782022-12-22T00:55:15ZengWolters Kluwer Medknow PublicationsDental Research Journal1735-33272008-02552013-01-0110110811110.4103/1735-3327.111810Progressive hemifacial atrophyAbhijeet SandeMukund RisbudAvinash KsharArati Oka ParanjpeProgressive hemifacial atrophy, also known as Parry-Romberg Syndrome, is an uncommon degenerative and poorly understood condition. It is characterized by a slow and progressive but self-limited atrophy affecting one side of the face. The incidence and the cause of this alteration are unknown. A cerebral disturbance of fat metabolism has been proposed as a primary cause. Possible factors that are involved in the pathogenesis include trauma, viral infections, heredity, endocrine disturbances and auto-immunity. The most common complications that appear in association to this disorder are: trigeminal neuralgia, facial paresthesia, severe headache and epilepsy. Characteristically, the atrophy progresses slowly for several years and, it becomes stable. The objective of this work is, through the presentation of a clinical case, to accomplish a literature review concerning general characteristics, etiology, physiopathology and treatment of progressive hemifacial atrophy.http://www.drjjournal.net/article.asp?issn=1735-3327;year=2013;volume=10;issue=1;spage=108;epage=111;aulast=SandeProgressive hemifacial atrophyParry-Romberg SyndromeRomberg′s disease
spellingShingle Abhijeet Sande
Mukund Risbud
Avinash Kshar
Arati Oka Paranjpe
Progressive hemifacial atrophy
Dental Research Journal
Progressive hemifacial atrophy
Parry-Romberg Syndrome
Romberg′s disease
title Progressive hemifacial atrophy
title_full Progressive hemifacial atrophy
title_fullStr Progressive hemifacial atrophy
title_full_unstemmed Progressive hemifacial atrophy
title_short Progressive hemifacial atrophy
title_sort progressive hemifacial atrophy
topic Progressive hemifacial atrophy
Parry-Romberg Syndrome
Romberg′s disease
url http://www.drjjournal.net/article.asp?issn=1735-3327;year=2013;volume=10;issue=1;spage=108;epage=111;aulast=Sande
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