Pulmonary Agenesis and Associated Pulmonary Hypertension: A Case Report and Review on Variability, Therapy, and Outcome

Pulmonary Agenesis and Associated Pulmonary Hypertension: A Case Report and Review on Variability, Therapy, and Outcome

Abstract Pulmonary agenesis is a rare congenital disorder with large variability in presentation and prognosis. We describe a full-term infant born with right-sided pulmonary agenesis who underwent thoracoscopic placement of a tissue expander. He ultimately died of pulmonary hypertension. Immunohist...

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Bibliographic Details
Main Authors:	Oliver Muensterer, Rosanna Abellar, David Otterburn, Rajamma Mathew
Format:	Article
Language:	English
Published:	Georg Thieme Verlag KG 2015-01-01
Series:	European Journal of Pediatric Surgery Reports
Subjects:	pulmonary agenesis pulmonary hypertension tissue expander thoracoscopy
Online Access:	http://www.thieme-connect.de/DOI/DOI?10.1055/s-0034-1395986

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