Moyamoya Disease, Which is Rare in Infancy: A Case Report
Moyamoya disease etiology is an undetermined vasculopathy and is mainly thought to affect the Internal Carotid Artery and Wills circle. An 8-month-old patient without any underlying disease was referred to our hospital with sudden extreme right hemiparesis. There was no evidence of meningeal irritat...
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| Format: | Article |
| Language: | English |
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Galenos Yayinevi
2023-12-01
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| Series: | Journal of Pediatric Emergency and Intensive Care Medicine |
| Subjects: | |
| Online Access: |
http://www.caybdergi.com/archives/archive-detail/article-preview/moyamoya-disease-which-is-rare-in-nfancy-a-case-re/62404
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| _version_ | 1797664694038691840 |
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| author | Edin Botan Ayşen Durak Merve Boyraz Derya Bako |
| author_facet | Edin Botan Ayşen Durak Merve Boyraz Derya Bako |
| author_sort | Edin Botan |
| collection | DOAJ |
| description | Moyamoya disease etiology is an undetermined vasculopathy and is mainly thought to affect the Internal Carotid Artery and Wills circle. An 8-month-old patient without any underlying disease was referred to our hospital with sudden extreme right hemiparesis. There was no evidence of meningeal irritation in the neurological examination, decreased tonus on the right side, strength in the upper right extremity 3/5 and strength in the lower right extremity 2/5, deep tendon reflexes were exaggerated. Cranial brain tomography angiography showed in both distal internal cerebral arteries and branches and a significantly curvy appearance, with similar changes present in the veins forming the Willis circle. Low molecular weight heparin, acetylsalicylic acid, and levetiracetam were started. On the fifth day of follow-up, motor activity in the lower right extremity returned to normal. The power loss of 2/5 in the upper right extremity was continuing. The patient was then transferred to a center with Moyamoya surgery, which may be needed. This case highlights the importance of considering Moyamoya disease as a classical etiologies of acute ischemic strokes in children. It also highlights the rare presentation among the Turkish population and the use of neurovascular imaging techniques to facilitate the diagnosis of Moyamoya diseas |
| first_indexed | 2024-03-11T19:34:02Z |
| format | Article |
| id | doaj.art-d0d482b4b4f34278976375f39f8fbb22 |
| institution | Directory Open Access Journal |
| issn | 2146-2399 2148-7332 |
| language | English |
| last_indexed | 2024-03-11T19:34:02Z |
| publishDate | 2023-12-01 |
| publisher | Galenos Yayinevi |
| record_format | Article |
| series | Journal of Pediatric Emergency and Intensive Care Medicine |
| spelling | doaj.art-d0d482b4b4f34278976375f39f8fbb222023-10-06T13:15:16ZengGalenos YayineviJournal of Pediatric Emergency and Intensive Care Medicine2146-23992148-73322023-12-0110322422710.4274/cayd.galenos.2023.5693313049054Moyamoya Disease, Which is Rare in Infancy: A Case ReportEdin Botan0Ayşen Durak1Merve Boyraz2Derya Bako3 University of Health Sciences Turkey, Van Training and Research Hospital, Clinic of Pediatric Critical Care Medicine, Van, Turkey Ankara University Faculty of Medicine, Department of Pediatrics, Ankara, Turkey University of Health Sciences Turkey, Van Training and Research Hospital, Clinic of Pediatrics, Van, Turkey University of Health Sciences Turkey, Van Training and Research Hospital, Clinic of Pediatric Radiology, Van, Turkey Moyamoya disease etiology is an undetermined vasculopathy and is mainly thought to affect the Internal Carotid Artery and Wills circle. An 8-month-old patient without any underlying disease was referred to our hospital with sudden extreme right hemiparesis. There was no evidence of meningeal irritation in the neurological examination, decreased tonus on the right side, strength in the upper right extremity 3/5 and strength in the lower right extremity 2/5, deep tendon reflexes were exaggerated. Cranial brain tomography angiography showed in both distal internal cerebral arteries and branches and a significantly curvy appearance, with similar changes present in the veins forming the Willis circle. Low molecular weight heparin, acetylsalicylic acid, and levetiracetam were started. On the fifth day of follow-up, motor activity in the lower right extremity returned to normal. The power loss of 2/5 in the upper right extremity was continuing. The patient was then transferred to a center with Moyamoya surgery, which may be needed. This case highlights the importance of considering Moyamoya disease as a classical etiologies of acute ischemic strokes in children. It also highlights the rare presentation among the Turkish population and the use of neurovascular imaging techniques to facilitate the diagnosis of Moyamoya diseas http://www.caybdergi.com/archives/archive-detail/article-preview/moyamoya-disease-which-is-rare-in-nfancy-a-case-re/62404 infantmoyamoya diseasecerebral angiographyacute stroke |
| spellingShingle | Edin Botan Ayşen Durak Merve Boyraz Derya Bako Moyamoya Disease, Which is Rare in Infancy: A Case Report Journal of Pediatric Emergency and Intensive Care Medicine infant moyamoya disease cerebral angiography acute stroke |
| title | Moyamoya Disease, Which is Rare in Infancy: A Case Report |
| title_full | Moyamoya Disease, Which is Rare in Infancy: A Case Report |
| title_fullStr | Moyamoya Disease, Which is Rare in Infancy: A Case Report |
| title_full_unstemmed | Moyamoya Disease, Which is Rare in Infancy: A Case Report |
| title_short | Moyamoya Disease, Which is Rare in Infancy: A Case Report |
| title_sort | moyamoya disease which is rare in infancy a case report |
| topic | infant moyamoya disease cerebral angiography acute stroke |
| url |
http://www.caybdergi.com/archives/archive-detail/article-preview/moyamoya-disease-which-is-rare-in-nfancy-a-case-re/62404
|
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