Progressive hemifacial atrophy
Progressive hemifacial atrophy, also known as Parry-Romberg Syndrome, is an uncommon degenerative and poorly understood condition. It is characterized by a slow and progressive but self-limited atrophy affecting one side of the face. The incidence and the cause of this alteration are unknown. A cere...
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Format: | Article |
Language: | English |
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Wolters Kluwer Medknow Publications
2013-01-01
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Series: | Dental Research Journal |
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Online Access: | http://www.drjjournal.net/article.asp?issn=1735-3327;year=2013;volume=10;issue=1;spage=108;epage=111;aulast=Sande |
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author | Abhijeet Sande Mukund Risbud Avinash Kshar Arati Oka Paranjpe |
author_facet | Abhijeet Sande Mukund Risbud Avinash Kshar Arati Oka Paranjpe |
author_sort | Abhijeet Sande |
collection | DOAJ |
description | Progressive hemifacial atrophy, also known as Parry-Romberg Syndrome, is an uncommon degenerative and poorly understood condition. It is characterized by a slow and progressive but self-limited atrophy affecting one side of the face. The incidence and the cause of this alteration are unknown. A cerebral disturbance of fat metabolism has been proposed as a primary cause. Possible factors that are involved in the pathogenesis include trauma, viral infections, heredity, endocrine disturbances and auto-immunity. The most common complications that appear in association to this disorder are: trigeminal neuralgia, facial paresthesia, severe headache and epilepsy. Characteristically, the atrophy progresses slowly for several years and, it becomes stable. The objective of this work is, through the presentation of a clinical case, to accomplish a literature review concerning general characteristics, etiology, physiopathology and treatment of progressive hemifacial atrophy. |
first_indexed | 2024-12-11T18:21:01Z |
format | Article |
id | doaj.art-cfd27ddbf41f446eacf0acc321ead878 |
institution | Directory Open Access Journal |
issn | 1735-3327 2008-0255 |
language | English |
last_indexed | 2024-12-11T18:21:01Z |
publishDate | 2013-01-01 |
publisher | Wolters Kluwer Medknow Publications |
record_format | Article |
series | Dental Research Journal |
spelling | doaj.art-cfd27ddbf41f446eacf0acc321ead8782022-12-22T00:55:15ZengWolters Kluwer Medknow PublicationsDental Research Journal1735-33272008-02552013-01-0110110811110.4103/1735-3327.111810Progressive hemifacial atrophyAbhijeet SandeMukund RisbudAvinash KsharArati Oka ParanjpeProgressive hemifacial atrophy, also known as Parry-Romberg Syndrome, is an uncommon degenerative and poorly understood condition. It is characterized by a slow and progressive but self-limited atrophy affecting one side of the face. The incidence and the cause of this alteration are unknown. A cerebral disturbance of fat metabolism has been proposed as a primary cause. Possible factors that are involved in the pathogenesis include trauma, viral infections, heredity, endocrine disturbances and auto-immunity. The most common complications that appear in association to this disorder are: trigeminal neuralgia, facial paresthesia, severe headache and epilepsy. Characteristically, the atrophy progresses slowly for several years and, it becomes stable. The objective of this work is, through the presentation of a clinical case, to accomplish a literature review concerning general characteristics, etiology, physiopathology and treatment of progressive hemifacial atrophy.http://www.drjjournal.net/article.asp?issn=1735-3327;year=2013;volume=10;issue=1;spage=108;epage=111;aulast=SandeProgressive hemifacial atrophyParry-Romberg SyndromeRomberg′s disease |
spellingShingle | Abhijeet Sande Mukund Risbud Avinash Kshar Arati Oka Paranjpe Progressive hemifacial atrophy Dental Research Journal Progressive hemifacial atrophy Parry-Romberg Syndrome Romberg′s disease |
title | Progressive hemifacial atrophy |
title_full | Progressive hemifacial atrophy |
title_fullStr | Progressive hemifacial atrophy |
title_full_unstemmed | Progressive hemifacial atrophy |
title_short | Progressive hemifacial atrophy |
title_sort | progressive hemifacial atrophy |
topic | Progressive hemifacial atrophy Parry-Romberg Syndrome Romberg′s disease |
url | http://www.drjjournal.net/article.asp?issn=1735-3327;year=2013;volume=10;issue=1;spage=108;epage=111;aulast=Sande |
work_keys_str_mv | AT abhijeetsande progressivehemifacialatrophy AT mukundrisbud progressivehemifacialatrophy AT avinashkshar progressivehemifacialatrophy AT aratiokaparanjpe progressivehemifacialatrophy |